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"Thiamine deficiency, infantile"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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¿µ¹® iron deficiency anemia ÇÑ±Û Ã¶°áÇ̺óÇ÷
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  ÀûÇ÷±¸ÀÇ ±â´ÉÀº »ê¼Ò¸¦ ¿î¹ÝÇϴµ¥ ÀÖ´Ù. ÀûÇ÷±¸ ¼Ó¿¡ »ê¼Ò¿Í °áÇÕÀ» ÇÏ¿© »ê¼Ò¸¦ ¿î¹ÝÇϴ Ç÷»ö¼Ò¶ó´Â ¹°ÁúÀÌ ÀÖ´Ù. Ã¶Àº ÀÌ Ç÷»ö¼ÒÀÇ Áß¿äÇÑ ºÎºÐÀ» ÀÌ·ç´Â °ÍÀ¸·Î Ã¶ÀÌ ¾øÀ¸¸é Ç÷»ö¼Ò°¡ ¸¸µé¾îÁú ¼ö°¡ ¾ø´Ù. Ç÷»ö¼Ò°¡ ¾øÀ¸¸é ¿ª½Ã ÀûÇ÷±¸µµ ¸¸µé¾îÁöÁö ¾ÊÀ¸¹Ç·Î Ã¼³»¿¡ Ã¶ÀÌ ºÎÁ·Çϸ頺óÇ÷ÀÌ »ý±ä´Ù. À̠ö°áÇ̼º ºóÇ÷Àº ºóÇ÷ÀÇ ¿øÀΠÁß¿¡¼­ °¡Àå ÈçÇÑ °ÍÀÌ´Ù(¾à 25%¸¦ Â÷ÁöÇÑ´Ù). Ã¶ÀúÀå·®ÀÇ ÀúÇÏ-°áÇÌ, Ç÷ûö³óµµÀÇ ÀúÇÏ, Æ®¶õ½ºÆä¸°·® »ó½Â, Æ®¶õ½ºÆä¸°Æ÷È­µµÀÇ ÀúÇÏ, Ç÷»ö¼Ò³óµµ ¶Ç´Â Ç츶ÅäÅ©¸®Æ®ÀÇ ÀúÇÏ, Àú»ö¼Ò¼º´ëÀûÇ÷±¸¸¦ Æ¯Â¡À¸·Î Çϴ ºóÇ÷·Î¼­, »ýü ³»¿¡¼­ Ã¶ÀÌ Àå±â¿¡ °ÉÃÄ °áÇ̵Ǹ砱נ¶§¹®¿¡ Ç÷»ö¼Ò »ý»ê °¨¼Ò¿¡ ÀÇÇØ ÀϾ´Ù. Ã¢ÀÚ¿¡¼­ÀǠöÈí¼ö·® ºÎÁ·, Ã¶ÀÇ ¼ö¿ä Áõ´ë(À¯¾Æ±â, »çÃá±â, ÀÓ½Å), Ã¶¼Ò½Ç°úÀ×(ÃâÇ÷)¿¡ ÀÇÇØ ÀϾ¸ç, Æ¯È÷ »çÃá±â¿¡¼­ Æó°æ±â±îÁöÀÇ ¿©¼º¿¡°Ô ¸¹´Ù. Áõ»óÀ¸·Î¼­´Â ¾ó±¼Ã¢¹é, ÇǷΰ¨, ÇǺÎâ¹é, ¼ÕÅé º¯È­(½ºÇ¬ ¸ð¾ç) µîÀ» ³ªÅ¸³½´Ù. ±¸°­ ¿µ¿ª¿¡¼­´Â ÇôÀÇ Á¢ÃËÅë, ¹ßÀû, °ÇÁ¶°¨, »ïÅ´°ï¶õÀ» ¼ö¹ÝÇϸé Ç÷¯¸Ó-ºó½¼(Plummer-Vinson)ÁõÈıºÀ̶ó°í ÇÑ´Ù. Ç÷¾× ¼Ò°ßÀº Ç÷ûöÀº ÀúÇÏÇϸç, Ã¶°áÇÕ´É·ÂÀÇ »ó½Â, Àú»ö¼Ò¼º ÀÛÀºÀûÇ÷±¸¼ºÀ» ³ªÅ¸³½´Ù.
