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¿µ¹® endocrine gland ÇÑ±Û ³»ºÐºñ»ù
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¿µ¹® pancreas ÇÑ±Û ÀÌÀÚ, ÃéÀå
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  ¼ÒÈ­±â°üÀÇ ÀϺκÐÀ¸·Î ÀÌÀÚ¾×À» ºÐºñÇÑ´Ù. ±×¸®°í, ±âŸ ´ë»ç¿¡ °ü¿©Çϴ ȣ¸£¸óÀ» ¶û°Ô¸£Çѽº ¼¶¼¼Æ÷¿¡¼­ ºÐºñÇÑ´Ù. º¹ºÎ³» »ùâÀÚÀÇ µÚÂÊ¿¡ À§Ä¡Çϸç, º¹º®¿¡ ºÙ¾î ÀÖ´Ù. ±×¸®°í ÀÌÀÚ¾×À» ºÐºñÇϴ ÀÌÀÚ°üÀº ´ãÁóÀ» ºÐºñÇϴ ¿Â¾µ°³°ü°ú ÇÔ²² »ùâÀÚÀÇ Áß°£ºÎ¿¡ °³±¸ÇÑ´Ù. µû¶ó¼­ ÀÌÀÚ¸Ó¸®ºÎÀÇ Á¾¾çÀ¸·Î ÁÖÀ§ Àå±â¸¦ ¾Ð¹ÚÇϰԠµÇ¸é, ÁÖÀ§ÀÇ ¿Â¾µ°³°üÀÌ °°ÀÌ ´­¸®°Ô µÇ¾î ´ãÁóºÐºñ°¡ µÇÁö ¾Ê¾Æ È²´ÞÀÌ ³ªÅ¸³­´Ù.
  
  ¼ÒÈ­È¿¼ÒÀΠÀÌÀÚ¾×À» ºÐºñÇϰí, À§¿¡¼­ ³»·Á¿Â À§»êÀ» ÁßÈ­½Ãų ¼ö Àִ ÁßÈ­È¿¼Ò¸¦ ºÐºñÇÑ´Ù. ±×¸®°í ¶û°Ô¸£Çѽº¼¶¼¼Æ÷¿¡¼­ ´ë»ç¿¡ Æ¯ÀÌÇѠȣ¸£¸óÀ» ºÐºñÇÑ´Ù. ¶û°Ô¸£Çѽº¼¶¼¼Æ÷´Â ¿°»öÀÇ ÇüÅ¿¡ µû¶ó 2°¡Áö ¼¼Æ÷°¡ Á¸ÀçÇϴµ¥, ¸ÕÀú ¾ËÆÄ¼¼Æ÷(alpha cell: 10~30%Á¤µµ)´Â »¡°²°Ô ¿°»öµÇ¸ç ±Û·çÄ«°ïÀ» ºÐºñÇÑ´Ù. ±×¸®°í ´Ù¸¥ ÇÑ Á¾·ùÀΠº£Å¸¼¼Æ÷(beta cell: 60~90%Á¤µµ)´Â ÆÄ¶þ°Ô ¿°»öµÇ¸ç, Àν¶¸°À» ºÐºñÇÑ´Ù.
