| dihydrolipoamide acetyltransferase | <enzyme> Part of the pyruvate dehydrogenase complex; acef isolated from e. Coli Registry number: EC 2.3.1.12 Synonym: dihydrolipoyl transacetylase, lipoate acetyltransferase, dihydrolipoyl acetyltransferase, acef gene product (26 Jun 1999) |
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| dihydrolipoamide acyltransferase | <enzyme> Component of branched-chain 2-oxo acid dehydrogenase multienzyme complex; mutation in this (e2) catalytic subunit identifies type II maple syrup urine disease Registry number: EC 2.3.1.- Synonym: dihydrolipoyl transacylase, branched chain acyltransferase, e2 transacylase (26 Jun 1999) |
| dihydrolipoamide dehydrogenase | <enzyme> An enzyme oxidizing dihydrolipoamide at the expense of NAD+; completes the oxidative decarboxylation of pyruvate; a part of several enzyme complexes (e.g., alpha-ketoglutarate dehydrogenase complex). Decreased activity leads to neuronal loss in brain resulting in psychomotor retardation. Synonym: coenzyme factor, lipoamide dehydrogenase, lipoamide reductase (NADH), lipoyl dehydrogenase. (05 Mar 2000) |
| dihydrolipoamide succinyltransferase | <enzyme> Component of the ketoglutarate dehydrogenase complex Registry number: EC 2.3.1.61 Synonym: succinyl-CoA-dihydrolipoate-s-succinyltransferase, dihydrolipoyl transsuccinylase, lipoyl transsuccinylase, lipoate succinyltransferase, lipoamide succinyltransferase, succinyl-coenzyme a-dihydrolipoate-s-succinyltransferase (26 Jun 1999) |
| dihydrolipoic acid | Reduced lipoic acid, formed by cleavage of the -S-S- bond as a result of the acceptance of two hydrogens. Compare: lipoic acid. (05 Mar 2000) |
Synonyms : Diaphorase (Lipoamide Dehydrogenase), Dihydrolipoyl Dehydrogenase, Glycine Decarboxylase Complex L-Protein, L-Protein, Glycine Decarboxylase Complex, Lipoamide Dehydrogenase, Valine, Lipoic Acid Dehydrogenase, Lipoyl Dehydrogenase, Dehydrogenase, Lipoamide
Synonyms : Acetyl-CoA-Dihydrolipoamide S-Acetyltransferase, Dihydrolipoamide Acetyltransferase, Dihydrolipoamide S-Acetyltransferase, Dihydrolipoyl Acetyltransferase, Dihydrolipoyl Transacetylase, Lipoate Acetyltransferase, Pyruvate Dehydrogenase Complex E2
| dihydrol |
the associated water molecule, (H2O)2.
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| dihydrolipoamide |
the reduced form of lipoamide, produced as an intermediate in the reactions in which lipoamide acts as a cofactor.
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| dihydrolipoamide S- |
[EC 2.3.1.12] an enzyme of the transferase class that is a component of the multienzyme pyruvate dehydrogenase complex (q.v.). The enzyme catalyzes the transfer of acetyl from acetyldihydrolipoamide to coenzyme A to form acetyl CoA; the enzyme is itself the physiological lipoamide in the reaction. Called also dihydrolipoyltransacetylase.
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| dihydrolipoamide acyltransferase |
an enzyme of the transferase class that is the lipoamide component of the multienzyme branched-chain α-keto acid dehydrogenase complex (q.v.). The enzyme catalyzes the transfer of the decarboxylated branched-chain acyl moiety to coenzyme A via its own lipoic acid group.
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| dihydrolipoamide dehydrogenase |
[EC 1.8.1.4] an enzyme of the oxidoreductase class that catalyzes the regeneration of lipoamide from dihydrolipoamide, reducing NAD+. The enzyme contains FAD and is a component of several oxidative decarboxylation enzyme complexes: branched-chain α-keto acid dehydrogenase complex, α-ketoglutarate dehydrogenase complex, and pyruvate dehydrogenase complex; deficiency of the enzyme, an autosomal recessive trait, causes lipoamide dehydrogenase deficiency.
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