¿µ¹® thiamine ÇÑ±Û Æ¼¾Æ¹Î
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  ºñŸ¹Î B1À̶ó°íµµ Çϸ砼ö¿ë¼º ºñŸ¹ÎÀ¸·Î ÀÎü´ë»ç¿¡ Áß¿äÇÑ Á¶È¿¼ÒÀÓ. °áÇ̽ÿ¡´Â °¢±âº´(beriberi)ÀÌ À¯¹ßµÇ¸ç ±× Áõ»óÀº ½ÉÀå±â´É»ó½Ç, ¸»ÃʽŰ濰 µîÀÌ ÀÖ´Ù.
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  • ¿µ¹®
    ÇѱÛ
  • acquired immune deficiency syndrome
    ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
  • biotin deficiency syndrome
    ºñ¿Àƾ°áÇÌÁõÈıº
  • deficiency
    1. °áÇÌ 2. °áÇÌÁõ
  • deficiency disease
    °áÇ̺´
  • erythropoietin deficiency anemia
    ¿¡¸®Æ®·ÎÆ÷ÀÌ¿¡Æ¾°áÇ̺óÇ÷
  • fat deficiency disease
    Áö¹æ°áÇ̺´
  • folate deficiency anemia
    ¿±»ê°áÇ̺óÇ÷
  • iron deficiency anemia
    ö°áÇ̺óÇ÷
  • immune deficiency
    ¸é¿ª°áÇÌ
  • leukocyte adhesion deficiency
    ¹éÇ÷±¸ºÎÂø°áÇÌ
  • nutritional deficiency disease
    ¿µ¾ç°áÇ̺´
  • nutritional deficiency state
    ¿µ¾ç°áÇÌ»óÅÂ
  • nutritional deficiency syndrome
    ¿µ¾ç°áÇÌÁõÈıº
  • vitamin deficiency
    ºñŸ¹Î°áÇÌ(Áõ)
  • infantile
    ¿µ¾Æ-
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 4 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • infantile spasm
    ¿µ¾Æ¿¬Ãà
  • thiamine
    Ƽ¾Æ¹Î
  • iron deficiency anemia
    ö°áÇ̺óÇ÷
  • deficiency
    °áÇÌ(Áõ)
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • thiamine
    Ƽ¾Æ¹Î
  • acid lipase deficiency
    »ê¼ºÁöÁúºÐÇØÈ¿¼Ò°áÇÌ
  • acquired immune deficiency
    ÈÄõ¸é¿ª°áÇÌ
  • acquired immune deficiency syndrome
    ÈÄõ¸é¿ª°áÇÌÁõÈıº, ¿¡ÀÌÁî
  • adhesion deficiency disorder
    À¯Âø°áÇÌÀå¾Ö
  • antibody deficiency syndrome
    Ç×ü°áÇÌÁõÈıº
  • erythropoietin deficiency anemia
    ¿¡¸®Æ®·ÎÆ÷¿¡Æ¾°áÇ̺óÇ÷
  • folate deficiency anemia
    ¿±»ê°áÇÌ
  • iron deficiency anemia
    ö°áÇ̺óÇ÷
  • ceruloplasmin deficiency
    ¼¼·ê·ÎÇö󽺹ΰáÇÌ
  • complement deficiency
    µµ¿òü°áÇÌ
  • deficiency
    °áÇÌ(Áõ)
  • deficiency disease
    ¿µ¾ç°áÇ̺´
  • fat deficiency disease
    Áö¹æ°áÇÌÁõ
  • functional deficiency
    ±â´É°áÇÌ
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  • ¿µ¹®
    ÇѱÛ
  • amnesia infantile (infantile amnesia)
    À¯¾Æ±â ±â¾ï»ó½Ç.
