| 영문 | porphyria | 한글 | 포르피린증 |
|---|---|---|---|
| 설명 | 포르피린 또는 그 전구물질의 형성이나 배설의 현저한 증가를 특징으로 하는 포르피린 대사장애에 대한 총칭. 네 개의 피롤핵이 메틸기로 연결된 포피린유도체의 총칭이다. 측쇄에 메틸기, 에틸기, 비닐기, 프로피온산기 등이 들어간 유로포피린, 코프로포피린, 프로토포피린, 헤마토포피린 등이 알려져 있다. 포르피린환에 Fe2+가 들어간 GPA은 글로빈과 결합하여 혈색소를 구성한다. 철포르피린으로서는 헤모글로빈, 시토크롬, 카타라아제 등이 있고, Mg2+를 갖는 것으로서는 엽록소가 있다. 생체조직 중, 주로 골수의 어린 적혈구 그리고 간에서 이루어지는 헴합성의 중간대사물질로, 혈색소나 각종 헴단백의 소재가 된다. 헴합성 이상에 의해 적혈구, 혈장, 소변, 대변의 포르피린체가 증가한다. 헴합성의 이상은 각 형의 포피리아, 빈혈, 납중독 등에서 볼 수 있다. |
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| ECG | Electro-Cardio-Graphy(-Gram); 심전도 = EKG 1. Conducting System Structu... |
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| PMD | Progressive Muscular Dystrophy; 진행성 근이영양증 Types of PMD(Progressive Muscular Dystroph... |
| TAPVR | Total Anomalous Pulmonary Venous Return = TAPVC 4 Types of TAPVR &... |
| AIP | Acute Intermittent Porphyria; 급성 간혈증 Porphyria |
| CEP | Congenital Erythropoetic Porphyria(= Gnther Disease; 선천성 조혈기성 Porphyria |
| SA | South African |
|---|---|
| AIP | Acute Intermittent Porphyria |
| CEP | Congenital erythropoietic porphyria |
| HEP | Hepatoerythropoietic porphyria |
| PCT | Porphyria Cutanea Tarda |
| South African type porphyria | Porphyria characterised by abdominal pain and neuropsychiatric abnormalities, by dermal sensitivity to light and mechanical trauma, by increased faecal excretion of proto-and coproporphyrin, and by increased urinary excretion of d-aminolevulinic acid, porphobilinogen, and porphyrins; due to a deficiency of protoporphyrinogen oxidase; autosomal dominant inheritance. Synonym: protocoproporphyria hereditaria, South African type porphyria. (05 Mar 2000) |
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| South African tick-bite fever | A typhus-like fever of South Africa caused by Rickettsia rickettsii and usually characterised by primary eschar and regional adenitis, rigors, and maculopapular rash on the fifth day, often with severe central nervous system symptoms. (05 Mar 2000) |
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| africa south of the sahara | All of africa except northern africa (africa, northern). (12 Dec 1998) |
| south | Lying toward the south; situated at the south, or in a southern direction from the point of observation or reckoning; proceeding toward the south, or coming from the south; blowing from the south; southern; as, the south pole. "At the south entry. <botany> " South-Sea tea See Yaupon. 1. To turn or move toward the south; to veer toward the south. 2. <astronomy> To come to the meridian; to cross the north and south line; said chiefly of the moon; as, the moon souths at nine. Origin: Southed; Southing. Source: Websters Dictionary (01 Mar 1998) |
| south africa | A republic in southern africa, the southernmost part of africa. It has three capitals: pretoria (administrative), cape town (legislative), and bloemfontein (judicial). The history is a fabric interwoven with hostile activity among the native tribes, particularly the zulus, the boers (dutch settlers), and the british. Officially the republic of south africa since 1960, it was called the union of south africa 1910-1960. (12 Dec 1998) |
| south american blastomycosis | A chronic fungal infection caused by Paracoccidioides brasiliensis, characterised by primary pulmonary lesions with dissemination to many visceral organs. Common findings include ulcerative granuloma lesions to the buccal mucosa (inner lining of the cheek) and nasal mucosa that extend to the surrounding skin. Generalised lymphangitis is also typical. More commonly seen in South America and the tropics. (27 Sep 1997) |