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  • ¿µ¹®
    ÇѱÛ
  • alveolar soft part sarcoma
    Æ÷»ó¿¬ºÎÀ°Á¾
  • maternal part
    ¸ðüºÎºÐ
  • opercular part
    µ¤°³ºÎºÐ
  • presenting part
    ¼±ÁøºÎ
  • part
    ºÎºÐ, ºÎ
  • annular pancreas
    °í¸®ÀÌÀÚ, °í¸®ÃéÀå
  • accessory pancreas
    µ¡ÀÌÀÚ, ºÎÃéÀå
  • dorsal pancreas
    µîÂÊÀÌÀÚ, ¹èÃøÃéÀå
  • exocrine pancreas
    ¿ÜºÐºñÀÌÀÚ, ¿ÜºÐºñÃéÀå
  • head of pancreas
    ÀÌÀÚ¸Ó¸®, ÃéµÎ
  • pancreas
    ÀÌÀÚ, ÃéÀå
  • pancreas divisum
    ºÐ¸®ÀÌÀÚ, ºÐ¸®ÃéÀå
  • ventral pancreas
    ¹èÂÊÀÌÀÚ, º¹ÃøÃéÀå
  • endocrine
    1. ³»ºÐºñ- 2. È£¸£¸ó-
  • endocrine cataract
    ³»ºÐºñ¹é³»Àå
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  • ¿µ¹®
    ÇѱÛ
  • endocrine
    ³»ºÐºñ-
  • multiple endocrine neoplasia
    º¹ÇÕ³»ºÐºñ»ù½Å»ý¹°
  • part
    ºÎºÐ, ºÎ
  • presenting part
    ¼±ÁøºÎ
  • head of pancreas
    ÀÌÀÚ¸Ó¸®
  • pancreas divisum
    ºÐ¸®ÀÌÀÚ, ºÐ¸®ÃéÀå
  • pancreas
    ÀÌÀÚ, ÃéÀå
  • accessory pancreas
    µ¡ÀÌÀÚ, µ¡ÃéÀå
  • annular pancreas
    °í¸®ÀÌÀÚ
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • maternal part
    ¸ðüºÎºÐ
  • opercular part
    µ¤°³ºÎºÐ
  • part
    ºÎºÐ, ºÎ
  • accessory pancreas
    µ¡ÀÌÀÚ, µ¡ÃéÀå
  • annular pancreas
    °í¸®ÀÌÀÚ
  • dorsal pancreas
    µîÂÊÀÌÀÚ
  • exocrine pancreas
    ¿ÜºÐºñÀÌÀÚ
  • pancreas head
    ÀÌÀÚ¸Ó¸®
  • pancreas
    ÀÌÀÚ, ÃéÀå
  • pancreas divisum
    ºÐÇÒÀÌÀÚ, ºÐÇÒÃéÀå
  • ventral pancreas
    ¹èÂÊÀÌÀÚ
  • multiple endocrine adenomatosis
    ´Ù¹ß³»ºÐºñ»ùÁ¾Áõ
  • endocrine cataract
    ³»ºÐºñ¹é³»Àå
  • endocrine
    ³»ºÐºñ
  • endocrine exophthalmos
    ³»ºÐºñ´«µ¹Ãâ(Áõ)
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  • ¿µ¹®
    ÇѱÛ
  • gastrointestinal endocrine cell
    À§Ã¢ÀÚ³»ºÐºñ¼¼Æ÷
  • anterior part of pons basilar part of pons
    ´Ù¸®³ú¾ÕºÎºÐ ´Ù¸®³ú¹Ù´ÚºÎºÐ
  • accessory pancreas
    (µ¡ÀÌÀÚ)
  • annular pancreas
    ˱ȗ̎, ˱ȗ̎ˌ.
  • annular pancreas
    °í¸®ÀÌÀÚ
  • head of pancreas
    ÃéÀå¸Ó¸®, ÃéµÎ(õýÔé).
  • head of pancreas
    ÀÌÀÚ¸Ó¸®
  • head of pancreas
    ÃéµÎ(ÃéµÎ).
  • Intermediate part(commissura) of bulb
    Áú¾î±Í¸Á¿ïÁß°£ºÎºÐ
  • Iridial part of retina
    ¸Á¸·È«Ã¼ºÎºÐ
  • Iridic part of retina
    ¸Á¸·È«Ã¤[Á¶¸®°³]ºÎºÐ
  • Laibal part
    ÀÔ¼úºÎºÐ
  • Lateral(part of) globus pallidus
    °¡ÂÊâ¹éÇÙ
  • abdominal part
    ¹èºÎºÐ
  • alisphenoidal part
    ³ªºñ»À³¯°³ºÎºÐ
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • anterior part of pons basilar part of pons
    ´Ù¸®³ú¾ÕºÎºÐ ´Ù¸®³ú¹Ù´ÚºÎºÐ
  • corticomedial part olfactory part
    °ÑÁú¾ÈÂʺκÐ
  • intermediate part red part
    Áß°£ºÎºÐ
  • cortical endocrine cell
    °ÑÁú³»ºÐºñ¼¼Æ÷
  • discrete multiple endocrine adenomatosis syndrome
    ºÐ¸®¼º ´Ù¹ß ³»ºÐºñ¼±Á¾ ÁõÈıº(ÝÂìÆàõÒýÛ¡Ò®ÝÂù²àÍðþñøý¦ÏØ).