  • Acquiered immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª °áÇÌÁõÈıº
  • Fluorine deficiency
    ºÒ¼Ò°áÇÌÁõ(Ý×áÈÌÀù¹ñø)
  • Folate deficiency
    ¿±»ê°áÇÌÁõ(ç¨ß«ÌÀù¹ñø)
  • Iodine deficiency
    ¿äµå °áÇÌÁõ(ÌÀù¹ñø)
  • Iron deficiency anemia
    ö°áÇ̼ººóÇ÷(ôÑÌÀù¹àõÞ¸úì)
  • Rh deficiency syndrome
    Rh °áÇÌÁõÈıº
  • T cell deficiency
    T¼¼Æ÷°áÇÌ
  • abdominal muscle deficiency syndrome
    º¹±Ù°á¼ÕÁõÈıº(ÜÙÐÉÌÀáßñøý¦ÏØ).
  • acid lipase deficiency
    »ê¼º ¸®ÆÄÁ¦ °áÇÌÁõ(ß«àõ¡­ÌÀù¹ñø)
  • acquired immune deficiency
    ÈÄõ¼º ¸é¿ª°áÇÌ
  • acquired immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª°áÇÌ ÁõÈıº
  • acquired immune deficiency syndrome
    ÈÄõ¼º ¸é¿ª°áÇÌÁõÈıº(ý­ô¸àõ Øóæ¹ÌÀù¹ñøý¦ÏØ)
  • adenosine,deficiency
    °áÇÌÁõ(ÌÀù¹ñø)
  • adrenocortical deficiency
    ºÎ½ÅÇÇÁú°áÇÌÁõ.
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • thiamine deficiency
    Ƽ¾Æ¹Î°áÇÌ
  • amnesia infantile (infantile amnesia)
    À¯¾Æ±â ±â¾ï»ó½Ç.
  • amnesia, infantile (infantile amnesia)
    À¯¾Æ±â ±â¾ï»ó½Ç.
  • thiamine
    Ƽ¾Æ¹Î
  • thiamine
    Ƽ¾Æ¹Î, ŸÀ̾ƹÎ
  • thiamine pyrophosphate
    ÇÇ·ÎÀλê(¡­ìÝß«)Ƽ¾Æ¹Î.
  • thiamine pyrophosphate
    ÇÇ·ÎÀÎ»êÆ¼¾Æ¹Î, ÆÄÀÌ·ÎÀλêŸÀ̾ƹÎ
  • acute anterior poliomyelitis =infantile par aly sis
    ±Þ¼º ȸ¹éô¼ö¿°(ÐáàõüéÛÜô±âÐæú).
  • aggressive infantile fibromatosis
    ħ½À À¯¾Æ(öÕã©àõ êáä®) ¼¶À¯Á¾Áõ(àéë«ðþñø)
  • chronic infantile neurological cutaneous articular syndrome
    ¸¸¼º À¯¾Æ ½Å°æ ÇǺΰüÀý ÁõÈıº
  • congenital infantile hemiplegia
    ¼±Ãµ¼º ¿µ¾Æ¼º Æí¸¶ºñ.
  • digital infantile fibromatosis
    ¼Õ¹ß°¡¶ô À¯¾Æ ¼¶À¯Á¾Áõ
  • early infantile autism
    Á¶±âÀ¯¾ÆÀÚÆóÁõ, Á¶±â¼Ò¾ÆÀÚÆóÁõ(¡­á³ä®í»øÍñø).
  • early infantile autism
    Á¶±âÀ¯¾ÆÀÚÆóÁõ(º´)(¡­í»øÍñø).
