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"carbohydrate-deficient glycoprotein syndrome"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
¾Ë±â½¬¿î ÀÇÇпë¾îÇ®ÀÌÁý, ¼­¿ïÀÇ´ë ±³¼ö ÁöÁ¦±Ù, °í·ÁÀÇÇÐ ÃâÆÇ À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
¿µ¹® testicular feminization syndrome ÇÑ±Û °íȯ¿©¼ºÈ­ÁõÈıº
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  ÀÌÂ÷¼ºÀåÀ» Æ÷ÇÔÇÏ¿©, ¿Ü¼º±âÀÇ ¹ßÀ°Àº ¿©¼ºÀÌÁö¸¸ °íȯÀÌ Á¸ÀçÇϰí, Àڱðú ÀڱðüÀÌ °áÇ̵Ǿî Àִ ³²¼º °ÅÁþ³²³àÇѸöÁõÀÇ ±Ø´ÜÀû ÇüÅÂÀÌ´Ù. À̰ÍÀº Å×½ºÅ佺Å×·ÐÀÇ ÀÛ¿ë¿¡ ´ëÇÑ ¸»´Ü±â°üÀÇ ÀúÇ׿¡ ±âÀÎÇÑ´Ù.
  
  
¿µ¹® irritable bowel syndrome ÇÑ±Û °ú¹Î¼º´ëÀåÁõÈıº
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  ¹èº¯Àå¾Ö, º¹Åë, º¹ºÎÆØ¸¸ µîÀÇ Áõ»óÀÌ ÀÖÀ¸³ª ±âÁúÀûÀΠº´º¯ÀÌ ¾øÀ½ÀÌ È®ÀεȠ¿¹¸¦ ÃѸÁ¶óÇÑ ÀÓ»ó ÁõÈıºÀÌ´Ù. °¡Àå ÈçÇÑ ¼ÒÈ­±â ÁúȯÀ̸ç(Àü¼ÒÈ­±â È¯ÀÚÀÇ 70~80%) °¡Àå ÈçÇÑ Áúº´(Àüü Àα¸ÀÇ ¾à 20%)ÀÌ´Ù. ¿©¼ºÀÌ ³²¼º¿¡ ºñÇØ 2¹è Á¤µµ ¸¹ÀÌ ¹ß»ýÇϸç 30´ë ¹× 40´ë¿¡¼­ È£¹ßÇÏ°í ¼±Áø °ø¾÷±¹¿¡¼­ ¸¹ÀÌ ¹ß»ýÇÑ´Ù. Áø´ÜÀ» À§Çؼ­´Â º´·Â Ã»Ãë°¡ °¡Àå Áß¿äÇ졒ʡ¢Á¾ °Ë»ç·Î¼­ ±âÁúº´À» Á¦¿ÜÇØ¾ß ÇÑ´Ù. Ä¡·á·Î´Â ¾ÈÁ¤¿ä¹ý(Á¤½Å°úÀû ¸é´ã ¹× ½É¸®¿ä¹ý, ½Å°æ¾ÈÁ¤Á¦), ½Ä»ç¿ä¹ý(°í¼¶À¯Áú À½½Ä ¼·Ãë, Àڱؼº À½½Ä ÇÇÇϱâ), ¾à¹° ¿ä¹ý(âÀÚ°æ·Ã ÁøÁ¤Á¦, º¯ºñ ¿ÏÈ­Á¦, Áö»çÁ¦) µîÀ» »ç¿ëÇÑ´Ù.
¿µ¹® withdrawal syndrome ÇÑ±Û ±Ý´ÜÁõÈıÙ
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  ¾ËÄÚ¿Ã, ¸¶¾à, ¹ÙºñÅõ¸£»ê°è ÃÖ¸é¾à µîÀÇ ¾à¹°À» Àå±â°£ º¹¿ëÇÏ¿© ¾à¹°ÀÌ ¾øÀ̴ °ßµô ¼ö ¾ø°ÔµÈ µÚ, ±× ¾à¹°À» ÁßÁöÇÑ °æ¿ì¿¡ ³ªÅ¸³ª´Â, °íÅëÀÌ ¼ö¹ÝµÇ´Â ½ÅüÀû Áõ»óÀ» ¸»ÇÑ´Ù. ¿¬¼Ó º¹¿ëÀÇ ±â°£¿¡ µû¶ó Áõ»óÀÌ ¹«°Å¿öÁø´Ù. Åë»óÀûÀ¸·Î ±¸Åä, ¼³»ç, Ç÷¾Ð»ó½Â, ºü¸¥¸Æ, ¶¡³², È¥¼ö µîÀÇ Áõ»óÀÌ ³ªÅ¸³­´Ù.
