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HPW hypergammaglobulinemic purpura of Waldenstrom
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Waldenstrom's macroglobulinaemia <haematology> A condition characterised by proliferation of cells resembling lymphocytes or plasma cells in the bone marrow, anaemia, increased sedimentation rate and hyperglobulinaemia. Physical findings include mucosal bleeding, skin purpura and enlargement of the lymph nodes, liver and spleen.
Origin: Gr. Haima = blood
(27 Sep 1997)
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waldenstrom macroglobulinaemia <radiology> Can cause infiltration of small bowel, associated with primary CNS lymphoma
(12 Dec 1998)
macroglobulinaemia The presence of increased levels of macroglobulins in the circulating blood.
Waldenstrom's macroglobulinaemia, macroglobulinaemia occurring in elderly persons, characterised by proliferation of cells resembling lymphocytes or plasma cells in the bone marrow, anaemia, increased sedimentation rate, and hyperglobulinaemia with a narrow peak in gamma-globulin or b2-globulin at about 19 S units. The spleen, liver, or lymph nodes are often enlarged and there is frequently purpura or mucosal bleeding.
Synonym: hyperglobulinaemic purpura, Waldenstrom's purpura, Waldenstrom's syndrome.
(05 Mar 2000)
Waldenstrom Jan G., Swedish physician, *1906.
See: Waldenstrom's macroglobulinaemia, Waldenstrom's purpura, Waldenstrom's syndrome, Waldenstrom's test.
(05 Mar 2000)
Waldenstrom's purpura <haematology> A condition characterised by proliferation of cells resembling lymphocytes or plasma cells in the bone marrow, anaemia, increased sedimentation rate and hyperglobulinaemia. Physical findings include mucosal bleeding, skin purpura and enlargement of the lymph nodes, liver and spleen.
(27 Sep 1997)
Waldenstrom's syndrome <haematology> A condition characterised by proliferation of cells resembling lymphocytes or plasma cells in the bone marrow, anaemia, increased sedimentation rate and hyperglobulinaemia. Physical findings include mucosal bleeding, skin purpura and enlargement of the lymph nodes, liver and spleen.
Origin: Gr. Haima = blood
(27 Sep 1997)
Waldenstrom's test A test for porphyrin in the urine; 2 ml of urine are mixed with an equal amount of 2% dimethyl-p-aminobenzaldehyde in 50/100 HCl. A red colour appears if urobilinogen (Ehrlich's benzaldehyde reaction) or porphobilinogen is present.
(05 Mar 2000)
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