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  • infantile muscular atrophy =Werdnig-Hoffmann disease
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  • infantile muscular atrophy =Werdnig-Hoffmann disease
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  • infantile muscular atrophy =Werdnig-Hoffmann disease
    ¿µ¾ÆÇü ±ÙÀ§ÃàÁõ(?ä®û¡ÐÉê×õêñø).
  • infantile muscular atrophy =Werdnig-Hoffmann disease
    ¿µ¾ÆÇü±ÙÀ§ÃàÁõ(?ä®û¡ÐÉê×õêñø).
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WH well hydrated; Werdnig-Hoffmann [syndrome]; whole homogenate; wound healing
WHD Werdnig-Hoffmann disease
WHS Werdnig-Hoffmann syndrome; Wolf-Hirschhorn syndrome
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WHD Werdnig-Hoffman disease
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    µ¿ÀǾî=Heffmann-Werdnig syndrome. °¡Á·¼º À¯Àü¼º ô¼ö¼º ±ÙÀ§Ãà.
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    µ¿ÀǾî=Heffmann-Werdnig syndrome. °¡Á·¼º À¯Àü¼º ô¼ö¼º ±ÙÀ§Ãà.
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Werdnig, Guido <person> Austrian neurologist, 1862-1919.
See: Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy.
(05 Mar 2000)
werdnig-hoffmann disease A recessively inherited acute infantile form of motor neuropathy with proximal muscle wasting particularly of the upper extremities. The chronic childhood form may be an arrested werdnig-hoffmann disorder.
(12 Dec 1998)
Werdnig-Hoffmann muscular atrophy Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised.
Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy.
(05 Mar 2000)
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Werdnig-Hoffmann paralysis Infantile muscular atrophy, considered by some to be identical with amyotonia congenita.
Ãâó:
Werdnig-Hoffmann d. Werdnig-Hoffmann spinal muscular atrophy.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
Werdnig-Hoffmann spinal muscular a. a progressive, infantile, autosomal recessive form of muscular dystrophy, usually occurring in siblings rather than in successive generations, and resulting from degeneration of the anterior horn cells of the spinal cord. It is marked by early onset (usually at about six months of age, but sometimes prenatally), hypotonia and wasting of the muscles, complete flaccid paralysis, and death, usually in early life. Called also Hoffmann's a., infantile spinal muscular a., and Werdnig-Hoffmann disease.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
Werdnig-Hoffmann spinal muscular atrophy (disease) see under atrophy.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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Werdnig autosomal recessive disease in which the degeneration of spinal nerve cells and brain nerve cells leads to atrophy of skeletal muscles and flaccid paralysis
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