  
  
¿µ¹® organic brain syndrome ÇÑ±Û ±âÁúÀû ³úÁõÈıº
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  ³úÀÇ ±âÁúÀûÀÎ(organic-:ÀÌ ¸»Àº ±â´ÉÀûÀÎ(functional)¿¡ ¹ÝÇϴ ¸»·Î½á) ¸ðµç °Ë»ç¸¦ ½ÃÇàÇϸ頾 ÀÌ»óÀ» ¹ß°ßÇÒ ¼ö Àִٴ ¶æÀÌ´Ù. ¹Ù²Ù¾î ¸»Çϸé, ±â´ÉÀûÀΠÀ̻󿡠ÀÇÇÑ ³úÁõÈıºÀº ¾î¶°ÇÑ °Ë»ç·Îµµ ÀÌ»óÀ» ¹ß°ßÇÒ ¼ö ¾øÀ¸³ª ºÐ¸íÈ÷ È¯ÀÚ¿¡°Ô ÀÌ»óÁõ»óÀÌ ³ªÅ¸³µÀ» ¶§ À̸¦ ¹­¾î¼­ ¸»ÇÑ´Ù. À̻󿡠ÀÇÇØ ½Å°æÇÐÀûÀΠÀÌ»óÀ» ³ªÅ¸³»´Â ÀÏ·ÃÀÇ º´ÀûÇö»óÀ» ¸ðµÎ ÅëÆ²¾î ¸»ÇÑ´Ù. ÀÌ º´Àº ÈçÈ÷ º¸¾Æ ¸¶Ä¡ Á¤½Åº´È¯ÀÚó·³ ¸»À» È¾¼³¼ö¼³Çϰí, ¾Ë¾ÆµéÀ» ¼ö ¾ø´Â ¸»À» Çϸç, ¶§·Î´Â ´Ù¸¥ »ç¶÷¿¡°Ô °ø°ÝÀûÀΠ¼ºÇâÀ» ³ªÅ¸³»±âµµ ÇÑ´Ù. ±×¸®°í ´Ù¸¥ »ç¶÷°ú µµÀúÈ÷ ±³·ù¸¦ ÇÒ ¼ö ¾ø´Â Á¤¼­¸¦ ³ªÅ¸³»±âµµ ÇÑ´Ù. ±×·¯³ª, ÀÌ º´ÀÌ ´Ù¸¥ Á¤½Åº´°ú ±¸º°µÇ´Â Æ¯Â¡ÀûÀΠÁõ»óÀº ¸ÕÀú, ÀǽÄÀǠȥŹÀÌ µ¿¹ÝµÇ´Â °æ¿ì°¡ ¸¹°í, ¶ÇÇÑ ±× Áõ»óÀÇ Á¤µµ°¡ º¯ÇѴٴ °ÍÀÌ´Ù. Áï, ¾ÆÄ§¿¡´Â Á¤»óÀûÀΠÇൿÀ» ÇÏ´Ù°¡ ¿ÀÈİ¡ µÇ¸é, ÀǽÄÀÌ Èå·ÁÁö¸é¼­ ¸»À» È¾¼³¼ö¼³ÇÑ´Ù¸é, À̴ ±âÁú¼º³úÁõÈıºÀÏ °¡´É¼ºÀÌ ³ô´Ù.
¿µ¹® Down syndrome ÇÑ±Û ´Ù¿îÁõÈıº
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  »ç¶÷ÀÇ 46°³ ¿°»öü Áß Á¦ 21¹ø ¿°»öüÀÇ ¼ö°¡ 1°³ ´õ ¸¹¾ÆÁö¹Ç·Î½á ³ªÅ¸³ª´Â º´ÀÌ´Ù. È¯ÀÚÀÇ »ý±è»õ°¡ ¸¶Ä¡ ¸ù°í »ç¶÷°ú ´à¾Ò´Ù ÇÏ¿© ÀÏ¸í ¸ù°íÁõ(mongolism)À̶ó°í ÇÏ¿´À¸³ª À߸øµÈ À̸§ÀÌ´Ù. ÀÌ º´Àº ¹Ýµå½Ã 21¹ø ¿°»öü°¡ 3°³°¡ µÇ´Â °æ¿ìÀ̿ܿ¡µµ 21¹ø ¿°»öüÀÇ ÀϺκÐÀÌ ´Ù¸¥ ¿°»öüÀÇ ÀϺκаú ±³È¯ÀÌ µÇ´Â translocationÇü µîÀÇ ´Ù¸¥ ¿°»öüÀ̻󿡼­µµ º¼ ¼ö°¡ ÀÖ´Ù. ¹ß»ý ºóµµ´Â Ãâ»ý¾Æ 700~1000¸íÁß 1¸í ²Ã·Î ³ªÅ¸³ª¸ç, ¿°»öü À̻󺴠Áß¿¡ °¡Àå ¸¹Àº °ÍÀ¸·Î ¾Ë·ÁÁ® ÀÖ´Ù. ÀÌ º´ÀÇ ¹ß»ýºóµµ´Â »ê¸ðÀÇ Ãâ»ê¿¬·É°ú ¹ÐÁ¢ÇÑ °ü°è°¡ ÀÖ¾î, 35¼¼ ÀÌÈİ¡ µÇ¸é ±âÇÏ ±Þ¼öÀûÀ¸·Î ÀÌ ÁúȯÀÚÀÇ Ãâ»ê¼ö°¡ Áõ°¡ÇÑ´Ù. ÀϹÝÀûÀ¸·Î ÀÌ Áúȯ¿¡ À־ ¾à 3ºÐÀÇ 1Àº ¸ðÄ£ÀÇ Ãâ»ê¿¬·É¿¡ ÀÇÁ¸ÇÏÁö ¾Ê°í, ³ª¸ÓÁö ¾à 3ºÐÀÇ 2´Â ¸ðÄ£ÀÇ ¿¬·É°ú Á÷Á¢ °ü·ÃÀÌ Àִ °ÍÀ¸·Î º¸°í ÀÖ´Ù. Áø´ÜÀº Æ¯Â¡ÀûÀΠ»ý±è»õ, Áï ¸ù°í »ç¶÷°°ÀÌ ´«²¿¸®°¡ À§·Î Ä¡ÄÑÁ® ÀÖ°í ´«°ÅÇ®ÀÌ µÎ²¨¿ì¸ç ÄàµîÀÌ ³·Àº Æ¯Â¡ÀûÀΠ¾ó±¼ ¸ð½À, ¶ÇÇÑ ±ÙÀ°ÀÇ ±äÀåµµ°¡ ÀúÇϵǰí Á¥À» ºü´Â Èû°ú ¿ïÀ½ ¼Ò¸®°¡ ¾àÇϸ砼չٴÚÀÇ Á¿츦 °¡¸£´Â ÇÑÁÙÀÇ ¼Õ±Ý(¿ø¼þÀ̿͠°°Àº ÇüÅÂÀÌ´Ù) µîÀǠƯ¡ÀûÀΠ¼Ò°ß¿¡ ÀÇÇØ º¸Á¶Áø´ÜÀ» Çϰí ÃÖÁ¾ÀûÀ¸·Î ¿°»öü ºÐ¼®¿¡ ÀÇÇØ È®ÁøÀ» ÇÑ´Ù. ÀÌ ´Ù¿îÁõÈıºÀǠȯÀڴ ´ë°³ Áö´ÉÀÌ ÀúÇϵǾî ÀÖ°í, ¿©·¯ °¡Áö Á¾·ùÀÇ ¼±Ãµ¼º ½ÉÀå±âÇüÀ» ¸¹ÀÌ µ¿¹ÝÇϰí ÀÖ´Ù.
