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Unverricht's disease A progressive myoclonic epilepsy; one of the degenerative gray matter disorders characterised by myoclonus and generalised seizures, with progressive neurological and intellectual decline; age of onset between 8 and 13 years of age; autosomal recessive inheritance.
(05 Mar 2000)
Unverricht, Heinrich <person> German physician, 1853-1912.
See: Unverricht's disease.
(05 Mar 2000)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Unverricht-Lundborg Syndrome - »õâ An autosomal recessive condition characterized by recurrent myoclonic and generalized seizures, ATAXIA, slowly progressive intellectual deterioration, dysarthria, and intention tremor. Myoclonic seizures are severe and continuous, and tend to be triggered by movement, stress, and sensory stimuli. The age of onset is between 8 and 13 years, and the condition is relatively frequent in the Baltic region, especially Finland. (From Menkes, Textbook of Child Neurology, 5th ed, pp109-110)
    Synonyms : Baltic Myoclonus Epilepsy, Unverricht Disease, Baltic Myoclonus Epilepsies, Disease, Unverricht, Diseases, Unverricht, Epilepsies, Baltic Myoclonus, Epilepsy, Baltic Myoclonus, Epilepsy, Mediterranean Myoclonic, Lundborg Unverricht Syndrome, Myoclonus, Baltic
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Unverricht's d. Baltic myoclonic epilepsy.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
Unverricht's disease (syndrome) myoclonic epilepsy.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
Unverricht-Lundborg disease Baltic myoclonic epilepsy.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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