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Najjar, Victor <person> U.S. Physician and biochemist, *1914.
See: Crigler-Najjar syndrome.
(05 Mar 2000)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 14 ÆäÀÌÁö: 1
Crigler-Najjar disease <syndrome> A rare genetic defect (autosomal recessive) where there is the inability to form bilirubin glucuronide due to the absence of the enzyme bilirubin-glucuronoside glucuronosyl transferase, finding include jaundice and irreversible brain damage in the severe form.
Inheritance: autosomal recessive.
(27 Sep 1997)
Crigler-Najjar syndrome <syndrome> A rare genetic defect (autosomal recessive) where there is the inability to form bilirubin glucuronide due to the absence of the enzyme bilirubin-glucuronoside glucuronosyl transferase, finding include jaundice and irreversible brain damage in the severe form.
Inheritance: autosomal recessive.
(27 Sep 1997)
Babes, Victor <person> Roumanian bacteriologist, 1854-1926.
See: Babesia, Babes' nodes, Babes-Ernst bodies.
(05 Mar 2000)
Marshall, Victor <person> U.S. Urologist, *1913.
See: Marshall-Marchetti-Krantz operation.
(05 Mar 2000)
Victor-Michaelis-Menten equation <chemistry> Equation derived from a simple kinetic model for a single-substrate non-cooperative enzyme-catalyzed reaction that successfully accounts for the hyperbolic adsorption isotherm) relationship between substrate concentration and reaction rate.
V = Vmax x S/(S + Km), where V is the initial velocity of the reaction, Km is the Michaelis constant, Vmax is the maximum rate approached by very high substrate concentrations and S is the initial substrate concentration.
Similar equations can be derived for conditions in which the product is present and for multisubstrate enzymes.
Synonym: Victor-Michaelis-Menten equation.
(12 Jul 2000)
von Ebner, Victor <person> Austrian histologist, 1842-1925.
See: Ebner's glands, Ebner's reticulum, imbrication lines of von Ebner, incremental lines of von Ebner.
(05 Mar 2000)
Mikity, Victor <person> U.S. Radiologist, *1919.
See: Wilson-Mikity syndrome.
(05 Mar 2000)
Mucha, Victor <person> Austrian dermatologist, 1877-1919.
See: Mucha-Habermann disease, Mucha-Habermann syndrome.
(05 Mar 2000)
Hanot, Victor <person> French physician, 1844-1896.
See: Hanot's cirrhosis.
(05 Mar 2000)
Henri, Victor <person> French 20th-century biochemist.
See: Michaelis-Menten equation.
(05 Mar 2000)
Hensen, Victor <person> German anatomist and physiologist, 1835-1924.
See: Hensen's canal, Hensen's cell, Hensen's disk, Hensen's duct, Hensen's knot, Hensen's line, Hensen's node, Hensen's stripe.
(05 Mar 2000)
Schilling, Victor <person> German haematologist, 1883-1960.
See: Schilling's blood count, Schilling's band cell, Schilling's index, Schilling test, Schilling type of monocytic leukaemia.
(05 Mar 2000)
Horsley, Sir Victor <person> English surgeon, 1857-1916.
See: Horsley's bone wax.
(05 Mar 2000)
Eisenmenger, Victor <person> German physician, 1864-1932.
See: Eisenmenger's complex, Eisenmenger's defect, Eisenmenger's disease, Eisenmenger's syndrome, Eisenmenger's tetralogy.
(05 Mar 2000)
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