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  • Hallervorden-Spatz syndrome
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  • hallervoden-spatz disease
    ÇÒ·¯º¸µç-½´ÆÄÂê º´, Hallervoden-Spatz º´
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  • hallervoden-spatz disease
    ÇÒ·¯º¸µç-½´ÆÄÂê º´, Hallervoden-Spatz º´
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HSD Hallervorden-Spatz disease; honestly significant difference; hydroxysteroid dehydrogenase; hypertoni...
HSS Hallermann-Streiff syndrome; Hallervorden-Spatz syndrome; Henoch-Schonlein syndrome; high-speed supe...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 2 ÆäÀÌÁö: 1
HSD Hallervorden Spatz disease
HSS Hallervorden Spatz syndrome
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
Spatz, Hugo <person> German neurologist and psychiatrist, 1888-1969.
See: Hallervorden-Spatz disease, Hallervorden-Spatz syndrome.
(05 Mar 2000)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 7 ÆäÀÌÁö: 1
Hallervorden-Spatz syndrome <neurology, syndrome> A progressive hereditary disorder with marked reduction in the number of myelin sheaths of the globus pallidus and substantia nigra with accumulation of iron pigment.
Manifestations include dysarthria, progressive mental deterioration, and corticospinal and extrapyramidal motor signs.
CT findings: high-signal lesions in globus pallidus bilaterally.
MRI findings: (T2-weighted spin-echo), hypointensity in globus pallidus (iron accumulation), small area of hyperintensity in internal segment (so-called eye of the tiger sign) corresponding to area of gliosis and vacuolation.
Inheritance: autosomal recessive.
(20 Mar 2000)
Weidel, Hugo <person> Austrian chemist, 1849-1899.
See: Weidel's reaction.
(05 Mar 2000)
Wintersteiner, Hugo <person> Austrian ophthalmologist, 1865-1918.
See: Wintersteiner rosettes.
(05 Mar 2000)
Schiff, Hugo <person> German chemist in Florence, 1834-1915.
See: Schiff base, Schiff's reagent, Kasten's fluorescent Schiff reagents, periodic acid-Schiff stain, ninhydrin-Schiff stain for proteins.
(05 Mar 2000)
Schottmueller, Hugo <person> German physician, 1867-1936.
See: Schottmueller's bacillus, Schottmueller's disease.
(05 Mar 2000)
Schutz, Hugo <person> 19th century German anatomist.
See: Schutz' bundle.
(05 Mar 2000)
HUGO Human Genome Organisation (the international organisation concerned with human genome research).
(12 Dec 1998)
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  • Hugo
    Victor(1802-1885) À§°í(ÇÁ¶û½ºÀÇ ÀÛ°¡,½ÃÀÎ,±ØÀÛ°¡)
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