  • eczema infantile =e. infantum<³ª>
    ¿µ¾Æ ½ÀÁø.
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Deficiency (Nanismus)
    °áÇÌ(³­ÀåÀÌÁõ)
    [¿¾ ¿ë¾î] °áÇÌ
  • Organogenetic deficiency
    ±â°ü¹ß»ý°áÇÌ
    [¿¾ ¿ë¾î] ±â°ü¹ß»ý°áÇÌ
  • Functional deficiency
    ±â´É°áÇÌ
    [¿¾ ¿ë¾î] ±â´ÉÀû°áÇÌ
  • Pituitary hormone deficiency (Pituitary dwarfism)
    ³úÇϼöüȣ¸£¸ó°áÇÌ (³úÇϼöü³­ÀåÀÌ)
    [¿¾ ¿ë¾î] ³úÇϼöüȣ¸£¸ó°áÇÌ (³úÇϼöü³­ÀåÀÌ)
  • Reaction deficiency
    ¹ÝÀÀ°áÇÌ
    [¿¾ ¿ë¾î] ¹ÝÀÀ°áÇÌ
  • Vitamin deficiency (Fetal osteodystrophy)
    ºñŸ¹Î°áÇÌ(žƻÀ¿µ¾çÀå¾Ö)
    [¿¾ ¿ë¾î] ºñŸ¹Î°áÇÌ(žƻÀ¿µ¾çÀå¾Ö)
  • Cellular deficiency (Acallosal cerebrum)
    ¼¼Æ÷°áÇÌ (³úµéº¸°á¿©³ú)
    [¿¾ ¿ë¾î] ¼¼Æ÷°áÇÌ
  • Intracellular deficiency (Albinism)
    ¼¼Æ÷¼Ó°áÇÌ (¹é»öÁõ)
    [¿¾ ¿ë¾î] ¼¼Æ÷³»°áÇÌ
  • Chromosomal deficiency
    ¿°»öü°áÇÌ
    [¿¾ ¿ë¾î] ¿°»öü°á½Ç
  • Stimulation deficiency
    ÀڱذáÇÌ
    [¿¾ ¿ë¾î] ÀڱذáÇÌ
  • Sensory deficiency
    °¨°¢°áÇÌ
    [¿¾ ¿ë¾î] °¨°¢°áÇÌ
  • Thyroid hormone deficiency (Cretinism)
    °©»ó»ùÈ£¸£¸ó°áÇÌ (°©»ó»ù³­ÀåÀÌ)
    [¿¾ ¿ë¾î] °©»ó¼±È£¸£¸ó°áÇÌ (°©»ó»ù³­ÀåÀÌ)
  • Deficiency
    °áÇÌ
    [¿¾ ¿ë¾î] °áÇÌ
  • Deficiency (Monstrous tumor)
    °áÇÌ (±«¹°Á¾)
    [¿¾ ¿ë¾î] °áÇÌ
  • Secretion deficiency
    ºÐºñ°áÇÌ
    [¿¾ ¿ë¾î] ºÐºñ°áÇÌ
´ëÇÑ»ýÈ­ÇкÐÀÚ»ý¹°ÇÐȸ ¿ë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 14 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • thiamine
    ŸÀ̾ƹÎ
  • thiamine pyrophosphate
    ŸÀ̾ƹΠÇÇ·ÎÀλê (ìÝß«)
  • conditioned vitamin deficiency
    Á¶°ÇºÎ(ðÉËìݾ) ºñŸ¹Î°áÇË(ÌÀù¹)
  • deficiency
    °áÇÌ(ÌÀù¹)
  • deficiency disease
    °áÇÌ Áúȯ(ÌÀù¹òðü´)
  • deficiency mutant
    "°áÇÌ º¯ÀÌü(ÌÀù¹Ü¨ì¶ô÷), (ÔÒ) auxotroph"
  • dietary deficiency
    ½ÄÀ̰áÇÌ(ç½å×ÌÀù¹)
  • familial high-density lipoprotein deficiency °¡Á·¼º °í¹Ðµµ ÁöÁú´Ü¹éÁú °áÇÌ (Ê«ðéàõÍÔÚËÓøò·òõ
    Ó±ÛÜòõÌÀù¹)