  • endocrine
    ³»ºÐºñ(Ò®ÝÂÝô)
  • endocrine cataract
    ³»ºÐºñ¼º¹é³»Àå
  • endocrine cell
    ³»ºÐºñ ¼¼Æ÷(Ò®ÝÂÝô á¬øà)
  • endocrine cell
    ³»ºÐºñ¼¼Æ÷
  • endocrine cell cluster
    ³»ºÐºñ¼¼Æ÷¹«¸®
  • endocrine cell of pineal gland
    ¼Û°úü³»ºÐºñ¼¼Æ÷
  • endocrine cell tumor
    ³»ºÐºñ ¼¼Æ÷ Á¾¾ç(¡­ðþåË)
  • endocrine exophthalmos
    ³»ºÐºñ¼º¾È±¸µ¹Ãâ(Áõ).
  • endocrine fracture
    ³»ºÐºñ¼º °ñÀý(Ò®ÝÂÝôàõÍéï½).
  • endocrine gland
    ³»ºÐºñ¼±(Ò®ÝÂù²àÊ)
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Cortical endocrine cell
    °ÑÁú³»ºÐºñ¼¼Æ÷
    [¿¾ ¿ë¾î] ÇÇÁú³»ºÐºñ¼¼Æ÷
  • ENDOCRINE GLAND
    ³»ºÐºñ»ù
    [¿¾ ¿ë¾î] ³»ºÐºñ¼±
  • ENDOCRINE GLANDS
    ³»ºÐºñ»ù
    [¿¾ ¿ë¾î] ³»ºÐºñ¼±
  • Medullary endocrine cell
    ¼ÓÁú³»ºÐºñ¼¼Æ÷
    [¿¾ ¿ë¾î] ¼öÁú³»ºÐºñ¼¼Æ÷
  • Endocrine cell of pineal gland
    ¼Û°úü³»ºÐºñ¼¼Æ÷
    [¿¾ ¿ë¾î] ¼Û°úü³»ºÐºñ¼¼Æ÷
  • Gastrointestinal endocrine cell
    À§Ã¢ÀÚ³»ºÐºñ¼¼Æ÷
    [¿¾ ¿ë¾î] À§Ã¢ÀÚ³»ºÐºñ¼¼Æ÷
  • Pancreatic endocrine cell
    ÀÌÀÚ³»ºÐºñ¼¼Æ÷
    [¿¾ ¿ë¾î] ÃéÀå³»ºÐºñ¼¼Æ÷
  • Endocrine cell
    ³»ºÐºñ¼¼Æ÷
    [¿¾ ¿ë¾î] ³»ºÐºñ¼¼Æ÷
  • (Accessory pancreas)
    (µ¡ÀÌÀÚ)
    [¿¾ ¿ë¾î] ºÎÃéÀå
  • Conjunction (Annular pancreas)
    °áÇÕ(°í¸®ÀÌÀÚ)
    [¿¾ ¿ë¾î] °áÇÕ
  • Dorsal pancreas
    µîÂÊÀÌÀÚ
    [¿¾ ¿ë¾î] ¹èÃøÃé
  • Ventral pancreas
    ¹èÂÊÀÌÀÚ
    [¿¾ ¿ë¾î] º¹ÃøÃé
  • Pancreas
    ÀÌÀÚ
    [¿¾ ¿ë¾î] ÃéÀå
  • PANCREAS
    ÀÌÀÚ[ÃéÀå]
    [¿¾ ¿ë¾î] ÃéÀå
  • Tail of pancreas
    ÀÌÀÚ²¿¸®
    [¿¾ ¿ë¾î] Ãé¹Ì
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  • ¿µ¹®
    ÇѱÛ
  • endocrine gland
    ³»ºÐºñ¼±(Ò®ÝÂÝôàÍ)
  • endocrine hormones
    ³»ºÐºñ¼±(Ò®ÝÂÝôàÍ) È£¸£¸ó
  • endocrine system
    ³»ºÐºñ¼±(Ò®ÝÂù²àÊ) ½Ã½ºÅÛ
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 8 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • part
    ºÎ, ºÎºÐ
  • endocrine
    ³»ºÐºñÀÇ
  • endocrine disease
    ³»ºÐºñÁúȯ
  • annular pancreas
    ˱ȗ̎ˌ
  • ectopic pancreas
    À̼ÒÃéÀå
  • head of pancreas
    ÃéÀå¸Ó¸®, ÃéµÎ
  • pancreas
    ̎ˌ
  • pancreas head
    ÃéµÎºÎ
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
AEP acute edematous pancreatitis; artificial endocrine pancreas; auditory evoked potential; average evok...
