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adenomyosarcoma <oncology, tumour> Wilm's tumour or nephroblastoma, is a cancerous tumour of the kidney in children.
Wilm's is the most common tumour of the kidney and the most common intra-abdominal tumour in children. The exact cause is unknown, but probably develops in foetal tissue due to an underlying genetic factor. Like retinoblastoma, both sporadic and inherited forms occur.
Believed to be caused by development of homozygosity for a deletion of the tip of the short arm of chromosome 11, which is presumed to contain a tumour suppressor gene.
(07 Oct 1997)
Previous: willow wattle, willow-weed, willow-wort, wills, Wilms, Max, wilms tumourNext: Wilms' tumour, Wilson block, Wilson, Clifford, wilson diseaseadenomyosarcoma -->Wilms' tumour
A malignant renal tumour of young children, composed of small spindle cells and various other types of tissue, including tubules and, in some cases, structures resembling foetal glomeruli, and striated muscle and cartilage. Often inherited as an autosomal dominant trait .
Synonym: adenomyosarcoma, embryoma of the kidney, nephroblastoma.
(05 Mar 2000)
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adenomyosarcoma Wilms' tumor: malignant renal tumor of young children characterized by hypertension and blood in the urine and the presence of a palpable mass
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adenomyosarcoma malignant renal tumor of young children characterized by hypertension and blood in the urine and the presence of a palpable mass
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