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • glycoprotein
    ´ç´Ü¹éÁú
  • variant surface glycoprotein
    »óÀÌÇ¥¸é´ç´Ü¹éÁú
  • anginal syndrome
    Çù½ÉÁõÁõÈıº
  • anterior interosseous nerve syndrome
    ¾Õ»À»çÀ̽ŰæÁõÈıº, Àü¹æ°ñ°£½Å°æÁõÈıº
  • anterior spinal artery syndrome
    ¾Õô¼öµ¿¸ÆÁõÈıº
  • anterior tibial compartment syndrome
    Á¾¾Æ¸®¾ÕÄ­ÁõÈıº, ¾ÕÁ¤°­±¸È¹ÁõÈıº
  • anxiety syndrome
    ºÒ¾ÈÁõÈıº
  • aortic arch syndrome
    ´ëµ¿¸ÆÈ°ÁõÈıº, ´ëµ¿¸Æ±ÃÁõÈıº
  • apallic syndrome
    ´ë³ú°ÑÁú»ó½ÇÁõÈıº, ´ë³úÇÇÁú»ó½ÇÁõÈıº
  • Apert syndrome
    ¾ÆÆä¸£ÁõÈıº
  • Asherman¡¯s syndrome
    ¾Æ¼Å¸¸ÁõÈıº
  • auriculotemporal syndrome
    ±Ó¹ÙÄû°üÀÚÁõÈıº, À̰³ÃøµÎ½Å°æÁõÈıº
  • Ayerza syndrome
    ¾Æ¿¹¸£»çÁõÈıº
  • acquired immune deficiency syndrome
    ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
  • acquired immunodeficiency syndrome
    ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • glycoprotein
    ´ç´Ü¹éÁú
  • acquired immunodeficiency syndrome
    (¢¡AIDS) ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
  • syndrome of inappropriate antidiuretic hormone
    Ç×ÀÌ´¢È£¸£¸óºÎÀûÀýºÐºñÁõÈıº
  • syndrome
    ÁõÈıº
  • adrenogenital syndrome
    ºÎ½Å¼º±âÁõÈıº
  • afferent loop syndrome
    µéâÀÚÁõÈıº
  • Alport syndrome
    ¾ËÆ÷Æ®ÁõÈıº
  • Asherman's syndrome
    (¢¡ intrauterine synechia) ¾Æ¼Å¸¸ÁõÈıº
  • carpal tunnel syndrome
    ¼Õ¸ñ±¼ÁõÈıº, ¼ö±Ù°üÁõÈıº
  • cauda equina syndrome
    ¸»ÃÑÁõÈıº, ¸¶¹ÌÁõÈıº
  • compartment syndrome
    ±¸È¹ÁõÈıº
  • contact urticaria syndrome
    Á¢Ã˵ε巯±âÁõÈıº
  • cubital tunnel syndrome
    ÆÈ²ß±¼ÁõÈıº
  • Cushing's syndrome
    Äí½ÌÁõÈıº
  • dialysis disequilibrium syndrome
    Åõ¼®ºÒ±ÕÇüÁõÈıº
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • glycoprotein
    ´ç´Ü¹éÁú
  • variant surface glycoprotein
    »óÀÌÇ¥¸é´ç´Ü¹éÁú
  • abstinence syndrome
    (¢¡withdrawal syndrome) ±Ý´ÜÁõÈıº
  • acquired immune deficiency syndrome
    ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
  • acquired immunodeficiency syndrome
    ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
  • acute brain syndrome
    ±Þ¼º³úÁõÈıº
  • acute radiation syndrome
    ±Þ¼º¹æ»ç¼±ÁõÈıº
  • adhesive syndrome
    À¯ÂøÁõÈıº
  • adrenogenital syndrome
    ºÎ½Å¼º±âÁõÈıº
  • adrenosympathetic syndrome
    ºÎ½Å±³°¨½Å°æÁõÈıº
  • advanced sleep phase syndrome
    ÀüÁø¼ö¸éÀ§»óÁõÈıº
  • aeroadaptation syndrome
    Ç×°ø¼øÀÀÁõÈıº
  • alveolar hypoventilation syndrome
    ÆóÆ÷Àúȯ±âÁõÈıº
  • alveolar-capillary block syndrome
    ÆóÆ÷¸ð¼¼Ç÷°üÂ÷´ÜÁõÈıº
  • amnestic syndrome
    ±â¾ï»ó½ÇÁõÈıº
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Glycoprotein hormones, ligands
    ´ç´Ü¹éÁú(ÓØÓ±ÛÜòõ)È£¸£¸ó, ¸®°£µå
  • alpha1-acid glycoprotein
    ¾ËÆÄ-»ê´ç´Ü¹é
  • glycoprotein
    ´ç´Ü¹éÁú(ÓØÓ±ÛÜòõ).