MEN Multiple Endocrine Neoplasia
  ; AD Trait
  1. MEN Type I(= Wermer Syndro...
PP   1) Presenting Part
  2) Plasma-Pheresis
  3) Pancreatic Polype...
BMAD Medicare Part B Annual Data [file]
CAP camptodactyly-arthropathy-pericarditis [syndrome]; Canada Assistance Plan; capsule; captopril; catab...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
ASPS Alveolar soft part sarcoma
IMHV intermediate part of the medial hyperstriatum ventrale
p.p.b. part per billion
ppt part per trillion
PD Pancreas Divisum
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • aberrant pancreas
    À̼Ҽº Ãé Á¶Á÷
    ÃéÀåÀÇ Á¶Á÷ÀÌ ÇØºÎÇÐÀûÀ¸·Î º»·¡ÀÇ À§Ä¡°¡ ¾Æ´Ñ °÷¿¡ Á¸ÀçÇÏ´Â °æ¿ì. °¡Àå ÈçÇÑ ºÎÀ§´Â À§¿Í ½ÊÀÌÁöÀåÀ̸ç Meckel °Ô½ÇÀ̳ª ȸÀå µî¿¡¼­µµ ¹ß°ßµÉ ¼ö ÀÖ´Ù. Å©±â´Â Á÷°æÀÌ ¼ö mm·ÎºÎÅÍ Å« °ÍÀº 3-4cmÀ¸·Î ´Ù¾çÇÏ´Ù. ±¹¼ÒÀûÀ¸·Î ´ÜÀÏ º´¼ÒÀÏ ¼öµµ ÀÖ°í ´Ù¹ß¼º ÀÏ ¼öµµ ÀÖ´Ù. ¾à°£ °íÇüÀÇ ¿¬È²»öÀ̳ª ȸ»öÀÇ »öÁ¶¸¦ ¶ì°í Á¡¸·¿¡ ¿¬ÇÑ ¼ÒÈ­°üÀÇ º®¿¡ Áý¶ôÀ» ÀÌ·ç°í Á¡¸· ÇÏÃþ¿¡ À§Ä¡ÇÏ¸ç °£È¤ Langerhans ¼¶¿¡ º¹ÇյDZ⵵ ÇÑ´Ù. À̵éÀº ´ë°Ô ¾Æ¹«·± Áõ»óÀÌ ¾øÀ¸³ª ¶§¶§·Î ´Ù¸¥ ¸ñÀûÀÇ Ä¡·á³ª °Ë»ç¸¦ ¹ÞÀ» ¶§ ¿ì¿¬È÷ ¹ß°ßµÈ´Ù. Áï °³º¹ ¼ö¼ú°ú ¹æ»ç¼± °Ë»ç ¹× ³»½Ã°æ °Ë»ç ½Ã ¼ÒÈ­°ü °­ ³»·Î ¾à°£ µ¹ÃâµÈ ¾ç»óÀ» ³ªÅ¸³½´Ù. µå¹°°Ô Ãéµµ ¼¼Æ÷Á¾
  • body of pancreas
    ÃéÀå ¸öÅë, Ãéü
  • discrete multiple endocrine adenomatosis syndrome
    ºÐ¸®¼º ´Ù¹ß ³»ºÐºñ ¼±Á¾ ÁõÈıº
  • disease of the pancreas
    ÃéÀå Áúȯ
  • ectopic pancreas
    À̼Ҽº ÃéÀå
    ºñÀÔ ÃéÀå, ºÎÃéÀåÀ̶ó°íµµ ÇÑ´Ù. ½Äµµ ÇϺο¡¼­ ȸÀå »çÀÌ¿¡ ¹ß»ýÇÑ´Ù.
  • endocrine diabetes
    ³»ºÐºñ¼º ´ç´¢º´
  • endocrine disorder
    ³»ºÐºñ Àå¾Ö
  • endocrine exophthalmos
    ³»ºÐºñ¼º ¾È±¸ µ¹Ãâ, ³»ºÐºñ¼º ¾È±¸ µ¹ÃâÁõ
  • endocrine gland
    ³»ºÐºñ »ù, ³»ºÐºñ ¼±
    1. Ç¥¸é°ú ¿¬°áµÊÀÌ ¾øÀÌ Ç÷°ü ¼ÓÀ¸·Î ºÐºñÇÏ´Â »ù. 2. È£¸£¸óÀ» ºÐºñÇÏ´Â ¼±. ¿ÜºÐºñ¼±°ú °°Àº µµ°üÀÌ ¾ø°í È£¸£¸óÀº Á÷Á¢ ü¾× ¼ÓÀ¸·Î ¹èÃâµÈ´Ù.
