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  • Werdnig Hoffmann paralysis
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  • infantile muscular atrophy =Werdnig-Hoffmann disease
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  • infantile muscular atrophy =Werdnig-Hoffmann disease
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  • infantile muscular atrophy =Werdnig-Hoffmann disease
    ¿µ¾ÆÇü ±ÙÀ§ÃàÁõ(?ä®û¡ÐÉê×õêñø).
  • infantile muscular atrophy =Werdnig-Hoffmann disease
    ¿µ¾ÆÇü±ÙÀ§ÃàÁõ(?ä®û¡ÐÉê×õêñø).
  • werdnig hoffmann paralysis
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  • werdnig-hoffman disease
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WH well hydrated; Werdnig-Hoffmann [syndrome]; whole homogenate; wound healing
WHD Werdnig-Hoffmann disease
WHS Werdnig-Hoffmann syndrome; Wolf-Hirschhorn syndrome
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WHD Werdnig-Hoffman disease
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  • werdnig hoffmann paralysis
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    µ¿ÀǾî=Heffmann-Werdnig syndrome. °¡Á·¼º À¯Àü¼º ô¼ö¼º ±ÙÀ§Ãà.
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Werdnig, Guido <person> Austrian neurologist, 1862-1919.
See: Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy.
(05 Mar 2000)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 7 ÆäÀÌÁö: 1
werdnig-hoffmann disease A recessively inherited acute infantile form of motor neuropathy with proximal muscle wasting particularly of the upper extremities. The chronic childhood form may be an arrested werdnig-hoffmann disorder.
(12 Dec 1998)
Werdnig-Hoffmann muscular atrophy Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised.
Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy.
(05 Mar 2000)
Baccelli, Guido <person> Italian physician, 1832-1916.
See: Baccelli's sign.
(05 Mar 2000)
Banti, Guido <person> Italian physician, 1852-1925.
See: Banti's disease, Banti's syndrome.
(05 Mar 2000)
Tizzoni, Guido <person> Italian physician, 1853-1932.
See: Tizzoni's stain.
(05 Mar 2000)
Engelmann, Guido <person> German surgeon, *1876.
See: Engelmann's disease.
(05 Mar 2000)
Fanconi, Guido <person> Swiss paediatrician, 1892-1979.
See: Fanconi's anaemia, Fanconi's pancytopenia, Fanconi's syndrome, De Toni-Fanconi syndrome, Lignac-Fanconi syndrome.
(05 Mar 2000)
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