  • glycoprotein
    ´ç´Ü¹éÁú(ÓØÓ±ÛÜòõ)
  • platelet glycoprotein
    Ç÷¼ÒÆÇ´ç´Ü¹é
  • Browns syndrome->superior oblique tendon sheath syndrome
    ºê¶ó¿îÁõÈıº
  • Cowdens syndrome = multiple hamartoma syndrome
    ´Ù¹ß¼º °ú¿ÀÁ¾ ÁõÈıº
  • ICE syndrome=iridocorneal endothelial syndrome
    ȫä°¢¸·³»ÇÇÁõÈıº
  • Lowes syndrome->oculocerebrorenal syndrome
    ·Î¿ìÁõÈıº
  • PIE syndrome => pulmonary infiltration with eosinophilia syndrome
    È£»ê±¸Áõ°¡¼º ÆóħÀ± ÁõÈıº
  • Q-T prolongation syndrome ; long Q-T syndrome
    Q-T°£°Ý ¿¬ÀåÁõÈıº.
  • Raeders syndrome=>painful Horners syndrome
    ·¹ÀÌ´õÁõÈıº
  • Steiners syndrome [=curtius syndrome, facial hemi
    ¾È¸é¹Ý(ÂÊ)ºñ´ëÁõ
  • UGH syndrome->uveitis-glaucoma-hemorrhage syndrome
    À¯Áö¿¡ÀÌÃëÁõÈıº
  • A-V syndrome
    A-VÁõÈıº
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • a-glycoprotein
  • alpha1-acid glycoprotein
    ¾ËÆÄ-»ê´ç´Ü¹é
  • glycoprotein
    ´ç´Ü¹éÁú(ÓØÓ±ÛÜòõ).
  • glycoprotein
    ´ç´Ü¹éÁú(ÓØÓ±ÛÜòõ)
  • membrane glycoprotein
    ¸·´ç´Ü¹é
  • platelet glycoprotein
    Ç÷¼ÒÆÇ´ç´Ü¹é
  • surface glycoprotein
    Ç¥¸é´ç´Ü¹é(Áú)(øúØüÓØÓ±ÛÜ)
  • angry back syndrome => excited skin syndrome
  • syndrome, Steiners [=curtius syndrome, facial hem
    ¾È¸é¹Ý(ÂÊ)ºñ´ëÁõ
  • abdominal muscle deficiency syndrome
    º¹±Ù°á¼ÕÁõÈıº(ÜÙÐÉÌÀáßñøý¦ÏØ).
  • absent pulmonary valve syndrome
    Æóµ¿¸ÆÆÇ°á¿©Áõ.
  • absent pulmonary valve syndrome
    Æóµ¿¸ÆÆÇ°á¿©Áõ.
  • absent testes syndrome
    °íȯ°á¿©ÁõÈıº
  • abstinence syndrome
    ±Ý´ÜÁõÈıº(Ð×Ó¨ñøý¦ÏØ).
  • acid aspiration syndrome
    À§»ê ÈíÀÔ ÁõÈıº
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Metabolic defect of steroid (Adrenogenital syndrome)
    ½ºÅ×·ÎÀ̵å´ë»ç°áÇÔ(ºÎ½Å»ý½Ä±âÁõÈıº)
    [¿¾ ¿ë¾î] ½ºÅ×·ÎÀ̵å´ë»ç°áÇÔ(ºÎ½Å»ý½Ä±âÁõÈıº)
  • Syndrome
    ÁõÈıº
    [¿¾ ¿ë¾î] ÁõÈÄ
  • Syndrome (Down)
    ÁõÈıº (´Ù¿îÁõÈıº)
    [¿¾ ¿ë¾î] ÁõÈÄ
´ëÇѱâ»ýÃæÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Loeffler's syndrome
    ·ÚÇ÷¯ÁõÈıº
  • variable surface glycoprotein (VSG)
    º¯À̼ºÇ¥¸é´ç´Ü¹éÁú
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • glycoprotein
    ´ç´Ü¹éÁú(ÓØÓ±ÛÜòõ)
  • Tamm-Horsfall glycoprotein
    Ž-È£¸£½ºÆú ´ç´Ü¹éÁú(ÓØÓ±ÛÜòõ)
  • Crigler-Najjar syndrome
    Å©¸®±Û·¯-³ª¾ß¸£ ÁõÈıº(ñøý¦ÏØ)
  • Down's syndrome
    ´Ù¿î ÁõÈıº(ñøý¦ÏØ) (ÔÒ) mongolism
  • ectopic hormone syndrome
    À̼Ò(ì¶á¶) È£¸£¸ó ÁõÈıº(ñøý¦ÏØ)
  • Fanconi's syndrome
    ÆÇÄÚ´Ï ÁõÈıº(ñøý¦ÏØ)
  • fragile X syndrome