  • familial lysosomal lipase deficiency
    °¡Á·¼º(Ê«ðéàõ) ¶óÀÌ¼Ò¼Ø ¶óÀÌÆäÀ̽º °áÇÌ(ÌÀù¹)
  • glucose-6-phosphate dehydrogenase deficiency
    ±Û·çÄÚ½º-6-Àλê(×òß«) µðÇÏÀ̵å·ÎÀú³×À̽º °áÇÌ(ÌÀ
  • primary deficiency
    ¿ø¹ß¼º °áÇÌ(ê«Û¡àõÌÀù¹)
  • secondary deficiency
    ÀÌÂ÷ °áÇÌ(ì£ó­ÌÀù¹)
  • simian acquired immune deficiency syndrome
    ¿ø¼þÀÌ ÈÄõ¼º¸é¿ª°áÇÌÁúȯ(ý­ô¸àõØóæ¹ÌÀù¹òðü´)
  • sulfite oxidase deficiency
    ¾ÆÈ²»ê(ä¬üÜß«) ¿Á½Ãµ¥À̽º °áÇÌ(ÌÀù¹)
KI ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 7 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • infantile
    ¿µ¾ÆÀÇ
  • deficiency
    °áÇÌÁõ
  • deficiency anemia
    °áÇ̼ººóÇ÷
  • iron deficiency anemia
    ö°áÇ̼ººóÇ÷
  • mineral deficiency
    ¹«±âÁú°áÇÌ(Áõ)
  • nutritional deficiency disease
    ¿µ¾ç°áÇÌÁõ
  • vitamin deficiency
    ºñŸ¹Î°áÇÌ(Áõ)
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
MD Doctor of Medicine [Lat. Medicinae Doctor]; magnesium deficiency; main duct; maintenance dose; major...
IGD idiopathic growth hormone deficiency; interglobal distance; isolated gonadotropin deficiency
MCD magnetic circular dichroism; mast-cell degranulation; mean cell diameter; mean of consecutive differ...
TPP   1) Thiamine diPhos-Phate
  2) Total Plasma Protein
B1 induced field in magnetic resonance imaging; radiofrequency magnetic field in nuclear magnetic reson...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
PTD Pyrithiamine-induced thiamine deficiency
TD Thiamine deficiency
T Thiamine
TMPase Thiamine monophosphatase
TRMA Thiamine responsive megaloblastic anemia
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • thiamine
    Ƽ¾Æ¹Î
    ºñŸ¹Î B º¹ÇÕü ¼ººÐ. 1926³â¿¡ ÃÖÃÊ·Î À¯¸®µÇ¾ú´Ù. Äá·ù, ³ì»ö ¾ßä, ¿Á¼ö¼ö, ³­È², °£, Çö¹Ì µî¿¡ Á¸ÀçÇϰí, Ç÷Àå ¹× ³ú ô¼ö¾×¿¡¼­µµ À¯¸® »óÅ·Πº¼ ¼ö ÀÖ´Ù. À̰ÍÀÇ È°¼ºÇüÀº Ƽ¾Æ¹Î ÆÄÀÌ·ÎÆ÷½ºÆäÀÌÆ®À̸ç, ÀÌ ºñŸ¹ÎÀÇ °áÇÌÀº °¢±âº´¸¦ ÀÏÀ¸Å°°Ô µÈ´Ù.
