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LPL Lipo-Protein Lipase
BSSL bile salt-stimulated lipase
CEL carboxyl-ester lipase
HSL herpes simplex labialis; hormone-sensitive lipase
HTGL hepatic triglyceride lipase
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ATLPL Adipose tissue lipoprotein lipase
BSSL Bile salt stimulated lipase
BSDL Bile salt-dependent lipase
CEL Carboxyl ester lipase
HL Hepatic Lipase
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Aeromonas hydrophilia lipase-acyltransferase <enzyme> A member of the lipase family; a distinct group of lipolytic enzymes which have a novel active site structure
Registry number: EC 3.1.1.-
Synonym: gcat
(26 Jun 1999)
diacylglycerol lipase <enzyme> An enzyme of the hydrolase class that catalyses the reaction of triacylglycerol and water to yield diacylglycerol and a fatty acid anion. The enzyme hydrolyzes triacylglycerols in chylomicrons, very-low-density lipoproteins, low-density lipoproteins, and diacylglycerols. It occurs on capillary endothelial surfaces, especially in mammary, muscle, and adipose tissue. Genetic deficiency of the enzyme causes familial hyperlipoproteinaemia type I.
Chemical name: Triacylglycero-protein acylhydrolase
Registry number: EC 3.1.1.34
(12 Dec 1998)
diglyceride lipase <enzyme> An enzyme of the hydrolase class that catalyses the reaction of triacylglycerol and water to yield diacylglycerol and a fatty acid anion. The enzyme hydrolyzes triacylglycerols in chylomicrons, very-low-density lipoproteins, low-density lipoproteins, and diacylglycerols. It occurs on capillary endothelial surfaces, especially in mammary, muscle, and adipose tissue. Genetic deficiency of the enzyme causes familial hyperlipoproteinaemia type I.
Chemical name: Triacylglycero-protein acylhydrolase
Registry number: EC 3.1.1.34
(12 Dec 1998)
familial lipoprotein lipase deficiency An rare inherited disorder where there is a deficiency of an enzyme (lipoprotein lipase) which breaks down fat molecules, causing the accumulation of fats or lipoproteins in the blood.
Symptoms in infancy include abdominal pain (appears as if its colic), failure to thrive and skin lesions (xanthomas).
(27 Sep 1997)
familial lipoprotein lipase inhibitor An inhibitor found in certain individuals that inhibits lipoprotein lipase resulting in accumulation of chylomicrons, VLDL, and triacylglycerols; similar in symptoms to familial lipoprotein lipase deficiency.
(05 Mar 2000)
lipase <enzyme> An enzyme that catalyses the hydrolysis of fats (monoglycerides, diglycerides and triglycerides) to glycerol and fatty acids. Calcium ions are usually required.
(13 Nov 1997)
lipase test A diagnostic test based on the measurement of lipase in blood and urine as an indicator of pancreatic disease.
(05 Mar 2000)
lipoprotein lipase <enzyme> An enzyme of the hydrolase class that catalyses the reaction of triacylglycerol and water to yield diacylglycerol and a fatty acid anion. The enzyme hydrolyzes triacylglycerols in chylomicrons, very-low-density lipoproteins, low-density lipoproteins, and diacylglycerols. It occurs on capillary endothelial surfaces, especially in mammary, muscle, and adipose tissue. Genetic deficiency of the enzyme causes familial hyperlipoproteinaemia type I.
Chemical name: Triacylglycero-protein acylhydrolase
Registry number: EC 3.1.1.34
(12 Dec 1998)
lipoprotein lipase deficiency, familial A rare familial condition characterised by massive chylomicronaemia and decreased levels of other lipoproteins. It is due to deficiency of lipoprotein lipase, an alkaline triglyceride hydrolase which catalyses an important step in the extrahepatic removal of triglyceride-rich lipoproteins from the blood.
(12 Dec 1998)
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