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  • Pierre Robin syndrome
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  • Bernard-Soulier disease
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  • bernard-soulier syndrome
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PRS Personality Rating Scale; Pierre Robin syndrome; plasma renin substrate; proctorectosigmoidoscopy
BSS Bernard-Soulier Syndrome
BSS Bachelor of Sanitary Science; balanced salt solution; Bernard-Soulier syndrome; black silk suture; b...
B-SS Bernard-Soulier syndrome
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 3 ÆäÀÌÁö: 1
BSS Bernard Soulier Syndrome
SLSJ Saguenay Lac Saint Jean
SLSJ Saguenay-Lac St-Jean
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  • Bernard-Soulier disease
    º£¸£³ª¸£-¼ú¸®¿¡ º´, Bernard-Soulier º´
    Å©±â¿Í ÇüŰ¡ ´Ù¾çÇÑ Ç÷¼ÒÆÇÀ» Ư¡À¸·Î ÇÏ´Â »ó¿°»öü ¿­¼º À¯Àü¼º ÁúȯÀ¸·Î, Ç÷¼ÒÆÇ ¸·Àº Ç÷Àå vWF
CancerWEB ¿µ¿µ ÀÇÇлçÀü ¸ÂÃã °Ë»ö °á°ú : 1 ÆäÀÌÁö: 1
Soulier, Jean Pierre <person> French haematologist, *1915.
See: Bernard-Soulier disease, Bernard-Soulier syndrome.
(05 Mar 2000)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
Changeux, Jean-Pierre <person> French 20th-century biochemist.
See: Monod-Wyman-Changeux model.
(05 Mar 2000)
Bernard-Soulier disease An autosomal recessive disorder of absent or decreased platelet membrane glycoproteins Ib, IX, and V (the receptor for factor VIII R. This deficiency can lead to a failure to bind von Willebrand factor, causing moderate bleeding.
(05 Mar 2000)
Bernard Soulier syndrome <haematology, syndrome> A congenital disorder where the platelets lack receptors which allow them to adhere to the walls of blood vessels. The genetic deficiency in platelet membrane glycoprotein Ib allows platelets to aggregate normally (c.f. Glanzmann's thrombasthenia) but they do not stick to collagen of sub endothelial basement membrane. The net result is a platelet function disorder that causes a prolonged bleeding time.
Symptoms include nosebleeds, easy bruising, heavy menstrual periods, bleeding gums and increased post-operative bleeding. Avoidance of aspirin, anti-inflammatories or any other agents which can cause bleeding is critical.
(06 Oct 1997)
Beclard, Pierre <person> French anatomist, 1785-1825.
See: Beclard's anastomosis, Beclard's hernia, Beclard's triangle.
(05 Mar 2000)
Berthelot, Pierre Eugene Marcellin <person> French chemist, 1827-1907.
See: Berthelot reaction.
(05 Mar 2000)
Bonnier, Pierre <person> French clinician, 1861-1918.
See: Bonnier's syndrome.
(05 Mar 2000)
Brasdor, Pierre <person> French surgeon, 1721-1798.
See: Brasdor's method.
(05 Mar 2000)
Broca, Pierre <person> French surgeon, neurologist, and anthropologist, 1824-1880.
See: Broca's angles, Broca's aphasia, Broca's basilar angle, Broca's facial angle, Broca's area, Broca's parolfactory area, Broca's diagonal band, Broca's centre, Broca's field, Broca's fissure, Broca's formula, Broca's visual plane, Broca's pouch.
(05 Mar 2000)
Budin, Pierre <person> French gynecologist, 1846-1907.
See: Budin's obstetrical joint.
(05 Mar 2000)
Rayer, Pierre <person> French physician, 1793-1867.
See: Rayer's disease.
(05 Mar 2000)
Marie, Pierre <person> French neurologist, 1853-1940.
See: Marie's ataxia, Charcot-Marie-Tooth disease, Bamberger-Marie disease, Bamberger-Marie syndrome, Marie-Strumpell disease, Strumpell-Marie disease, Brissaud-Marie syndrome, Foix-Cavany-Marie syndrome.
(05 Mar 2000)
Vernier, Pierre <person> French mathematician, 1580-1637.
See: Vernier acuity.
(05 Mar 2000)
Maroteaux, Pierre <person> French medical geneticist, *1926.
See: Maroteaux-Lamy syndrome.
(05 Mar 2000)
Gerdy, Pierre <person> A French surgeon, 1797-1856.
See: Gerdy's fibres, Gerdy's fontanel, Gerdy's hyoid fossa, Gerdy's ligament, Gerdy's interatrial loop, Gerdy's tubercle.
(05 Mar 2000)
Mauriac, Pierre <person> French physician, *1882.
See: Mauriac's syndrome.
(05 Mar 2000)
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