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"aminoadipic saemialdehyde synthase"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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  • synthase
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  • Glycogen synthase
    ±Û¸®ÄÚ°ÕÇÕ¼º(ùêà÷)
  • glycogen synthase
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  • cystathionine beta-synthase
    ½Ã½ºÅ¸Æ¼¿À´Ñº£Å¸ÇÕ¼ºÈ¿¼Ò
  • glycogen synthase
    ´ç¿ø ÇÕ¼ºÈ¿¼Ò
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  • aminoadipic pathway
    ¾Æ¹Ì³ë¾ÆµðÇÈ °æ·Î(ÌèÖØ)
  • amylose synthetase(synthase)
    "¾Æ¹Ð·Î½º½ÅÅ×Å×À̽º, ¾Æ¹Ð·Î½º½ÅÅ×À̽º"
  • ATP synthase
    ATP ½ÅÅ×À̽º
  • citrate synthase
    ½ÃÆ®¸£»ê(ß«) ½ÅÅ×À̽º
  • glycogen synthase
    ±Û¶óÀÌÄÚÀü ½ÅÅ×À̽º
  • proton translocating ATP synthase
    ¾ç¼ºÀÚ(åÕàõí­) ÀüÀÌ ATP ½ÅÅ×À̽º
  • starch synthase
    ³ì¸» ½ÅÅ×À̽º
  • synthase
    "½ÅÅ×À̽º, ÇÕ¼ºÈ¿¼Ò(ùêà÷ý£áÈ)"
  • synthase-phosphorylase kinase
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ALAS delta-aminolevulinate synthase
ALASH delta-aminolevulinate synthase, housekeeping type
bNOS brain nitric oxide synthase
CBS cervicobrachial syndrome; chronic brain syndrome; clinical behavioral science; conjugated bile salts...
CS calf serum; campomelic syndrome; carcinoid syndrome; cardiogenic shock; caries-susceptible; carotid ...
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alpha-AAA DL-alpha-aminoadipic acid
NO Synthase nitric oxide synthase
iNOS 1.Inducible NO synthase
HPS 3-Hexulosephosphate synthase
ALAS 5'-aminolevulinate synthase
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
aminoadipic saemialdehyde synthase <enzyme> Bifunctional enzyme with both lysine-ketoglutarate reductase (EC 1.5.1.8) and saccharopine dehydrogenase (EC 1.5.1.9) activities
Registry number: EC 1.5.1.-
Synonym: aasa synthase
(26 Jun 1999)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
aminoadipic d-saemialdehyde synthase <enzyme> A bifunctional enzyme used in lysine degradation; it has a lysine:alpha-ketoglutarate reductase activity as well as a saccharopine dehydrogenase activity. A deficiency of this enzyme results in familial hyperlysinaemia.
(05 Mar 2000)
alpha-aminoadipic acid 2-amino-1,6-hexanedioic acid;an intermediate of lysine biosynthesis in higher fungi and bacteria, but not in algae and higher plants. Also in degradation of lysine in mammals.
(05 Mar 2000)
2-aminoadipic acid <chemical> 2-aminohexanedioic acid. An amino acid isolated from vibrio cholera.
Chemical name: Hexanedioic acid, 2-amino-
(12 Dec 1998)
aspartate-saemialdehyde dehydrogenase <enzyme> An enzyme that catalyses the conversion of l-aspartate 4-saemialdehyde, orthophosphate, and NADP+ to yield l-4-aspartyl phosphate and NADPH.
Chemical name: L-Aspartate-4-saemialdehyde:NADP+ oxidoreductase (phosphorylating)
Registry number: EC 1.2.1.11
(12 Dec 1998)
malonate saemialdehyde OHC-CH2-COO-;the transaminated product of beta-alanine; elevated in hyper-beta-alaninaemia.
(05 Mar 2000)
malonate saemialdehyde decarboxylase <enzyme> Forms acetaldehyde and carbon dioxide
Registry number: EC 4.1.1.-
(26 Jun 1999)
glutamate-1-saemialdehyde 2,1-aminomutase <enzyme> Catalyses the conversion of glutamate 1-saemialdehyde to 5-aminolevulinate via 4,5-diaminovalerate in pyridoxane-dependent reactions; genbank x82072 (heml protein from pseudomonas aeruginosa)
Registry number: EC 5.4.3.8
Synonym: glu-s-aminotransferase, glutamate-1-saemialdehyde aminotransferase, heml protein, heml gene product
(26 Jun 1999)
glutamate gamma-saemialdehyde -OOCCH(NH3)+CH2CH2C HO;an intermediate in l-proline and l-ornithine metabolism; becomes elevated in type II hyperprolinaemia.
(05 Mar 2000)
glutamate-saemialdehyde dehydrogenase <enzyme> Converts 5-glutamyl phosphate to glutamate 5-saemialdehyde in the presence of NADPH; see also glutamic-gamma-saemialdehyde dehydrogenase which catalyses the oxidation of 1-pyrroline-5-carboxylate to l-glutamate in the presence of nad
Registry number: EC 1.2.1.41
Synonym: beta-glutamylphosphate reductase, glutamate 5-saemialdehyde dehydrogenase, gamma-glutamylphosphate reductase, proa gene product
(26 Jun 1999)
methylmalonate saemialdehyde OHC-CH(CH3)-COO-;an intermediate in l-valine catabolism; elevated in certain inborn disorders.
(05 Mar 2000)
saemialdehyde The monoaldehyde of a dicarboxylic acid, so called because half the COOH groups of the original acid are reduced to the aldehyde while the other half are unchanged; e.g., glutamic acid gamma-saemialdehyde, OHC-CH2CH2CH(NH3)+-COO-. Many saemialdehyde's are intermediates in the biosynthesis and metabolic degradation of amino acids (e.g., l-proline, l-lysine, l-glutamate).
(05 Mar 2000)
succinate saemialdehyde -OOC-CH2-CH2-CHO;an intermediate in the catabolism of gamma-aminobutyrate.
Succinate saemialdehyde dehydrogenase, an enzyme that catalyses the reaction of succinate saemialdehyde and either NAD+ or NADP+ to form succinate and NADH (or NADPH); a deficiency of this enzyme is associated with 4-hydroxybutyric aciduria.
(05 Mar 2000)
succinate saemialdehyde reductase <enzyme> Nadp dependent
Registry number: EC 1.1.1.-
Synonym: sucinate saemialdehyde reductase (nadp)
(26 Jun 1999)
N-succinylglutamate 5-saemialdehyde dehydrogenase <enzyme> Catalyses conversion of n-succinylglutamate saemialdehyde to n-succinylglutamate; member of catabolic arginine succinyltransferase pathway; isolated from pseudomonas aeruginosa; genbank af011922
Registry number: EC 1.2.1.-
Synonym: arud gene product, sgsd enzyme
(26 Jun 1999)
ethylmalonate-saemialdehyde dehydrogenase <enzyme> Forms butyryl-CoA
Registry number: EC 1.2.1.-
Synonym: ethylmalonic saemialdehyde dehydrogenase, emsa dehydrogenase
(26 Jun 1999)
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