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  • racemase
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  • carnitine
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  • carnitine palmitoyl transferase, deficiency
    Carnitine palmitoyl transferase, deficiency
  • plasma membrane carnitine transport defect
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  • carnitine
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  • carnitine barrier
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ALCAR acetyl-L-carnitine
CPT carnitine palmityl transferase; carotid pulse tracing; chest physiotherapy; child protection team; c...
MCD magnetic circular dichroism; mast-cell degranulation; mean cell diameter; mean of consecutive differ...
SCD scleroderma; service-connected disability; sickle-cell disease; spinocerebellar degeneration; subacu...
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MR Mandelate racemase
ALC Acetyl-L-Carnitine
ALCAR Acetyl-L-Carnitine
CPT Carnitine Palmitoyl Transferase
CPTI Carnitine Palmitoyltransferase I
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  • carnitine
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    ºñŸÀÎ À¯µµÃ¼. ¸», µÅÁö, ¼ÒÀÇ °ñ°Ý±Ù¿¡ Á¸ÀçÇÑ´Ù. À̰ÍÀ» µ¿¹°¿¡ ÁÖ»çÇÏ¸é ±¸Åä, ¼³»ç, À¯¿¬, »êµ¿ µîÀ» ÀÏÀ¸Å²´Ù. Ç×°©»ó¼±Á¦·Î »ç¿ëµÈ´Ù.
  • racemase
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    ±¤ÇÐÀûÀ¸·Î Ȱ¼ºÀÇ ¹°ÁúÀÇ ¶ó½Ã¹ÌÈ­¸¦ Ã˸ÅÇÏ´Â È¿¼Ò.
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
carnitine racemase <enzyme> Homologous to enoyl hydratases and isomerases; converts d(+)-carnitine to l(-)-carnitine; isolated from e. Coli
Registry number: EC 5.1.-
Synonym: caid gene product
(26 Jun 1999)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
alanine racemase <enzyme> A pyridoxal-phosphate protein that reversibly catalyses the conversion of l-alanine to d-alanine.
Chemical name: Alanine racemase
Registry number: EC 5.1.1.1
(12 Dec 1998)
alpha-methylacyl-CoA racemase <enzyme> Involved in catabolism of branched-chain fatty acids derived from isoprenoids; acts on pristanoyl-CoA and trihydroxycoprostanoyl-CoA, but not on 3-methyl branched-chain or linear-chain acyl coas; amino acid sequence has been determined; genbank u89905 (rat) and u89906 (mouse); also isolated from human liver
Registry number: EC 5.1.99.-
Synonym: meac CoA racemase
(26 Jun 1999)
racemase <enzyme> Enzymes that catalyze inversion of the configuration around an asymmetric carbon in a substrate having one (racemase) or more (epimerase) centre(s) of asymmetry. For example; hydroxyproline, ribulose phosphate).
Registry number: EC 5.1
(21 Jun 2000)
glutamate racemase <enzyme> Catalyses the conversion of l-glutamate to d-glutamate; muri protein was isolated from e. Coli
Registry number: EC 5.1.1.3
Synonym: muri protein, muri gene product
(26 Jun 1999)
proline racemase <enzyme> An enzyme that reversibly converts d-proline to l-proline.
(05 Mar 2000)
hydantoin racemase <enzyme> Catalyses the racemization of 5-substituted hydantoins in pseudomonas to their corresponding n-carbamoyl amino acids and ultimately to the corresponding l-amino acid
Registry number: EC 5.1.99.-
Synonym: hyue protein, hyue gene product
(26 Jun 1999)
lysine racemase <enzyme> Interconverts the d- and l-isomers
Registry number: EC 5.1.1.5
(26 Jun 1999)
carnitine <biochemistry> _ Hydroxy _ trimethyl aminobutyric acid. Compound that transports long chain fatty acids across the inner mitochondrial membrane in the form of acyl carnitine. Sometimes referred to as Vitamin Bt or Vitamin B7.
(18 Nov 1997)
carnitine acyltransferases <enzyme> Acyltransferases in the inner mitochondrial membrane that catalyze the reversible transfer of acyl groups from acyl-CoA to l-carnitine and thereby mediate the transport of activated fatty acids through that membrane.
Registry number: EC 2.3.1.-
(12 Dec 1998)
carnitine amidase <enzyme> Hydrolyzes l-carnitine amide steroselectively
Registry number: EC 3.5.1.-
(26 Jun 1999)
carnitine coenzyme A ligase <enzyme> Caic protein isolated from e. Coli
Registry number: EC 6.2.1.-
Synonym: carnitine CoA ligase, crotonobetaine CoA ligase, caic gene product
(26 Jun 1999)
carnitine dehydratase <enzyme> From E coli; catalyses the reversible dehydration of (l)-carnitine forming crotonobetaine
Registry number: EC 4.2.1.-
Synonym: caib protein, caib gene product
(26 Jun 1999)
carnitine o-acetyltransferase <enzyme> An enzyme that catalyses the formation of o-acetylcarnitine from acetyl-CoA plus carnitine.
Chemical name: Acetyl-CoA:carnitine O-acetyltransferase
Registry number: EC 2.3.1.7
(12 Dec 1998)
carnitine o-palmitoyltransferase <enzyme> An enzyme that catalyses reversibly the conversion of palmitoyl-CoA to palmitoylcarnitine in the inner mitochondrial membrane.
Chemical name: Palmitoyl-CoA:L-carnitine O-palmitoyltransferase
Registry number: EC 2.3.1.21
(12 Dec 1998)
carnitine palmitoyltransferase <enzyme> An enzyme that reversibly forms acylcarnitines and coenzyme A from carnitine and acylcoenzyme A (often, palmitoyl-CoA); important in fatty acid oxidation. Deficiency of isozyme I results in ketogenesis with hypoglycaemia; deficiency of isozyme II affects primarily skeletal muscle.
(05 Mar 2000)
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