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    Poikiloderma of Civatte
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Civatte, Achille <person> French dermatologist, 1877-1956.
See: Civatte bodies, Civatte's disease, poikiloderma of Civatte.
(05 Mar 2000)
Civatte bodies Eosinophilic hyaline spherical body's seen in or just beneath the epidermis, particularly in lichen planus, formed by necrosis of individual basal cells.
Synonym: colloid bodies.
(05 Mar 2000)
Civatte's disease poikiloderma of Civatte
poikiloderma A variegated hyperpigmentation and telangiectasia of the skin, followed by atrophy.
Origin: poikilo-+ G. Derma, skin
(05 Mar 2000)
poikiloderma atrophicans and cataract The rothmund-thomson syndrome, a genetic disorder with numerous features affecting skin (premature aging, excess pigmentation, dilated blood vessels),eyes ( uvenile cataract), nose (saddle nose), teeth (maldeveloped), skeletal system (congenital bone defects) hair (abnormal), gonads (underdevelopment) limbs (soft tissue contractures), growth (short stature). Blood (anaemia) and a tendency to develop a type of bone cancer (osteogenic sarcoma). The rts gene is on chromosome 8. The syndrome is recessive so to be affected with rts a child has to have two rts genes, one from each parent.
(12 Dec 1998)
poikiloderma atrophicans vasculare A rare condition that simulates chronic radiodermatitis in appearance; may eventuate as mycosis fungoides.
Synonym: parakeratosis variegata, parapsoriasis lichenoides.
Poikiloderma of Civatte, reticulated pigmentation and telangiectasia of the sides of the cheeks and neck; common in middle-aged women.
Synonym: Civatte's disease.
(05 Mar 2000)
poikiloderma congenitale An autosomal recessive syndrome occurring principally in females, characterised by the presence of reticulated, atrophic, hyperpigmented, telangiectatic cutaneous plaques, often accompanied by juvenile cataracts, saddle nose, congenital bone defects, disturbances in the growth of hair, nails, and teeth, and hypogonadism.
(12 Dec 1998)
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