| South American trypanosomiasis | Trypanosomiasis caused by Trypanosoma (or Schizotrypanum) cruzi and transmitted by certain species of reduviid (triatomine) bugs. In its acute form, it is seen most frequently in young children, with swelling of the skin at the site of entry, most often the face, and regional lymph node enlargement; in its chronic form it can assume several aspects, commonly cardiomyopathy, but megacolon and megaesophagus also occur; natural reservoirs include dogs, armadillos, rodents, and other domestic, domiciliated, and wild mammals. Synonym: Chagas' disease, Chagas-Cruz disease, Cruz trypanosomiasis. (05 Mar 2000) |
| south Australia | A state in south central Australia. Its capital is adelaide. It was probably first visited by f. Thyssen in 1627. Later discoveries in 1802 and 1830 opened up the southern part. It became a british province in 1836 with this self-descriptive name and became a state in 1901. (12 Dec 1998) |
| south southerly | <zoology> The old squaw; so called in imitation of its cry. Synonym: southerly, and southerland. See Old. Source: Websters Dictionary (01 Mar 1998) |
| new south wales | A state in southeastern Australia. Its capital is sydney. It was discovered by captain cook in 1770 and first settled at botany bay by marines and convicts in 1788. It was named by captain cook who thought its coastline resembled that of south wales. (12 Dec 1998) |
| indians, south american | An ethnic group belonging to the mongoloid racial stock in south america. (12 Dec 1998) |
| acute intermittent porphyria | <gastroenterology, haematology> A group of rare inherited metabolic disorders that result from a disturbance in porphyrin metabolism, causing increased formation and excretion of porphyrin or its precursors. It is caused by hepatic overproduction of d-aminolevulinic acid, which has greatly increased urinary excretion and of porphobilinogen, and some increase of uroporphyrin, due to a deficiency of porphobilinogen deaminase. Clinical features: intermittent acute attacks of hypertension, abdominal colic, psychosis, and polyneuropathy, but with no photosensitivity. It is exacerbated by the ingestion of certain drugs such as; barbiturates). Inheritance: autosomal dominant. (20 Sep 2002) |
| acute porphyria | <gastroenterology, haematology> A group of metabolic disorders that result from a disturbance in porphyrin metabolism, causing increased formation and excretion of porphyrin or its precursors. Acute intermittent porphyria is a rare inherited (autosomal dominant) form that can result in abdominal pain, photosensitivity and neurological disturbances. The various forms can be differntiated measuring various blood prophyrins. (27 Sep 1997) |
| bovine porphyria | Porphyria as a mendelian recessive trait in certain breeds of cattle. (05 Mar 2000) |
| variegate porphyria | Porphyria characterised by abdominal pain and neuropsychiatric abnormalities, by dermal sensitivity to light and mechanical trauma, by increased faecal excretion of proto-and coproporphyrin, and by increased urinary excretion of d-aminolevulinic acid, porphobilinogen, and porphyrins; due to a deficiency of protoporphyrinogen oxidase; autosomal dominant inheritance. Synonym: protocoproporphyria hereditaria, South African type porphyria. (05 Mar 2000) |
| congenital erythropoietic porphyria | A group of metabolic disorders that result from a disturbance in porphyrin metabolism, causing increased formation and excretion of porphyrin or its precursors. Acute intermittent porphyria is a rare inherited (autosomal dominant) form that can result in abdominal pain, photosensitivity and neurological disturbances. The various forms can be differntiated measuring various blood prophyrins. Inheritance: autosomal dominant. (27 Sep 1997) |
제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
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제품명 |
판매사 |
보험코드 | 성분/함량 | 구분/보험급여 |
|---|