  • thiamine hydrochloride
    ¿°»ê Ƽ¾Æ¹Î
  • thiamine test
    ŸÀ̾ƹΠ½ÃÇè
  • aggressive infantile fibromatosis
    ħ½À À¯¾Æ ¼¶À¯Á¾Áõ
  • chronic infantile neurological cutaneous articular syndrome
    ¸¸¼º À¯¾Æ ½Å°æ ÇǺαº
  • congenital infantile hemiplegia
    ¼±Ãµ¼º ¿µ¾Æ¼º Æí¸¶ºñ
  • infantile ankylosis
    À¯¾Æ¼º °­Á÷
  • infantile cerebrocerebellar diplegic paralysis
    ¼Ò¾Æ³ú¼º ¾çÃø ¸¶ºñ
    ¿µ¾Æ±â¿¡ ÁøÇàÇÏ¿© »çÁö¸¦ ¸ðµÎ ħ¹üÇÏ¿©, ´ë³ú¿Í ¼Ò³úÀÇ »ó¹ÝµÇ´Â ºÎºÐÀÇ ¹ßÀ°ºÎÀüÀ̳ª ÆÄ±«ÀÇ È¥ÇÕÀ¸·Î ³ªÅ¸³­´Ù.
  • infantile eczema
    ¼Ò¾Æ½ÀÁø
    ¾î¸°À̵鿡°Ô »ý±â´Â ½ÀÁø. Á¥¸ÔÀÌ ¶§¿¡´Â ÇǺÎÀÇ ÇØºÎÀû, »ý¸®ÀûÀΠƯÀ̼ºÀ¸·Î ÀÎÇÏ¿© ½ÀÁøÀÌ ¸¹ÀÌ »ý±â´Âµ¥, ƯÈ÷ ƯÀÌÇÑ ¸ð¾çÀ» ÇϹǷΠÀ̸¦ ¼Ò¾Æ ½ÀÁøÀ̶ó°í Çϸç, Áõ¼¼¿¡ µû¶ó À¯À¯¾Æ ¾È¸é µÎºÎ ±Þ¼º ½ÀÁø, À¯¾Æ Áö·ç¼º ½ÀÁø, ¼Ò¾Æ °ÇÁ¶¼º ½ÀÁøÀÇ 3°¡Áö·Î ±¸ºÐµÈ´Ù.
  • infantile melanodontia
    ½Å»ý¾Æ Èæ»ö Ä¡¾ÆÁõ
  • infantile paralysis
    ¼Ò¾Æ ¸¶ºñ, ¼Ò¾Æ³ú¼º ¿îµ¿ ½ÇÁ¶¼º ¸¶ºñ
    µ¿ÀǾî=
  • infantile perseveration
    À¯¾Æ±â ¾ð¾îÀÇ ÀÜÁ¸
  • infantile stiff skin syndrome
    ¿µ¾Æ ÇǺΠ°æÁ÷ ÁõÈıº
  • infantile swallow
    À¯¾Æ¼º ¿¬ÇÏ
  • infantile tooth
    À¯Ä¡
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
thiamine deficiency A nutritional condition produced by a deficiency of thiamine in the diet, characterised by anorexia, irritability, and weight loss. Later, patients experience weakness, peripheral neuropathy, headache, and tachycardia. In addition to being caused by a poor diet, thiamine deficiency in the united states most commonly occurs as a result of alcoholism, since ethanol interferes with thiamine absorption. In countries relying on polished rice as a dietary staple, beriberi prevalence is very high.
(12 Dec 1998)
thiamine <chemical> 3-((4-amino-2-methyl-5-pyrimidinyl)methyl)-5-(2- hydroxyethyl)-4-methylthiazolium chloride.
Chemical name: Thiazolium, 3-((4-amino-2-methyl-5-pyrimidinyl)methyl)-5-(2-hydroxyethyl)-4-methyl- chloride
(12 Dec 1998)
thiamine monophosphate <chemical> Thiamine dihydrogen phosphate ester. The monophosphate ester of thiamine.
Synonym: monophosphothiamine; vitamin b1 monophosphate.
