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dihydrolipoamide acetyltransferase <enzyme> Part of the pyruvate dehydrogenase complex; acef isolated from e. Coli
Registry number: EC 2.3.1.12
Synonym: dihydrolipoyl transacetylase, lipoate acetyltransferase, dihydrolipoyl acetyltransferase, acef gene product
(26 Jun 1999)
dihydrolipoamide acyltransferase <enzyme> Component of branched-chain 2-oxo acid dehydrogenase multienzyme complex; mutation in this (e2) catalytic subunit identifies type II maple syrup urine disease
Registry number: EC 2.3.1.-
Synonym: dihydrolipoyl transacylase, branched chain acyltransferase, e2 transacylase
(26 Jun 1999)
dihydrolipoamide dehydrogenase <enzyme> An enzyme oxidizing dihydrolipoamide at the expense of NAD+; completes the oxidative decarboxylation of pyruvate; a part of several enzyme complexes (e.g., alpha-ketoglutarate dehydrogenase complex). Decreased activity leads to neuronal loss in brain resulting in psychomotor retardation.
Synonym: coenzyme factor, lipoamide dehydrogenase, lipoamide reductase (NADH), lipoyl dehydrogenase.
(05 Mar 2000)
dihydrolipoamide succinyltransferase <enzyme> Component of the ketoglutarate dehydrogenase complex
Registry number: EC 2.3.1.61
Synonym: succinyl-CoA-dihydrolipoate-s-succinyltransferase, dihydrolipoyl transsuccinylase, lipoyl transsuccinylase, lipoate succinyltransferase, lipoamide succinyltransferase, succinyl-coenzyme a-dihydrolipoate-s-succinyltransferase
(26 Jun 1999)
dihydrolipoic acid Reduced lipoic acid, formed by cleavage of the -S-S- bond as a result of the acceptance of two hydrogens.
Compare: lipoic acid.
(05 Mar 2000)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 2 ÆäÀÌÁö: 1
  • Dihydrolipoamide Dehydrogenase - »õâ A flavoprotein containing oxidoreductase that catalyzes the reduction of lipoamide by NADH to yield dihydrolipoamide and NAD+. The enzyme is a component of several MULTIENZYME COMPLEXES.
    Synonyms : Diaphorase (Lipoamide Dehydrogenase), Dihydrolipoyl Dehydrogenase, Glycine Decarboxylase Complex L-Protein, L-Protein, Glycine Decarboxylase Complex, Lipoamide Dehydrogenase, Valine, Lipoic Acid Dehydrogenase, Lipoyl Dehydrogenase, Dehydrogenase, Lipoamide
  • Dihydrolipoyllysine-Residue Acetyltransferase - »õâ An enzyme that catalyzes the acetyltransferase reaction using ACETYL CoA as an acetyl donor and dihydrolipoamide as acceptor to produce COENZYME A (CoA) and S-acetyldihydrolipoamide. It forms the (E2) subunit of the PYRUVATE DEHYDROGENASE COMPLEX.
    Synonyms : Acetyl-CoA-Dihydrolipoamide S-Acetyltransferase, Dihydrolipoamide Acetyltransferase, Dihydrolipoamide S-Acetyltransferase, Dihydrolipoyl Acetyltransferase, Dihydrolipoyl Transacetylase, Lipoate Acetyltransferase, Pyruvate Dehydrogenase Complex E2
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dihydrol the associated water molecule, (H2O)2.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
dihydrolipoamide the reduced form of lipoamide, produced as an intermediate in the reactions in which lipoamide acts as a cofactor.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
dihydrolipoamide S- [EC 2.3.1.12] an enzyme of the transferase class that is a component of the multienzyme pyruvate dehydrogenase complex (q.v.). The enzyme catalyzes the transfer of acetyl from acetyldihydrolipoamide to coenzyme A to form acetyl CoA; the enzyme is itself the physiological lipoamide in the reaction. Called also dihydrolipoyltransacetylase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
dihydrolipoamide acyltransferase an enzyme of the transferase class that is the lipoamide component of the multienzyme branched-chain α-keto acid dehydrogenase complex (q.v.). The enzyme catalyzes the transfer of the decarboxylated branched-chain acyl moiety to coenzyme A via its own lipoic acid group.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
dihydrolipoamide dehydrogenase [EC 1.8.1.4] an enzyme of the oxidoreductase class that catalyzes the regeneration of lipoamide from dihydrolipoamide, reducing NAD+. The enzyme contains FAD and is a component of several oxidative decarboxylation enzyme complexes: branched-chain α-keto acid dehydrogenase complex, α-ketoglutarate dehydrogenase complex, and pyruvate dehydrogenase complex; deficiency of the enzyme, an autosomal recessive trait, causes lipoamide dehydrogenase deficiency.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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