    Ãë¾à(öªå°) X ÁõÈıº(ñøý¦ÏØ)
  • general adaptation syndrome
    ÀÏ¹Ý ÀûÀÀ ÁõÈıº(ìéÚõ îêëëñøý¦ÏØ)
  • Hunter's syndrome
    ÇåÅÍ ÁõÈıº(ñøý¦ÏØ)
  • Hurler's syndrome
    Çæ·¯ ÁõÈıº(ñøý¦ÏØ)
  • Lesch-Nyhan syndrome
    ·¹½¬-´ÏÇÑ ÁõÈıº(ñøý¦ÏØ)
  • Pendred's syndrome
    Ææµå·¹µå ÁõÈıº(ñøý¦ÏØ)
  • phytanic acid storage syndrome
    ÇÇź»ê(ß«) ÃàÀû ÁõÈıº(õëîÝñøý¦ÏØ)
  • Sanfillipo's syndrome
    ¼¾Çʸ®Æ÷ ÁõÈıº(ñøý¦ÏØ)
  • simian acquired immune deficiency syndrome
    ¿ø¼þÀÌ ÈÄõ¼º¸é¿ª°áÇÌÁúȯ(ý­ô¸àõØóæ¹ÌÀù¹òðü´)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • glycoprotein
    ´ç´Ü¹éÁú
  • Banti's syndrome
    ¹ÝƼÁõÈıº
  • battered child syndrome
    ÇÇÇÐ´ë¾ÆÁõÈıº
  • Behcet's syndrome
    º£Ã¼Æ®ÁõÈıº
  • blind loop syndrome
    ¸Í°èÁ¦ÁõÈıº
  • cauda equina syndrome
    ¸¶¹ÌÁõÈıº
  • cord compression syndrome
    ô¼ö¾Ð¹ÚÁõÈıº
  • Cushing's syndrome
    Äí½ÌÁõÈıº
  • double crush syndrome
    ÀÌÁߺмâÁõÈıº
  • empty sella syndrome
    °øÅÍŰ¾ÈÁõÈıº
  • facet syndrome
    ôÃßÈİüÀýÁõÈıº
  • fetal distress syndrome
    žưï¶õÁõÈıº
  • gonadal dysgenesis; Turner's syndrome
    ¼º¼±À̹߻ýÁõ, ÅͳÊÁõÈıº
  • Guillain-Barre syndrome
    ±æ¶û¹Ù·¹ÁõÈıº
  • hypogenetic lung syndrome
    Àú¹ß»ýÆóÁõÈıº
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
MS Maffuci syndrome; maladjustment score; mandibular series; Marfan syndrome; Marie-Strumpell [syndrome...
SGP serine glycerophosphatide; sialoglycoprotein; Society of General Physiologists; soluble glycoprotein...
CS calf serum; campomelic syndrome; carcinoid syndrome; cardiogenic shock; caries-susceptible; carotid ...
PCS palliative care service; Patient Care System; patterns of care study; pelvic congestion syndrome; ph...
PPS Personal Preference Scale; physician, patient and society [course]; polyvalent pneumococcal polysacc...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
CDGS Carbohydrate Deficient Glycoprotein Syndrome
"syndrome X" syndrome
AGP 1-Acid glycoprotein
GP 2-glycoprotein
GP I glycoprotein I
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • A-V syndrome
    A-V ÁõÈıº
  • Aarskog syndrome
    ¾Æ¸£½ºÄÚ±× ÁõÈıº
    À¯Àü¼º ÁõÈıºÀÇ Çϳª·Î X-¿¬°ü¼º ÇüÁú·Î À¯ÀüµÈ´Ù. Ư¡À¸·Î´Â ¾È±¸ °Ý¸®Áõ, ³ÐÀº À­ ÀÔ¼ú, ¼î¿Ã, ÀÛÀº ¼Õ µîÀÌ ÀÖ´Ù. ¾È¸é ¼º±â Çü¼º Àå¾Ö
  • Aase syndrome
    ¾ÆÁî ÁõÈıº
    °æ¹ÌÇÑ ¼ºÀå Áö¿¬, ÀúÇü¼º ºóÇ÷, ´Ù¾çÇÑ ¹éÇ÷±¸ °¨¼ÒÁõ, ¼¼ °³·Î °¥¶óÁø ¾öÁö¹ß°¡¶ô, Á¼Àº ¾î±ú, ´ÊÀº õ¹® Æó¼â, ¾ðûÀÌ, ±¸°³ ÆÄ¿­, ¸Á¸·º´Áõ µîÀ» Ư¡À¸·Î ÇÏ´Â ÁõÈıºÀ¸·Î¼­ ¿­¼ºÀ¸·Î À¯ÀüµÇ´Â °ÍÀ¸·Î »ý°¢µÈ´Ù.
