| 영문 | Wilson's disease | 한글 | 윌슨병 |
|---|---|---|---|
| 설명 | 간이나 뇌에 구리가 비정상적으로 쌓여 일어나는 유전성 대사병. 간경화증이나 신경 증상이 따르는데, 손 떨림이나 언어 장애가 생기고 눈의 각막 주위에 녹갈색 고리가 나타난다. 영국의 신경과 의사 윌슨(Wilson)이 분류한 병이다. 보통염색체 열성으로 유전된다. 한국에서도 현재까지 50여 예가 보고되어 있다. 이병은 보통염색체 열성으로 유전되며, ATP7B라는 윌슨병 유전자가 13번 염색체에 위치한다. 특징으로 구리가 간, 뇌 및 각막에 축적하여 만성 간염 또는 간경화와 같은 간손상을 일으키고, 뇌 특히 렌즈핵의 퇴행 변화와 각막모서리에 녹갈색의 Kayser-Fleischer 고리를 형성한다. 임상증상의 발현은 보통 5~15세에 시작하는데 30~40세가 되도록 증상이 없을 수도 있다. |
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| SIR | single isomorphous replacement; specific immune release; standardized incidence ratio; syndrome of i... |
|---|---|
| AR | 1) Aortic Regurgitation = AI Echo소견 &... |
| AVR | Augmented Voltage Right arm Frank N. Wilson Lead I, II, III와 같은 크기의 E... |
| CTW | central terminal of Wilson; combined testicular weight |
| KW | Keith-Wagener [ophthalmoscopic finding]; Kimmelstiel-Wilson [syndrome]; Kugelberg-Welander [syndrome... |
| WD | Wilson disease |
|---|---|
| SIR | Signal Intensity Ratio |
| SIR | Silent Information Regulator |
| SIR | Standardised Incidence Ratio |
| SIR | Standardized incidence rates |
| Wilson, Sir William | <person> English dermatologist, 1809-1884. See: Wilson's disease, Wilson's lichen. (05 Mar 2000) |
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| Adams, Sir William | <person> British surgeon, 1760-1829. (05 Mar 2000) |
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| Bowman, Sir William | <person> B. Nantwich, Cheshire, July 20th, 1816. Was a Surgeon and Anatomist. Was Surgeon to Birmingham General Hospital and went to London in 1837. Was elected F.R.S. (1841) and F.R.C.S. (1854) and was appointed Professor of Anatomy and Physiology at King's College, London (1848-1956). Was the leading Opthalmic Surgeon in England. D. At his house, Joldwynds, near Dorking, Mar. 29th, 1892. Bowman's Capsule - surrounding the glomerulus in the kidney. Bowman's Glands - glands in the olfactory mucous membrane. On the structure and use of the Malpighian bodies of the kidney. Phil Trans. 1842. Much of Bowman's best anatomical work is to be found in Robert Todd's Cyclopaedia of Anatomy and Physiology. London 1835-1859. Lived: 1816-1892. (05 Dec 1998) |
| Macewen, Sir William | <person> Scottish surgeon, 1848-1924. See: Macewen's sign, Macewen's symptom, Macewen's triangle. (05 Mar 2000) |
| Gairdner, Sir William | <person> Scottish physician, 1824-1907. See: Gairdner's disease. (05 Mar 2000) |
| Wilde, Sir William | <person> Irish oculist and otologist, 1815-1876. See: Wilde's cords, Wilde's triangle. (05 Mar 2000) |
| Crookes, Sir William | <person> British physicist and chemist, 1832-1919; winner of the Nobel Prise in chemistry in 1907. See: Crookes' glass, Crookes-Hittorf tube. (05 Mar 2000) |
| Pym, Sir William | <person> English physician, 1772-1861. See: Pym's fever. (05 Mar 2000) |
| Stokes, Sir William | <person> Irish surgeon, 1839-1900. See: Stokes amputation, Gritti-Stokes amputation. (05 Mar 2000) |
| Turner, Sir William | <person> English anatomist, 1832-1916. See: intraparietal sulcus of Turner, Turner's sulcus. (05 Mar 2000) |
| Fergusson, Sir William | <person> Scottish surgeon, 1808-1877. See: Fergusson's incision. (05 Mar 2000) |
| Leishman, Sir William | <person> Scottish surgeon, 1865-1926. See: Leishmania, Leishman's chrome cells, Leishman's stain, Leishman-Donovan body. (05 Mar 2000) |
| Wilson block | The commonest form of right bundle-branch block, characterised in lead I by a tall slender R wave followed by a wider S wave of lower voltage. (05 Mar 2000) |
| Wilson, Clifford | <person> English physician, *1906. See: Kimmelstiel-Wilson disease, Kimmelstiel-Wilson syndrome. (05 Mar 2000) |
| wilson disease | <radiology> Abnormal copper metabolism: defect in serum ceruloplasmin, autosomal recessive Findings: copper deposition in liver most likely to be cirrhosis, increased density, degenerative changes in brain, arthritis, Kayser-Fleischer ring in Descemet's membrane (12 Dec 1998) |
| Wilson, Frank Norman | <person> U.S. Cardiologist, 1890-1952. See: Wilson block. (05 Mar 2000) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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