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  • hereditary adrenogenital syndrome
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  • hereditary adrenogenital syndrome
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  • adrenogenital hyperplasia
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AGS adrenogenital syndrome; Alagille syndrome; American Geriatrics Society; audiogenic seizures
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AGS Adrenogenital Syndrome
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    Adrenogenital disorder, unspecified
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    Adrenogenital disorders
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    1. ºñÁ¤»óÀ¸·Î ´Ù·®ÀÇ ¾Èµå·ÎÁ¨¼ºÀÇ ½ºÅ×·ÎÀ̵å, ƯÈ÷ µðÇÏÀ̵å·Î ¿¡ÇǾȵå·Î½ºÅ×·ÐÀÌ ºÎ½ÅÀ¸·ÎºÎÅÍ ºÐºñµÇ¾î ±× °á°ú ³²¾Æ¿¡¼­´Â Á¶¼÷Áõ, ¿©¾Æ¿¡¼­´Â ³²¼ºÈ­¸¦ ÀÏÀ¸Å²´Ù. °¡Àå ÈçÇÑ ¿øÀÎÀÌ 21?-hydroxylaseÀÇ ¼±Ãµ¼º °áÇÌ. ¸Å¿ì µå¹°°Ô »ý¸íÀ» ÀÒ°Ô µÇ´Â °æ¿ì°¡ Àִµ¥ ÀÌ´Â 2?-dehydroxylaseÀÇ ¿ÏÀü °áÇÌÀÌ ¿øÀÎÀÌ´Ù. 2. ºÎ½Å ÇÇÁúÀÇ ±â´É Ç×Áø¿¡ ÀÇÇÑ ÁõÈıºÀ¸·Î ¿©¼º¿¡¼­´Â ÀϹÝÀûÀ¸·Î Ãâ»ý ½Ã¿¡ °¡¼º ¹ÝÀ½¾ç ³²¼ºÈ­°¡ ÀÖ°í, ³²¼º¿¡¼­´Â ¼ºÀû Á¶¼÷À» º¸À̳ª »ýÈÄ 3-4³â Àü¿¡´Â ÃâÇöÇÏÁö ¾Ê´Â´Ù. À̵é ÀÓ»ó ¼Ò°ßÀº ÄÚ¸£Æ¼¼ÕÀÇ »ý»ê °áÇ̰ú ¾Èµå·Î°ÕÀÇ »ý»ê °úÀ׿¡ ÀÇÇÏ¿© ³ªÅ¸³­´Ù.
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adrenogenital syndrome <syndrome> A general term for a group of disorders which involve hyperplasia (or malignant tumours) of the adrenal cortex. Features include masculinisation of women, feminisation of men or precocious sexual development of children.
(27 Sep 1997)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Adrenogenital Syndrome - »õâ Abnormal SEX DIFFERENTIATION caused by disorders of the GONADS or the ADRENAL GLANDS, such as CONGENITAL ADRENAL HYPERPLASIA and ADRENAL CORTEX NEOPLASMS. Due to abnormal steroid biosynthesis, clinical features include VIRILISM in females; FEMINIZATION in males; or precocious sexual development in children.
    Synonyms : Adrenogenital Syndromes, Syndrome, Adrenogenital, Syndromes, Adrenogenital
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adrenogenital syndrome Congenital adrenal hyperplasia (CAH) refers to any of several autosomal recessive diseases resulting from defects in steps of the synthesis of cortisol from cholesterol by the adrenal glands. Most of these diseases involve excessive or defective production of sex steroids and can pervert or impair development of primary or secondary sex characteristics in affected infants, children, and adults. ...
Ãâó: en.wikipedia.org/wiki/Adrenogenital_syndrome
adrenogenital s. a general term for the group of syndromes in which inappropriate masculinization or feminization, sometimes with precocious puberty, results from disorders of adrenal function that also affect gonadal steroidogenesis; it includes congenital adrenal hyperplasia and tumors of the adrenal cortex.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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