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  • cystathionine
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  • cystathionine beta-synthase
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  • cystathionine synthetase
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  • cystathionine
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CBS cervicobrachial syndrome; chronic brain syndrome; clinical behavioral science; conjugated bile salts...
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CBS Cystathionine beta synthase
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cystathionine beta-lyase <enzyme> An enzyme catalyzing the hydrolysis of l-cystathionine to pyruvate, l-homocysteine, and NH3.
See: cystathionine gamma-lyase.
Synonym: beta-cystathionase, cystine lyase.
(05 Mar 2000)
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cystathionine <chemical> Chemical name: L-Homocysteine, S-(2-amino-2-carboxyethyl)-, (R)-
(12 Dec 1998)
cystathionine beta-synthase <enzyme> A multifunctional pyridoxal phosphate enzyme. In the second stage of cysteine biosynthesis it catalyses the reaction of homocysteine with serine to form cystathionine with the elimination of water.
Chemical name: L-Serine hydro-lyase (adding homocysteine)
Registry number: EC 4.2.1.22
(12 Dec 1998)
cystathionine gamma-lyase <enzyme> A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyses the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate.
Chemical name: L-Cystathionine cysteine-lyase (deaminating)
Registry number: EC 4.4.1.1
(12 Dec 1998)
cystathionine gamma-synthase o-succinylhomoserine (thiol)-lyase
homocysteine cystathionine gamma-synthase <enzyme> Homocysteine and cystein yield cystathionine and h2s
Registry number: EC 4.4.-
Synonym: hccg-s
(26 Jun 1999)
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