| ASAS | argininosuccinate synthetase |
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| ASL | antistreptolysin; argininosuccinate lyase |
| ASS | acute serum sickness; acute spinal stenosis; anterior superior spine; argininosuccinate synthetase |
| ASSP | argininosuccinate synthetase pseudogene |
| ASSX | argininosuccinate synthetase pseudogene |
| ASL | Argininosuccinate lyase |
|---|---|
| AS | Argininosuccinate synthetase |
| AL | argininosuccinate lyase |
| NO Synthase | nitric oxide synthase |
| iNOS | 1.Inducible NO synthase |
| argininosuccinate synthase | <enzyme> An enzyme of the urea cycle that catalyses the formation of argininosuccinic acid from citrulline and aspartic acid in the presence of ATP. Absence or defect of this enzyme causes the metabolic disease citrullinaemia in man. Chemical name: L-Citrulline:L-aspartate ligase (AMP-forming) Registry number: EC 6.3.4.5 (12 Dec 1998) |
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| argininosuccinate lyase | <enzyme> An enzyme of the urea cycle which splits argininosuccinate to fumarate plus arginine. Its absence leads to the metabolic disease argininosuccinic acidemia in man. Chemical name: N-(L-Argininosuccinate) arginine-lyase Registry number: EC 4.3.2.1 (12 Dec 1998) |
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| abequose synthase | <enzyme> Converts cdp-4-keto-3,6-dideoxy-d-glucose to cdp-3,6-dideoxy-d-galactose (cdp-abequose); requires NADPH, analogous to udp-glucose-4-epimerase Registry number: EC 5.1.3.- Synonym: rfbj gene product (26 Jun 1999) |
| acetoacetyl-acyl carrier protein synthase | <enzyme> E coli enzyme, that catalyses condensation of malonyl-acyl carrier protein plus acetyl-acyl carrier protein; not inhibited by cerulenin Registry number: EC 2.3.1.- Synonym: acetoacetyl-acp synthase (26 Jun 1999) |
| acetolactate synthase | <enzyme> A flavoprotein that catalyses the formation of acetolactate from 2 moles of pyruvate in the biosynthesis of valine and the formation of acetohydroxybutyrate from pyruvate and alpha-ketobutyrate in the biosynthesis of isoleucine. Chemical name: Acetolactate pyruvate-lyase (carboxylating) Registry number: EC 4.1.3.18 (12 Dec 1998) |
| acridone synthase | <enzyme> Catalyses the condensation of n-methylanthraniloyl-CoA and 3 malonyl-CoA to produce 1,3-dihydroxy-n-methylacridone Registry number: EC 2.3.1.- (26 Jun 1999) |
| acyl-malonyl-ACP synthase | <enzyme> An enzyme condensing malonyl-ACP and acyl-cys-protein to 3-oxoacyl-ACP + cys-protein + CO2, and similar reactions, as steps in fatty acid synthesis; cys-protein is also a part of the fatty acid synthase complex. Synonym: acyl-malonyl-ACP synthase, beta-ketoacyl-ACP synthase. (05 Mar 2000) |
| adenylosuccinate synthase | <enzyme> A carbon-nitrogen ligase. During purine ribonucleotide biosynthesis, this enzyme catalyses the synthesis of adenylosuccinate from GTP, imp, and aspartate with the formation of orthophosphate and GDP. Chemical name: IMP:L-aspartate ligase (GDP-forming) Registry number: EC 6.3.4.4 (12 Dec 1998) |
| adenylylosuccinate synthase | <enzyme> A carbon-nitrogen ligase. During purine ribonucleotide biosynthesis, this enzyme catalyses the synthesis of adenylosuccinate from GTP, imp, and aspartate with the formation of orthophosphate and GDP. Chemical name: IMP:L-aspartate ligase (GDP-forming) Registry number: EC 6.3.4.4 (12 Dec 1998) |
| agropine synthase | <enzyme> Final enzyme in the three enzyme pathway for agropine synthesis; cyclises deoxymannityl-glutamine to the lactone, agropine Registry number: EC 4.2.1.- Synonym: ags gene product (26 Jun 1999) |
| alkylglycerone-phosphate synthase | <enzyme> Replaces the acyl moiety of acyldhap with a long chain fatty alcohol; intact alcohol including the oxygen atom is incorporated into alkyl-dhap Registry number: EC 2.5.1.26 Synonym: adhps, alkyl-dihydroxyacetone phosphate synthase, alkyl-dhap synthase, alkyldihydroxyacetone phosphate synthetase, acylglycerone-3-phosphate-long chain-alcohol o-3-phospho-2-oxopropanyl transferase, alkyldihydroxyacetonephosphate synthase (26 Jun 1999) |
| aminoadipic d-saemialdehyde synthase | <enzyme> A bifunctional enzyme used in lysine degradation; it has a lysine:alpha-ketoglutarate reductase activity as well as a saccharopine dehydrogenase activity. A deficiency of this enzyme results in familial hyperlysinaemia. (05 Mar 2000) |
| aminoadipic saemialdehyde synthase | <enzyme> Bifunctional enzyme with both lysine-ketoglutarate reductase (EC 1.5.1.8) and saccharopine dehydrogenase (EC 1.5.1.9) activities Registry number: EC 1.5.1.- Synonym: aasa synthase (26 Jun 1999) |
| aminodeoxychorismate synthase | <enzyme> From E coli; probably catalyses the conversion of chorismate to 4-amino-4-deoxychorismate; see also paba protein Registry number: EC 2.6.1.- Synonym: pabb gene product, adc synthase (26 Jun 1999) |
| amylopectin synthase | <enzyme> From eimeria tenella; catalyses udpglucose alpha 1,4-glucan alpha-4-glucosyltransferase forming amylopectin, similar to glycogen synthase in eukaryotes Registry number: EC 2.4.1.- (26 Jun 1999) |
| anthranilate synthase | <enzyme> An enzyme that catalyses the formation of anthranilate (o-aminobenzoate) and pyruvic acid from chorismate and glutamine. Anthranilate is the biosynthetic precurser of tryptophan and numerous secondary metabolites, including inducible plant defense compounds. Chemical name: Chorismate pyruvate-lyase (amino-accepting) Registry number: EC 4.1.3.27 (12 Dec 1998) |
Synonyms : Argininosuccinate Synthetase, Synthase, Argininosuccinate, Synthetase, Argininosuccinate
| argininosuccinate synthase |
[EC 6.3.4.5] an enzyme of the ligase class that catalyzes the condensation of citrulline and aspartate to form argininosuccinate. The reaction is a part of the urea cycle in the liver (see illustration at urea cycle, under cycle). Written also argininosuccinate synthetase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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| argininosuccinate synthase deficiency |
an autosomal recessive aminoacidopathy characterized by marked elevation in plasma and urine levels of citrulline, with hyperammonemia and sometimes secondary oroticaciduria. Neonatal and late onset forms exist and clinical findings, which vary widely in severity, include mental retardation and neurologic abnormalities. Called also citrullinemia and citrullinuria.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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