  • abnormal laterality syndrome
    ÁÂ¿ì ºñ´ëĪ ÀÌ»ó ÁõÈıº
    ½ÉÀå¿¡¼­ Á¤»óÀûÀÎ ÁÂ¿ì ´ëĪÀÌ µÚ¹Ù²î°Å³ª ºÒ¿ÏÀüÇÑ °æ¿ì·Î¼­, ÁÂÃøÀ̳ª ¿ìÃøÇüÀ¸·Î ´ëĪÀÎ °æ¿ì°¡ ÀÖ°í À̵鿡¼­ ¿©·¯ °¡Áö ½ÉÀå ±âÇüÀÌ µ¿¹ÝµÇ´Âµ¥ ÀÌ·¯ÇÑ °æ¿ì¸¦ ½ÉÀåÀÇ ÁÂ¿ì ºñ´ëĪ ÀÌ»ó ÁõÈıºÀ̶ó ÇÑ´Ù. À̵é Áúȯ¿¡¼­´Â ½ÉÀå »Ó ¾Æ´Ï¶ó ÁÖ ±â°üÁö¿Í »óÆóµ¿¸ÆÀÇ À§Ä¡ °ü°è ¹× ÆóÀÇ ºÐ¿±, °£°ú ºñÀåÀÇ ÇüÅ ¹× À§Ä¡°¡ ´Þ¶óÁö¸ç ƯÈ÷ ºñÀåÀÌ ¾ø´Â ¹«ºñÁõ
  • absent pulmonary valve syndrome
    Æó µ¿¸Æ ÆÇ °á¿© ÁõÈıº
    ´Üµ¶À¸·Î ÀϾ´Â °æ¿ì´Â ±ØÈ÷ µå¹°¸ç, ½É½Ç Áß°Ý °á¼Õ, ¿ì½Ç ´©µÎºÎ ÇùÂø¿¡ ÇÕº´ÇÏ´Â °æ¿ì°¡ ºñ±³Àû ¸¹´Ù. Áï Fallot 4ÁõÈÄÀÇ ÇÕº´ ±âÇüÀ¸·Î ³ªÅ¸³­´Ù. ÀÌ °æ¿ì ÁÂ¿ì Æóµ¿¸ÆÀÇ È®´ë, ¥±À½ Æóµ¿¸Æ ¼ººÐÀÇ ¿ÏÀü ¼Ò½Ç, ÇÇÄ¡°¡ ³·Àº È®Àå±â ÀâÀ½À» ³ªÅ¸³½´Ù. À̰ÍÀ» µ¿¹ÝÇÑ Fallot 4ÁõÈÄ´Â À¯¾Æ±â¿¡ ¿ïÇ÷¼º ½ÉºÎÀüÀ» ÀÏÀ¸Å°±â ½±´Ù.
  • absent testes syndrome
    °íȯ °á¿© ÁõÈıº
  • abstinence syndrome
    ±Ý´Ü ÁõÈıº
  • acid aspiration syndrome
    À§»ê ÈíÀÔ ÁõÈıº
  • acquired immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª °áÇÌ ÁõÈıº
    1. ÇöÀúÇÑ ¸é¿ª °áÇ̰ú ÇÔ²² ±âȸ°¨¿°, ¼Ó¹ß¼º ¾Ï ¹× ½Å°æ°è Áõ¼¼°¡ µ¿¹Ý. ¹ÙÀÌ·¯½º ÀÚü¿¡ ÀÇÇÑ º´º¯°ú ¸é¿ª´É·Â ÀúÇÏ¿¡ µû¸¥ ±âȸ °¨¿° µîÀÇ ÀÌÂ÷Àû º´º¯ÀÇ µÎ °¡Áö·Î ´ëº°. HIV¿¡ ÀÇÇØ ¹ß»ýµÇ´Â ÁúȯÀ¸·Î ½Å°æ°è°¡ Áß¿ä Ç¥ÀûÁß Çϳª. ¹ÙÀÌ·¯½º¿¡ °¨¿°µÈ »ç¶÷ÀÇ 40% Á¤µµ°¡ Áúº´ÀÌ ¹ß»ý. ¹ÙÀÌ·¯½ºÀÇ Á÷Á¢ÀûÀÎ ¿µÇâ¿¡ ÀÌÇÑ º´º¯À¸·Î´Â ¸²ÇÁ±¸¼º ¼ö¸·¿°°ú HIV ³ú¿° µîÀÌ ÀÖÀ½. 2. ÈÄõ¼º ¸é¿ª°áÇÌÁõ. Àΰ£ ¸é¿ª°áÇÌ ¹ÙÀÌ·¯½º
  • acquired immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª°áÇÌ ÁõÈıº
  • acute HIV infection syndrome
    ±Þ¼º ÀÎü ¸é¿ª °áÇÌ ¹ÙÀÌ·¯½º Áúȯ °¨¿° ÁõÈıº
  • acute muscle compartment syndrome
    ±Þ¼º ±Ù±¸¿ª ÁõÈıº
    °ñÀý, ºÎÁ¾, ÃâÇ÷¿¡ ´ëÇÑ ¼Ó¹ß¼ºÀ¸·Î ±Ù±¸¿ª³»ÀÇ ºÎÇǰ¡ ±Þ¼ºÀ¸·Î Áõ°¡ÇÏ¿© ¸ð¼¼Ç÷°üÀÌ ¾Ð¹ÚÀ» ¹Þ¾Æ ¹ß»ýÇÑ ±Ù±¸¿ª ÁõÈıº.
  • acute respiratory distress syndrome
    ±Þ¼º È£Èí°ï¶õ ÁõÈıº
    ¼ºÀΠȣÈíºÎÀü, ¼ï Æó, ¹Ì¸¸¼º ÆóÆ÷ ¼Õ»ó, ±Þ¼º ÆóÆ÷ ¼Õ»ó, ¿Ü»ó¼º ÀæÀº Æó µîÀÌ ÀÖ´Ù. ¹Ì¸¸¼ºÀ¸·Î ÆóÆ÷ ¸ð¼¼Ç÷°üÀÌ ¼Õ»óÀ» ÀÔ¾î ÃÊ·¡µÇ¸ç ÀÓ»óÀûÀ¸·Î´Â ±Þ°ÝÈ÷ »ý±ä ½ÉÇÑ È£Èí°ï¶õ, ºó¸Æ, û»öÁõ ¹× »ê¼Ò¿ä¹ý¿¡ ¹ÝÀÀÇÏÁö ¾Ê´Â µ¿¸Æ Àú»ê¼ÒÁõ µîÀ» Ư¡À¸·Î ÇÑ´Ù.
