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beta-alanine <chemical> Beta-alanine. An amino acid formed in vivo by the degradation of dihydrouracil and carnosine. Since neuronal uptake and neuronal receptor sensitivity to beta-alanine have been demonstrated, the compound may be a false transmitter replacing gaba. A rare genetic disorder, hyper-beta-alaninaemia, has been reported.
Chemical name: beta-Alanine
(12 Dec 1998)
beta-alanine-pyruvate aminotransferase <enzyme> An enzyme that reversibly transfers the amino group of beta-alanine to paruvate, thus producing l-alanine and malonate saemialdehyde. A deficiency of this enzyme is believed to be the cause of hyper-beta-alaninaemia.
(05 Mar 2000)
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  • beta-Alanine - »õâ An amino acid formed in vivo by the degradation of dihydrouracil and carnosine. Since neuronal uptake and neuronal receptor sensitivity to beta-alanine have been demonstrated, the compound may be a false transmitter replacing GAMMA-AMINOBUTYRIC ACID. A rare genetic disorder, hyper-beta-alaninemia, has been reported.
    Synonyms : beta-Alanine Hydrochloride, beta-Alanine, Calcium Salt (2:1), beta-Alanine, Monopotassium Salt, beta-Alanine, Monosodium Salt, 3 Aminopropionic Acid, Hydrochloride, beta-Alanine, beta Alanine, beta Alanine Hydrochloride, beta Alanine, Monopotassium Salt
  • beta-Alanine-Pyruvate Transaminase - »õâ A PYRIDOXAL PHOSPHATE containing enzyme that catalyzes the transfer of an amino group from L-ALANINE to 3-oxopropanoate to generate PYRUVATE and BETA-ALANINE.
    Synonyms : beta-Alanine - Pyruvate Transaminase, beta-Alanine Pyruvate Aminotransferase, Aminotransferase, beta-Alanine Pyruvate, Pyruvate Aminotransferase, beta-Alanine, Transaminase, beta-Alanine-Pyruvate, beta Alanine Pyruvate Aminotransferase
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