  • endocrine organ
    ³»ºÐºñ ±â°ü
    ³»ºÐºñ ±â´ÉÀ» ´ã´çÇÏ´Â ½Åü ±â°üÀ¸·Î ³úÇϼöü, ½Ã»ó ÇϺÎ, °©»ó¼±, ÃéÀå, ºÎ½Å, ºÎ°©»ó¼±°ú »ý½Ä ±â°üÀÌ ÀÖ´Ù.
  • endocrine system
    ³»ºÐºñ°è
    ÀÎüÀÇ Á¶Àý ±â´ÉÀ¸·Î ¼¼Æ÷°£ÀÇ ´ëÈ­¸¦ È­ÇÐ ¹°ÁúÀΠȣ¸£¸óÀ» ÅëÇØ¼­ È­ÇÐÀûÀÎ ½ÅÈ£¸¦ ÀÌ¿ëÇÏ¿© Ç¥Àû ¼¼Æ÷µé¿¡ ÀÛ¿ëÇÑ´Ù. ÈçÇÑ ³»ºÐºñ°è ÀÌ»óÀº ºñÁ¤»óÀûÀÎ ¼ºÀå, ¿¡³ÊÁö ¼öÁØ º¯È­ ¿Âµµ º¯È­¿¡ÀÇ ºÎÀûÀÀ ¹× ¼³¸íµÇÁö ¾Ê´Â üÁß º¯È­·Î ³ªÅ¸³­´Ù. ´Ù´¢, °úµµÇÑ °¥Áõ, üÁß °¨¼Ò¸¦ µ¿¹ÝÇÑ ½Ä¿å °ú´Ù´Â ´ç´¢º´ÀÇ Æ¯Â¡ÀÌ´Ù. ½Ã·Â º¯È­, ½ÅÀå ±â´ÉÀå¾Ö, »çÁöÀÇ Ç÷¾× ¼øÈ¯ °¨¼Ò´Â Àå±â°£ÀÇ ´ç´¢·Î ÀÎÇÑ ÁøÇàµÈ Ç÷°ü °æÈ­ÀÇ Áõ»óÀÌ´Ù.
  • head of pancreas
    ÃéÀå ¸Ó¸®, ÃéµÎ
  • multiple endocrine neoplasia
    ´Ù¹ß¼º ³»ºÐºñ Á¾¾ç
  • pancreas
    ÃéÀå, ÀÌÀÚ
    À§ µÚÂÊ¿¡ ÀÖ´Â °¡´Ã°í ±ä »ï°¢ÁÖ ¸ð¾çÀÇ Àå±â. ź¼öÈ­¹°, ´Ü¹éÁú, Áö¹æ µîÀ» ¼ÒÈ­ÇÏ´Â È¿¼Ò¸¦ ³½´Ù.
  • pancreas cancer
    ÃéÀå ¾Ï
    ÃéÀå¿¡ »ý±â´Â ¾Ï. ÃéÀå
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
exocrine part of pancreas exocrine part of pancreas
bone diseases, endocrine Diseases of the bones related to hyperfunction or hypofunction of the endocrine glands.
(12 Dec 1998)
multiple endocrine adenomatosis The presence of functioning tumours in more than one endocrine gland, commonly the pancreatic islets and parathyroid glands, which may be associated with Zollinger-Ellison syndrome; dominant inheritance.
Synonym: multiple endocrine adenomatosis.
(05 Mar 2000)
multiple endocrine deficiency syndrome <syndrome> Acquired deficiency of the function of several endocrine glands, usually on an auto-immune basis.
Synonym: multiple glandular deficiency syndrome.
(05 Mar 2000)
multiple endocrine neoplasia (type I) This is a hereditary disorder in which two or more of the following glands: parathyroid, pancreas, pituitary, adrenals or thyroid develop hyperplasia or a tumour.
(type II) This is a hereditary disorder in which two or more of the following glands: thyroid, adrenal or parathyroid, develop overgrowth (hyperplasia) or malignant cells (cancer). The underlying cause is genetic and a positive family history for this illness is a risk factor.
