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  • arylsulfatase A
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  • arylsulfatase a deficiency
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  • arylsulfatase A
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  • arylsulfatase a deficiency
    ¾Æ¸±¼³ÆÄŸÁ¦ A °áÇÌÁõ(¡­ÌÀù¹ñø)
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arylsulfatase <enzyme> An enzyme that cleaves phenol sulfates, including cerebroside sulfates (i.e., a phenol sulfate + H2O &rarr; a phenol + sulfate anion). Some arylsulfatases are inhibited by sulfate (type II) and some are not (type I).
Synonym: sulfatase.
(05 Mar 2000)
arylsulfatases <enzyme> Enzymes that catalyze the hydrolysis of a phenol sulfate to yield a phenol and sulfate. Arylsulfatase a, b, and c have been separated. A deficiency of arylsulfatases is one of the causes of metachromatic leukodystrophy (leukodystrophy, metachromatic).
Chemical name: Aryl-sulfate sulfohydrolase
Registry number: EC 3.1.6.1
(12 Dec 1998)
arylsulfate sulfotransferase <enzyme> From a human intestinal bacterium; catalyses the transfer of the sulfate group of phenylsulfate esters to phenolic compounds
Registry number: EC 2.8.2.22
Synonym: asstase, arylsulfate-phenol sulfotransferase
(26 Jun 1999)
arylsulfonates Organic sulfonic acid esters or salts which contain an aromatic hydrocarbon radical.
(12 Dec 1998)
arylsulfonic acids Organic sulfonic acid derivatives which contain an aromatic hydrocarbon radical.
(12 Dec 1998)
arylsulfotransferase <enzyme> A sulfotransferase that catalyses the sulfation of a phenol in the presence of 3'-phosphoadenylylsulfate as sulfate donor to yield an aryl sulfate and adenosine 3',5'-bisphosphate. A number of aromatic compounds can act as acceptors; however, organic hydroxylamines are not substrates. Sulfate conjugation by this enzyme is a major pathway for the biotransformation of phenolic and catechol drugs as well as neurotransmitters.
Chemical name: 3'-Phosphoadenylylsulfate:phenol sulfotransferase
Registry number: EC 2.8.2.1
(12 Dec 1998)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 4 ÆäÀÌÁö: 1
  • Arylsulfatases - »õâ Enzymes that catalyze the hydrolysis of a phenol sulfate to yield a phenol and sulfate. Arylsulfatase A, B, and C have been separated. A deficiency of arylsulfatases is one of the causes of metachromatic leukodystrophy (LEUKODYSTROPHY, METACHROMATIC). EC 3.1.6.1.
    Synonyms : Arylsulphatases, Pseudo Arylsulfatase A
  • Arylsulfonates - »õâ Organic sulfonic acid esters or salts which contain an aromatic hydrocarbon radical.
    Synonyms : Aryl Sulfonates, Sulfonates, Aryl
  • Arylsulfonic Acids - »õâ Organic sulfonic acid derivatives which contain an aromatic hydrocarbon radical.
    Synonyms : Acids, Arylsulfonic
  • Arylsulfotransferase - »õâ A sulfotransferase that catalyzes the sulfation of a phenol in the presence of 3'-phosphoadenylylsulfate as sulfate donor to yield an aryl sulfate and adenosine 3',5'-bisphosphate. A number of aromatic compounds can act as acceptors; however, organic hydroxylamines are not substrates. Sulfate conjugation by this enzyme is a major pathway for the biotransformation of phenolic and catechol drugs as well as neurotransmitters. EC 2.8.2.1.
    Synonyms : Acetaminophen Sulphotransferase, Aryl Sulfotransferase, Catecholamine Sulfotransferase A, Catecholamine Sulfotransferase B, Dopamine Sulfotransferase, Flavonoid Sulfotransferase, Phenol Sulfokinase, Phenol Sulfotransferase M, Phenol Sulfotransferase P
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arylsulfatase B Lysosomal enzyme deficient in MPS VI.
Ãâó: www.mpssociety.org/lib-glossary.html
arylsulfatase A The lack of this enzyme results in the toxic accumulation of sulfatide deposits in metachromatic leukodystrophy, leading to demyelination of the CNS.
Ãâó: www.myelin.org/glossary.htm
arylsulfatase B The enzyme, or tiny cellular machine, that people with MPS VI don't have enough of. The enzyme works within the lysosomes of every cell to break down and recycle a specific kind of material
Ãâó: www.maroteaux-lamy.com/pc/about/Glossary.asp
arylsulfatase [EC 3.1.6.1] any of a group of enzymes of the hydrolase class that catalyze the cleavage of sulfate residues from sulfate esters; physiological substrates are generally sulfolipids or sulfated polysaccharides, while in vitro substrates include aryl or alkyl sulfates. Called also sulfatase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
arylsulfatase A deficiency metachromatic leukodystrophy.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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