  • adaptation syndrome
    ÀûÀÀÁõÈıº, Á¶ÀýÁõÈıº
    »ýü¿¡ ¿Ü·ÂÀÌ °¡ÇØÁö¸é, ºÎ½Å ÇÇÁú°è, ³úÇϼöü°¡ Ȱµ¿ÇÏ¿© ºÎ½Å ÇÇÁú È£¸£¸óÀÌ °ú·® ºÐºñµÇ¾î ¿Ü·Â¿¡ ÀúÇ×Çϴµ¥, ÀÌ È°µ¿ÀÇ Á¤µµ¿¡ µû¶ó °¢Á¾ ÁúȯÀÌ À¯¹ßµÈ´Ù´Â °³³ä.
  • adrenal Cushing's syndrome
    ºÎ½Å Äí½Ì ÁõÈıº
    °úÀ×ÀÇ ÄÚ¸£Æ¼ÄÚÀ̵忡 ÀÇÇØ ³ªÅ¸³ª´Â Áõ»óÀ» ÀÏÄÃÀ¸¸ç ´ë°³ ´çÁú ÄÚ¸£Æ¼ÄÚÀ̵åÀÇ °ú¿ë·®¿¡ ÀÇÇØ »ý±â°í ºÎ½Å ÇÇÁúÀÇ ÄÚ¸£Æ¼ÄÚÀÌµå »ý»ê¿¡ ÀÇÇÑ °æ¿ì´Â µå¹°´Ù. ÀÚ¿¬ ¹ß»ýÀÇ Äí½Ì ÁõÈıºÀº ¼ºÀÎÀÇ °æ¿ì ´ÙÀ½°ú °°Àº °¡´É¼ºÀÌ ÀÖ´Ù. 1
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
carbohydrate-deficient glycoprotein syndrome <syndrome> An inborn error of carbohydrate metabolism manifesting as a genetic multisystem disorder of autosomal recessive inheritance. A predominant feature is severe central and peripheral nervous system involvement resulting in psychomotor retardation, seizures, cerebellar ataxia, and other symptoms which include growth retardation, retinitis pigmentosa, hypothyroidism, and fatty liver. The notable biochemical feature is the deficiency of a large number of blood glycoproteins and decreased activities of various blood coagulation factors.
(12 Dec 1998)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
a1-acid glycoprotein <biology> Plasma protein of mammals and birds, 38% carbohydrate. In humans a single chain glycoprotein of 39 kD. Increased levels are associated with inflammation, pregnancy and various diseases.
(18 Nov 1997)
acetylgalactosaminyl-O-glycosyl-glycoprotein beta-1,3-N-acetylglucosaminyltransferase <enzyme> Forms oligosaccharide core class 3 (glcnac beta 1-3galnac) in mucins and various glycoproteins
Registry number: EC 2.4.1.147
Synonym: udp-glcnac-galnac-r beta 3-acetylglucosaminyltransferase, agggag-transferase
(26 Jun 1999)
amyloidogenic glycoprotein <protein> An integral membrane glycoprotein of the brain and related to the Drosophila vnd gene product. A precursor of _ amyloid, that accumulates in Alzheimer's disease and Down's syndrome.
See: amyloid precursor protein.
(18 Nov 1997)
b2-glycoprotein II <enzyme> A glycine-rich, heat-labile beta-glycoprotein found in blood. It is a proactivator of complement 3 in the alternate pathway of complement activation. Factor b is converted by factor d to c3 convertase.
Registry number: EC 3.4.21.47
(12 Dec 1998)
beta-1,3-galactosyl-0-glycosyl-glycoprotein beta-1,3-N-acetylglucosaminyltransferase <enzyme> Capable of adding a glcnac residue to g1cnacman(3)g1cnac; from mung bean seedlings
Registry number: EC 2.4.1.146
Synonym: n-acetylglucosaminyltransferase II, gal3-(glcnac6)galnac-mucin (glcnac--gal)3-glcnactransferase
(26 Jun 1999)
beta-1,3-galactosyl-O-glycosyl-glycoprotein beta-1,6-acetylglucosaminyl transferase <enzyme> With EC 2.4.1.148 this is called beta6-glcnac-transferase b
Registry number: EC 2.4.1.102
Synonym: gal3-galnac-mucin-6-glcnac transferase, udp-glcnac-gal1-3galnac-r-(glcnac to galnac)-beta1-6glcnac transferase, core 2 glcnac transferase, core 2-n-acetylglucosaminyltransferase, core 2 beta6-gn-t
(26 Jun 1999)
beta-1,4-mannosyl-glycoprotein beta-1,4-N-acetylglucosaminyltransferase <enzyme> Induced in preneoplastic stage of liver carcinogenesis promoted by orotic acid in rats; adds "bisecting n-acetylglucosaminyl residue in beta 1,4 linkage to the beta-linked mannose of the core of asparagine-linked oligosaccharides
Registry number: EC 2.4.1.144
Synonym: n-acetylglucosaminyltransferase III, udpgnac-glycopeptide beta4-n-acetylglucosaminyl transferase III, udpgnac-magtransferase III, udp-n-acetylglucosamine-beta-d-mannoside beta-1,4-n-acetylglucosaminyltransferase III
(26 Jun 1999)
variable surface glycoprotein <protein> One of a battery of antigenicdeterminants expressed by a microorganism to elude immune detection.
