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  • seizure
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MERRF Syndrome Myoclonic Epilepsy & Ragged Red Fibers Syndrome
MTA malignant teratoma, anaplastic; medical technical assistant; medical technology assessment; metatars...
SME severe myoclonic epilepsy
SMEI severe myoclonic epilepsy of infancy
DISC   ; Supratentorial Lesion(brain lesion)½Ã
    --Destructive lesion -...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
JME Juvenile Myoclonic Epilepsy
MERRF Myoclonic Epilepsy and Ragged Red Fibers
MERRF Myoclonic epilepsy with ragged-red fibers
PME Progressive myoclonic epilepsy
SMEI Severe myoclonic epilepsy in infancy
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myoclonic seizure Seizure associated with single or repetitive myoclonic jerks.
(05 Mar 2000)
myoclonic Showing myoclonus.
(05 Mar 2000)
myoclonic astatic epilepsy A petit mal variant characterised by atonic (drop attacks) and tonic or tonic-clonic attacks in neurologically disabled (hemiplegic, ataxic, etc.) children with mental retardation; characterised in EEG by 2/sec spike and wave discharges; usually progresses in spite of medication.
(05 Mar 2000)
epilepsy, myoclonic A progressive encephalopathy characterised by myoclonic jerks (single or repetitive muscle contractions involving one body part or the entire body), mental retardation, and ataxia. The disease, an autosomal recessive form of epilepsy, occurs usually at puberty. The most significant pathological findings are lafora's inclusion bodies, which contain mucopolysaccharides.
(12 Dec 1998)
epilepsy with myoclonic absences A form of generalised epilepsy characterised by absence seizures, severe bilateral rhythmic clonic jerks often associated with tonic contraction, and an EEG 3 Hz spike and wave pattern. Age of onset is usually around seven years and males are more often affected.
(05 Mar 2000)
juvenile myoclonic epilepsy An epilepsy syndrome typically beginning in early adolescence, and characterised by early morning myoclonic jerks that may progress into a generalised tonic-clonic seizure. A genetic disorder: some families have had gene linkage to chromosome-6. The EEG is characterised by generalised polyspike and wave discharges at 4-6 Hz.
(05 Mar 2000)
absence seizure <neurology> A type of seizure that in contrast to the grand mal seizure, are noted for their brevity and for the degree of loss of awareness (brief staring spell) accompanied by minimal motor manifestations. A common form of childhood epilepsy.
(06 Oct 1997)
akinetic seizure Seizure characterised by sudden loss of muscle tone.
Synonym: akinetic seizure.
(05 Mar 2000)
atonic seizure Seizure characterised by sudden loss of muscle tone.
Synonym: akinetic seizure.
(05 Mar 2000)
atypical absence seizure An absence seizure associated with an EEG pattern of irregular or slow spike and wave at less than 2.5 Hz or paroxysmal fast activity on an abnormally slow background EEG.
(05 Mar 2000)
audiogenic seizure A reflex seizure precipitated by loud noises, rare in humans. Audiogenic seizures in rodents are an animal model of epilepsy.
(05 Mar 2000)
major motor seizure A grand mal seizure or other convulsive seizure.
(05 Mar 2000)
gelastic seizure A seizure characterised by laughing. This seizure type is often accompanied by hypothalamic lesions, such as hamartomas.
(05 Mar 2000)
generalised seizure <neurology> A type of seizure that results in loss of consciousness, generalised muscle contractions, urinary incontinence, tongue biting and a post-ictal state (confusion and lethargy) following cessation of the seizure.
Synonym: grand-mal seizure.
See: epilepsy.
(03 Jul 1999)
generalised tonic-clonic seizure <neurology> A type of seizure that results in loss of consciousness, generalised muscle contractions, urinary incontinence, tongue biting and a post-ictal state (confusion and lethargy) following cessation of the seizure.
Synonym: grand-mal seizure.
See: epilepsy.
(03 Jul 1999)
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