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  • cystathionine
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  • cystathionine beta-synthase
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  • cystathionine synthetase
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CBS cervicobrachial syndrome; chronic brain syndrome; clinical behavioral science; conjugated bile salts...
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CBS Cystathionine beta synthase
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cystathionine beta-synthase <enzyme> A multifunctional pyridoxal phosphate enzyme. In the second stage of cysteine biosynthesis it catalyses the reaction of homocysteine with serine to form cystathionine with the elimination of water.
Chemical name: L-Serine hydro-lyase (adding homocysteine)
Registry number: EC 4.2.1.22
(12 Dec 1998)
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cystathionine <chemical> Chemical name: L-Homocysteine, S-(2-amino-2-carboxyethyl)-, (R)-
(12 Dec 1998)
cystathionine beta-lyase <enzyme> An enzyme catalyzing the hydrolysis of l-cystathionine to pyruvate, l-homocysteine, and NH3.
See: cystathionine gamma-lyase.
Synonym: beta-cystathionase, cystine lyase.
(05 Mar 2000)
cystathionine gamma-lyase <enzyme> A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyses the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate.
Chemical name: L-Cystathionine cysteine-lyase (deaminating)
Registry number: EC 4.4.1.1
(12 Dec 1998)
cystathionine gamma-synthase o-succinylhomoserine (thiol)-lyase
homocysteine cystathionine gamma-synthase <enzyme> Homocysteine and cystein yield cystathionine and h2s
Registry number: EC 4.4.-
Synonym: hccg-s
(26 Jun 1999)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Cystathionine beta-Synthase - »õâ A multifunctional pyridoxal phosphate enzyme. In the second stage of cysteine biosynthesis it catalyzes the reaction of homocysteine with serine to form cystathionine with the elimination of water. Deficiency of this enzyme leads to HYPERHOMOCYSTEINEMIA and HOMOCYSTINURIA. EC 4.2.1.22.
    Synonyms : Cystathionine Synthetase, Cystathionine beta Synthase, Sulfhydrase, Serine, Synthetase, Cystathionine, beta Thionase, beta-Synthase, Cystathionine
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