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MMD mass median diameter; minimum morbidostatic dose; moyamoya disease; myotonic muscular dystrophy
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MMD Moyamoya disease
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    1. ³»°æ µ¿¸Æ ¸»´ÜºÎ¿¡ ÇùÂø, Æó»öÀÇ ¾ç»óÀÌ ³ªÅ¸³ª´Â Áúȯ.Àª¸®½º µ¿¸Æ·û Æó»öÁõ, ³úÀúºÎ ÀÌ»ó Ç÷°ü¸ÁÁõÀ̶ó°íµµ ÇÑ´Ù. µ¹¹ß¼º ³ú Ç÷°ü ºÎÀüÁõ¿¡¼­ º¼ ¼ö Àִµ¥ ³ú ÀúºÎÀÇ Á¤»ó Ç÷°ü ´ë½Å¿¡ ¼Òµ¿¸ÆÀÇ Èñ¹ÌÇÑ ±×¹° ¸ð¾ç
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moyamoya disease <radiology> Progressive obstructive/occlusive cerebral arteritis, affecting distal ICA at bifurcation into its branches (anterior 2/3 of circle of Willis), usually involving both hemispheres, aetiology: unknown, age: predominantly in children and young adults. Clinical: headaches, behavioural disturbances, recurrent hemiparetic attacks radiographic findings: large network of vessels in BG (puff of smoke) and upper brainstem fed by, basilar a., ACA, MCA (dilatation of lenticulo-striates and anterior choroidal a.), anastomosis between leptomeningeal and dural meningeal arteries complication: subarachnoid haemorrhage (occasionally)
(12 Dec 1998)
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  • Moyamoya Disease - »õâ A chronic cerebral vasculopathy primarily occurring in childhood and characterized by slowly progressive carotid artery narrowing and occlusion at the base of the brain. An extensive network of anastomoses forms between branches of the carotid arteries, resulting in a characteristic angiographic appearance. The condition may be idiopathic (classic moyamoya disease) or occur in association with ANEMIA, SICKLE CELL; DOWN SYNDROME; CRANIOCEREBRAL TRAUMA; RADIOTHERAPY induced arterial injury; NEUROFIBROMATOSIS; and other diseases. Clinical manifestations include hemiparesis, headache, seizures, and delayed mental development. In older individuals, this disease may present as SUBARACHNOID HEMORRHAGE. (From Adams et al., Principles of Neurology, 6th ed, p831; Clin Neurol Neurosurg 1997 Oct;99 Suppl 2:S36-8)
    Synonyms : Moya-Moya Disease, Moyamoya Disease, Classic, Moyamoya Disease, Primary, Moyamoya Disease, Secondary, Moyamoya Syndrome, Classic Moyamoya Disease, Disease, Classic Moyamoya, Disease, Moya-Moya, Disease, Primary Moyamoya, Moya Moya Disease
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moyamoya d. cerebral ischemia due to occlusion of large arteries at the circle of Willis, with secondary proliferation of an abnormal network of vessels at the base of the brain, causing progressive neurologic disability; hemorrhage may occur from the dilated vessels.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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