| CBS | cervicobrachial syndrome; chronic brain syndrome; clinical behavioral science; conjugated bile salts... |
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| CBS | Cystathionine beta synthase |
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| cystathionine | <chemical> Chemical name: L-Homocysteine, S-(2-amino-2-carboxyethyl)-, (R)- (12 Dec 1998) |
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| cystathionine beta-lyase | <enzyme> An enzyme catalyzing the hydrolysis of l-cystathionine to pyruvate, l-homocysteine, and NH3. See: cystathionine gamma-lyase. Synonym: beta-cystathionase, cystine lyase. (05 Mar 2000) |
| cystathionine beta-synthase | <enzyme> A multifunctional pyridoxal phosphate enzyme. In the second stage of cysteine biosynthesis it catalyses the reaction of homocysteine with serine to form cystathionine with the elimination of water. Chemical name: L-Serine hydro-lyase (adding homocysteine) Registry number: EC 4.2.1.22 (12 Dec 1998) |
| cystathionine gamma-lyase | <enzyme> A multifunctional pyridoxal phosphate enzyme. In the final step in the biosynthesis of cysteine it catalyses the cleavage of cystathionine to yield cysteine, ammonia, and 2-ketobutyrate. Chemical name: L-Cystathionine cysteine-lyase (deaminating) Registry number: EC 4.4.1.1 (12 Dec 1998) |
| cystathionine gamma-synthase | o-succinylhomoserine (thiol)-lyase |
| homocysteine cystathionine gamma-synthase | <enzyme> Homocysteine and cystein yield cystathionine and h2s Registry number: EC 4.4.- Synonym: hccg-s (26 Jun 1999) |
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Synonyms :
Synonyms : Cystathionine Synthetase, Cystathionine beta Synthase, Sulfhydrase, Serine, Synthetase, Cystathionine, beta Thionase, beta-Synthase, Cystathionine
Synonyms : Cystine Desulfohydrolase, Cystathionine gamma Lyase, Deaminase, Homoserine, Dehydratase, Homoserine, Desulfhydrase, Cysteine, Desulfhydrase, Cystine, Desulfohydrolase, Cystine, gamma Cystathionase, gamma-Lyase, Cystathionine
| cystathionine |
(cys
출처: www.mercksource.com/pp/us/cns/cns_hl_dorlands.jspz...
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| cystathionine β-synthase |
[EC 4.2.1.22] an enzyme of the lyase class that catalyzes the condensation of serine and homocysteine to form cystathionine as a step in the catabolism of methionine. It is a pyridoxal-phosphate protein, found in the mammalian liver.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| cystathionine β-synthase deficiency |
an autosomal recessive aminoacidopathy characterized by homocystinuria accompanied by hypermethioninemia. Clinical abnormalities occur primarily in the eye and the skeletal, nervous, and vascular systems; ectopia lentis, osteoporosis, mental retardation, and thrombosis are the most common manifestations. In older literature, the disorder is sometimes called homocystinuria (q.v.).
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| cystathionine γ-lyase |
[EC 4.4.1.1] an enzyme of the lyase class that catalyzes the cleavage of cystathionine to cysteine, α-ketoglutarate, and ammonia as a step in the metabolism of methionine. It is a pyridoxal-phosphate protein and the reaction occurs in the liver. Deficiency of the enzyme, an autosomal recessive trait, results in cystathioninuria. Called also γ-cystathionase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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