Incidence: approximately 3 in 100,000 people in the general population.
Origin: Gr. Plassein = to form
(27 Sep 1997)
multiple endocrine neoplasia 1 <radiology> Multiple endrocrine neoplasia syndrome three P's.
Pituitary adenoma, 65% can develop Cushing's, acromegaly, prolactinoma, parathyroid hyperplasia / adenoma, 88% can develop hyper-PTH
pancreatic isleT-cell tumour, gastrinoma (Z-E) most common, 50% of Z-E can develop MEN-1, inconstant features: bronchial/intestinal carcinoid, thyroid adenoma, adrenal cortical tumour, lipoma, thymoma tissue expression
Primary hyperparathyroidism (90%), Gastrinoma (30%), Prolactinoma (15%), Other (10%).
Synonym: Wermer syndrome
(12 Dec 1998)
multiple endocrine neoplasia 2 <radiology> Multiple endocrine neoplasia syndrome, medullary thyroid carcinoma, usually multifocal; metastasis to local nodes, lung, liver, usually calcify in liver, pheochromocytoma, almost always bilateral, parathyroid hyperplasia, may be secondary to calcitonin secreted by medullary thyroid carcinoma inconstant feature: adrenal cortical hyperplasia
Synonym: Sipple syndrome
(12 Dec 1998)
multiple endocrine neoplasia 3 <radiology> Multiple endocrine neoplasia syndrome (type 2B, type 3), medullary thyroid carcinoma, pheochromocytoma, marfanoid habitus (Cf: Marfan syndrome), mucosal neuromas, neurofibromas, ganglioneuromatosis coli More info: MEN syndrome 2B
Synonym: Schimke, marfanoid syndrome
(12 Dec 1998)
multiple endocrine neoplasia type 1 A rare syndrome characterised by hyperplasia and/or neoplasms of the pituitary, parathyroid glands, and pancreatic islets. Hyperparathyroidism occurs in 90% of the cases and is usually the first manifestation of the syndrome. The most frequent pancreatic manifestation is gastrinoma typically leading to zollinger-ellison syndrome. The appearance of this condition has been limited to the loss of allelic heterozygosity at the 11q13 locus on the long arm of chromosome 11. Patients overall exhibit long survival times. Chemotherapy is rare and surgical management is generally dependent on the genetic expression in individual patients.
(12 Dec 1998)
multiple endocrine neoplasia type 2 <syndrome> This is a hereditary disorder in which two or more of the following glands: thyroid, adrenal or parathyroid, develop overgrowth (hyperplasia) or malignant cells (cancer). The underlying cause is genetic and a positive family history for this illness is a risk factor.
Incidence: approximately 3 in 100,000 people in the general population.
(27 Sep 1997)
multiple endocrine neoplasia type 2a A type of multiple endocrine neoplasia characterised by a virtually 100% incidence of medullary thyroid carcinoma, a 50% incidence of pheochromocytoma, and a lesser incidence of parathyroid adenomas associated with hyperparathyroidism. The condition is always transmitted through autosomal dominant inheritance. Genetic testing can identify individuals with the trait in early infancy. Treatment is usually excision of the enlarged parathyroid glands.
(12 Dec 1998)
multiple endocrine neoplasia type 2b A type of multiple endocrine neoplasia occurring as an isolated congenital presentation or as a distinct autosomal dominant disease. It is characterised by the 100% incidence of medullary thyroid carcinoma and frequent pheochromocytomas; patients seldom exhibit hyperparathyroidism. It is distinguished from men 2a by its characteristic physical appearance resulting from numerous neural defects including mucosal neuromas of the eyelids, lips, and tongue. The neural abnormalities also include widespread neurogangliomatosis of the gastrointestinal tract leading to abnormal gut motility. Treatment usually requires total thyroidectomy following evaluation for the presence of pheochromocytomas.
(12 Dec 1998)
neoplastic endocrine-like syndromes Endocrine syndromes due to hormone production by neoplasms of non-endocrine tissue, or by other than the usual endocrine tissues. They are often the first indication of a previously undetected neoplasm.
(12 Dec 1998)
diagnostic techniques, endocrine Methods and procedures for the diagnosis of diseases or dysfunction of the endocrine glands or demonstration of their physiological processes.
(12 Dec 1998)
endocrine Pertaining to internal secretions, hormonal.
Compare: exocrine.
Origin: Gr. Krinein = to separate
(18 Nov 1997)
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