Chemical name: Thiazolium, 3-((4-amino-2-methyl-5-pyrimidinyl)methyl)-4-methyl-5-(2-(phosphonooxy)ethyl)-, chloride
(12 Dec 1998)
thiamine pyrophosphatase <enzyme> The coenzyme form of vitamin B1 (thiamine), deficiency of which causes beri beri. Forms the prosthetic group of pyruvate dehydrogenase, _ ketoglutarate dehydrogenase and transketolase, in which it is involved in transfer of a 2 carbon unit. Marker for the trans cisternae of the Golgi complex.
(18 Nov 1997)
thiamine pyrophosphate <biochemistry> Co carboxylase. A cofactor that has an unusually acidic carbon atom able to form carbon carbon bonds. Found in pyruvate dehydrogenase and transketolase.
(18 Nov 1997)
thiamine triphosphate <chemical> 3-((4-amino-2-methyl-5-pyrimidinyl)methyl)-4-methyl-5-(4,6,8,8-tetrahydroxy-3,5,7-trioxa-4,6,8-triphosphaoct-1-yl)thiazolium hydroxide, inner salt, p,p',p''-trioxide. The triphosphate ester of thiamine. In leigh's disease, this compound is present in decreased amounts in the brain due to a metabolic block in its formation.
Chemical name: Thiazolium, 3-((4-amino-2-methyl-5-pyrimidinyl)methyl)-4-methyl-5-(4,6,8,8-tetrahydroxy-3,5,7-trioxa-4,6,8-triphosphaoct-1-yl)-, inner salt, P,P',P''-trioxide
(12 Dec 1998)
aggressive infantile fibromatosis A childhood counterpart of abdominal or extra-abdominal desmoid tumours, characterised by firm subcutaneous nodules that grow rapidly in any part of the body that invade locally and recur but do not metastasize.
(05 Mar 2000)
autism, infantile A syndrome beginning in infancy and characterised by a lack of responsiveness to other people, gross impairment in verbal and nonverbal communication skills, and bizarre responses to the environment.
(12 Dec 1998)
progressive infantile spinal muscular atrophy Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised.
Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy.
(05 Mar 2000)
spasms, infantile Primary generalised epileptic seizures occurring in infants between birth and twelve months of age consisting of brief synchronous contractions of the neck, torso, and both arms. These seizures often occur in infants with underlying neurologic diseases. The prognosis for these infants is grave, with approximately ninety percent developing mental retardation in addition to their seizures. The eeg has a typical hypsarrhythmia pattern. The spasms and hypsarrhythmia have a tendency to disappear over the first three to five years of life, only to be replaced by other forms of generalised seizures. Infantile spasms sometimes respond to valproic acid or acth.
(12 Dec 1998)
supravalvar aortic stenosis-infantile hypercalcaemia syndrome <syndrome> Supravalvar aortic stenosis associated with elfin facies, mental retardation, and hypercalcaemia; usually sporadic; perhaps an irregular dominant trait.
(05 Mar 2000)
diffuse infantile familial sclerosis <radiology> Dysmyelinating disease, autosomal recessive, usually presents by 1 yr, specific enzyme deficiency identified, rapid spontaneous nystagmus, poikilothermia
Synonym: Krabbe leukodystrophy
(12 Dec 1998)
infantile Pertaining to an infant or to infancy.
Origin: L. Infantilis
(18 Nov 1997)
infantile acute haemorrhagic oedema of the skin A generally benign form of cutaneous vasculitis, characterised by ecchymotic purpura, often in a cockade pattern, and inflammatory oedema in infants.
(05 Mar 2000)
infantile autism A severe emotional disturbance of childhood characterised by qualitative impairment in reciprocal social interaction and in communication, language, and social development.
Synonym: autistic disorder, childhood schizophrenia, early infantile autism, Kanner's syndrome.
(05 Mar 2000)
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