(09 Oct 1997)
mannosyl-glycoprotein endo-beta-n-acetylglucosaminidase <enzyme> A group of related enzymes responsible for the endohydrolysis of the di-n-acetylchitobiosyl unit in high-mannose-content glycopeptides and glycoproteins.
Chemical name: Glycopeptide-D-mannosyl-N(4)-(N-acetyl-D-glucosaminyl)2-asparagine 1,4-N-acetyl-beta-glucosaminohydrolase
Registry number: EC 3.2.1.96
(12 Dec 1998)
glycine-rich beta-glycoprotein <enzyme> A glycine-rich, heat-labile beta-glycoprotein found in blood. It is a proactivator of complement 3 in the alternate pathway of complement activation. Factor b is converted by factor d to c3 convertase.
Registry number: EC 3.4.21.47
(12 Dec 1998)
glycoprotein <protein> Proteins with covalently attached sugar units, either bonded via the OH group of serine or threonine O glycosylated) or through the amide NH2 of asparagine (N glycosylated).
Includes most secreted proteins (serum albumin is the major exception) and proteins exposed at the outer surface of the plasma membrane. Sugar residues found include: mannose, N acetyl glucosamine, N acetyl galactosamine, galactose, fucose and sialic acid.
(18 Nov 1997)
glycoprotein endo-alpha-1,3-mannosidase <enzyme> An endomannosidase; cleaves glucosyl alpha1-3-mannose from monoglucosylated oligosaccharide (glcman(7-9)glcnac) of the glycoprotein produced in the golgi membrane
Registry number: EC 3.2.1.130
Synonym: glucosyl mannosidase
(26 Jun 1999)
glycoprotein glycosyltransferase <enzyme> Enzymes which add monosaccharides from nucleoside mono-or diphosphate monosaccharides onto glycoproteins
Registry number: EC 2.4.1.-
(26 Jun 1999)
glycoprotein hormones, alpha subunit A non-covalently bound subunit of the glycoprotein hormones tsh, fsh, lh, and hcg which originates in the anterior pituitary gland and placenta. This subunit is virtually identical in structure and indistinguishable by radioimmunoassay in all of the above glycoproteins. It is present in both men and women, but is elevated in postmenopausal women and in patients with hypothyroidism, uraemia and malignant tumours. The alpha subunit may be involved directly in recognition of certain receptors.
(12 Dec 1998)
glycoprotein hormone-specific N-acetylgalactosamine transferase <enzyme> Transfers galnac to the terminal glcnac moieties of glcnac2man3glcnac2asn
Registry number: EC 2.4.1.-
Synonym: ghs-acgalnh2 transferase, glycoprotein hormone galnac transferase, glycoprotein hormone - n-acetylgalactosaminyltransferase
(26 Jun 1999)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Carbohydrate-Deficient Glycoprotein Syndrome - »õâ An inborn error of carbohydrate metabolism manifesting as a genetic multisystem disorder of autosomal recessive inheritance. A predominant feature is severe central and peripheral nervous system involvement resulting in psychomotor retardation, seizures, cerebellar ataxia, and other symptoms which include growth retardation, retinitis pigmentosa, hypothyroidism, and fatty liver. The notable biochemical feature is the deficiency of a large number of blood glycoproteins and decreased activities of various blood coagulation factors.
    Synonyms : Carbohydrate Deficient Glycoprotein Syndrome, Carbohydrate-Deficient Glycoprotein Syndromes, Glycoprotein Syndrome, Carbohydrate Deficient, Glycoprotein Syndromes, Carbohydrate-Deficient, Syndrome, Carbohydrate-Deficient Glycoprotein
ÇÑ¿µ/¿µÇÑ »çÀü À¯»ç °Ë»ö °á°ú : 12 ÆäÀÌÁö: 1
  • ¿µ¹®
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    ´ç´Ü¹é(Áú)(Á¡¾×¼Ò ¹× ¿¬°ñÀÇ ÁÖ¼ººÐ)
  • Down's syndrome
    ´Ù¿î ÁõÈıº(Mongolism)
  • HunterRussel syndrome
    ÇåÅÍ ·¯¼¿ ÁõÈıº(À¯±â ¼öÀº Áßµ¶)
  • Reye('s) syndrome
    ¶óÀÌ ÁõÈıº(¼Ò¾Æ¿¡°Ô ÈçÈ÷ ÀÖ´Â ³úÀå¾Ö)
  • behcets syndrome
    º£ÀÌú´(´«,ÀÔÀÇ Á¡¸·,À½ºÎ¿¡ º´ÀÌ »ý±è)
  • empty nest syndrome
    (Á¤ÀÇ)¼ºÀåÇÑ ÀڽĵéÀÌ ´Ù ¶°³ª¹ö¸° ³ë³â ºÎºÎ¿¡°Ô ÈçÈ÷ ³ªÅ¸³ª´Â ÁõÈıº(Á¤½ÅÀû ºÒ¾ÈÁ¤°ú ¿ì¿ïÁõÀ» ¼ö¹ÝÇÏ´Â ÇãÅ»°¨)
  • general adaptation syndrome
    ¹üÀûÀÀ ÁßÈıº
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    °í¾Ð ½Å°æ ÁõÈıº
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    º£Æ®³² ÈÄ ÁõÈıº
  • premenstrual syndrome
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  • respiratory distress syndrome
    (½Å»ý¾ÆÀÇ)È£Èí Àå¾Ö ÁõÈıº
  • syndrome
    ÁõÈıº;ÇൿÇü
ÀÌ ¾Æ·¡ ºÎÅÍ´Â °á°ú°¡ ¾ø½À´Ï´Ù.
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