| 영문 | hemophilia | 한글 | 혈우병 |
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| 설명 | 선천성-유전성으로 혈액응고인자의 결핍에 의한 병. 선천적으로 출혈하기 쉬운 체질로서, 자발적 또는 가벼운 외상에 의해서도 쉽게 출혈하며, 지혈이 잘 되지 않아 때로는 사망하는 수도 있다. 유전형식은 반성열성유전이며, 혈우병 가족에 속하는 여자에 의하여 그 유전자가 자녀에게 전해지는데, 이 병이 나타나는 것은 거의 남자아이이고, 여자아이에게는 드물게 나타난다. 혈장 속에 존재하는 항혈우병 글로불린이 선천적으로 결여 또는 부족하기 때문에 혈액응고 과정에서 트롬보플라스틴의 출현이 불완전하게 되는 것을 혈우병A라고 한다. 증세는 출생 직후부터 나타나는데, 신생아의 배꼽에서 다량의 출혈을 볼 때가 있다. 많은 경우 보행을 시작할 무렵에 타박이나 손상이 실마리가 되어 발견되는 수가 많다. 그 밖에 칫솔에 의한 잇몸출혈, 발치 후의 출혈, 코점막의 손상 등으로도 쉽게 출혈하여 잘 멎지 않는다. 무릎관절이나 발관절에 종창-동통을 수반하는 혈액관절을 일으키는 수가 많고, 관절의 기형이나 기능장애를 남긴다. 검사에서는 혈액응고 시간이 현저하게 길어지고, 프로트롬빈의 소비가 현저하게 감소되며, 또한 출혈시간도 연장된다. 이와 같은 고전적인 혈우병 외에, 임상적으로 혈우병과 같은 증세를 나타내면서 혈액응고 이상에 약간의 차이가 나는 사례가 보고되어 있다. 즉, 혈우병 B는 트롬보플라스틴 생성에 필요한 인자 중의 제-인자가 결여되어 있는 것이다. 혈우병 C는 제-인자가 결여된 것이고, 이것은 혈우병 A 및 B(크리스마스병)와는 달리 남녀 모두에 보이며, 우성유전을 한다. |
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| HEM | hematology, hematologist; hematuric; hemophilia; hemorrhage; hemorrhoids |
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| HEMB | hemophilia B |
| NHA | National Health Association; National Hearing Association; National Hemophilia Association; nonspeci... |
| NHF | National Health Federation; National Hemophilia Foundation; nonimmune hydrops fetalis |
| CVA | 1) Cardio-Vascular Accident(Attack) 2) Cerebro-Vascular Accident(Attack);... |
| HA | Hemophilia A |
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| VEGF/VPF | Vascular endothelial growth factor/ vascular permeability factor |
| VPF/VEGF | Vascular permeability factor/vascular endothelial growth factor |
| VCAM-1 | 1/vascular cell adhesion molecule-1 |
| AVR | Acute vascular rejection |
| hemophilia | <disease, haematology> A haemorrhagic diathesis occurring in two main forms: 1. Haemophilia A (classic haemophilia, factor VIII deficiency), an X linked disorder due to deficiency of coagulation factor VIII. 2. Haemophilia B (factor IX deficiency, Christmas disease), also X linked, due to deficiency of coagulation factor IX. Both forms are determined by a mutant gene near the telomere of the long arm of the X chromosome (Xq), but a different loci and are characterised by subcutaneous and intramuscular haemorrhages, bleeding from the mouth, gums, lips and tongue, haematuria and haemarthroses. (18 Nov 1997) |
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| acute vascular occlusion | <cardiology, surgery> A serious condition that results from the sudden blockage of an artery, usually with a blood clot. (27 Sep 1997) |
| acute vascular purpura | <dermatology> This relatively rare disorder is characterised by skin purpura, joint pains, abdominal pain and renal disease (glomerulonephritis). Although Henoch-Schonlein purpura or anaphylactoid purpura, is thought to be a immune complex mediated disease, its exact cause is unknown. Its typical benign coarse can, however, include renal failure. (27 Sep 1997) |
| articular vascular circle | An anastomosis of vessels encircling a joint. See: articular vascular network. Synonym: circulus articularis vasculosus. (05 Mar 2000) |
| articular vascular network | A vascular rete in the neighborhood of a joint, where such arrangements are common, enabling a collateral circulation by which blood will be supplied distal to the joint regardless of compromises resulting from joint position. Synonym: circulus articularis vasculosus, rete vasculosum articulare, articular network. (05 Mar 2000) |
| articular vascular network of elbow | Vascular networks in the region of the elbow, composed of anastomoses between branches of the radial and middle collateral, superior and inferior ulnar collateral, radial recurrent, interosseous recurrent, and recurrent ulnar arteries. Synonym: rete articulare cubiti. (05 Mar 2000) |
| articular vascular network of knee | An arterial network over the front and sides of the knee, formed by branches of the descending genicular artery, of the five genicular arteries from the popliteal, of the anterior tibial recurrent, and of the fibular circumflex branch of the posterior tibial. Synonym: rete articulare genus. (05 Mar 2000) |
| atherosclerotic vascular disease | <cardiology> The progressive narrowing and hardening of the arteries over time. This is known to occur to some degree with aging, but other risk factors that accelerate this process have been identified. These factors include: high cholesterol, high blood pressure, smoking, diabetes and family history for atherosclerotic disease. (27 Sep 1997) |
| blood-vascular system | The heart and the blood vessels by which blood is pumped and circulated through the body. (12 Dec 1998) |
| vascular | <physiology> Pertaining to blood vessels or indicative of a copious blood supply. (18 Nov 1997) |
| vascular anticoagulant | <protein> Group of calcium-binding proteins that interact with acidic membrane phospholipids in membranes. They contain 4 or 8 repeats of a 61 amino acid domain that folds into 5 a helices. Also known by several other names (e.g. Lipocortins, endonexins), reflecting the history of their discovery in different contexts. See: lipocortin, endonexin I & II, calpactin, p70 and calelectrin. (18 Nov 1997) |
| vascular bud | An endothelial sprout arising from a blood vessel. (05 Mar 2000) |
| vascular bundle | Strand of vascular tissue in a plant, composed of xylem and phloem. (18 Nov 1997) |
| vascular cambium | Lateral meristem that forms the secondary tissue and is located between the xylem and phloem. (09 Oct 1997) |
| vascular capacitance | The relationship between the volume of blood contained within a segment of vasculature and the pressure distending the vascular walls over a wide range of pressures and volumes. The veins of the body are not only conduits for the return of blood to the right heart, but they also determine most of the vascular capacitance and contain most of the blood volume. Changes in vascular capacitance provide a quick and effective mechanism for the filling of the right heart, thereby influencing cardiac output. Vascular capacitance is somewhat analogous to vascular resistance but whereas vascular resistance relates to flow through a blood vessel, vascular capacitance relates to the volume contained in it. (12 Dec 1998) |
| vascular hemophilia |
von Willebrand's disease: a form of hemophilia discovered by Erik von Willebrand; a genetic disorder that is inherited as an autosomal recessive trait; characterized by a deficiency of the coagulation factor and by mucosal bleeding
출처: wordnet.princeton.edu/perl/webwn
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| Vascular hemophilia | a form of hemophilia discovered by Erik von Willebrand |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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