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"Hereditary Sensory and Autonomic Neuropathies"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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¿µ¹® sensory nerve ÇÑ±Û °¨°¢½Å°æ
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  °¨°¢¼¼Æ÷°¡ ¹ÞÀº ÀÚ±ØÀ» ÁßÃ߽Ű濡 Àü´ÞÇϴ ½Å°æ. ´«À̳ª ÇǺΠµî¿¡ Àִ °¨°¢±â°¡ ¿ÜºÎ·ÎºÎÅÍ ÀÚ±ØÀ» ¹ÞÀ¸¸é °¨°¢½Å°æÀ» °ÅÃĠô¼ö¿Í ´ë³ú°ÑÁú±îÁö °¨°¢ÀÌ Àü´ÞµÈ´Ù. À̿͠°°ÀÌ ¿ÜºÎ·ÎºÎÅÍ ³»ºÎ¸¦ ÇâÇØ Àü´ÞµÇ´Â °¨°¢½Å°æÀº ±¸½É¼º ½Å°æ°èÅëÀ̸ç, ¿ø½É¼º ¿îµ¿½Å°æ°èÅë ¹× ÀÚÀ²½Å°æ°èÅë¿¡ ÇÊÀûÇϴ ¸»ÃʽŰæÀÇ ÇϳªÀÌ´Ù. ÀÌ °¨°¢½Å°æ¿¡´Â Èİ¢½Å°æ(³ú½Å°æ¥°)-½Ã°¢½Å°æ(³ú½Å°æ¥±)-´«µ¹¸²½Å°æ(³ú½Å°æ¥²)-»ïÂ÷½Å°æ(³ú½Å°æ¥´)-¾ó±¼½Å°æ(³ú½Å°æ¥¶)-û°¢½Å°æ(³ú½Å°æ¥·)-ÇôÀενŰæ(³ú½Å°æ¥¸)-¹ÌÁֽŰæ(³ú½Å°æ¥¹) ¹× Ã´¼ö½Å°æÀÌ ÀÖ´Ù. °¨°¢½Å°æ Áß ¹ÌÁֽŰæÀ» Á¦¿ÜÇϸ頸ðµÎ µÎºÎ¿¡ ºÐÆ÷µÇ¾î ÀÖ°í, Èİ¢½Å°æ-½Ã°¢½Å°æ-û°¢½Å°æÀÇ ¼¼°¡Áö´Â Æ¯È÷ ºÐÈ­µÈ °¨°¢»óÇǸ¦ Áö¹èÇÑ´Ù. ÇôÀενŰæÀº ¹Ì°¢ÀÇ ¸»´ÜÀåÄ¡¿Í ±× ¹ÛÀÇ ºÎºÐ¿¡ ¿¬°áµÇ°í ¹ÌÁֽŰæÀº Èä°­°ú º¹°­ÀÇ ±â°ü¿¡ ºÐÆ÷µÇ¾î ±¸½É¼º Ãæ°ÝÀ» ÁßÃß¿¡ Àü´ÞÇϸ砻ïÂ÷½Å°æÀº Ã´¼öÀÇ °¢ ¸¶µð¿¡ Àִ ½Å°æ¿¡ ÇØ´çÇÏ¿©(¸Ó¸®ÀÇ ÇǺÎ-Á¡¸· µîÀǠǥ¸é°¨°¢°ú ½ÉºÎ°¨°¢À» °üÀåÇÑ´Ù. Ã´¼öÀÇ °¨°¢½Å°æ°èÅë¿¡µµ ÇǺο͠½ÉºÎ, ³»ÀåÀÇ ºÐÆ÷¿¡ µû¸¥ ±¸º°ÀÌ ÀÖ´Ù. 
¿µ¹® Dilatation and Curettage(D & C) ÇÑ±Û Àڱñܾ¼ú, ÀڱøñÈ®Àå
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  ÀÚ±ÃÀ̶õ Å¾ư¡ ¼öŵǾ ºÐ¸¸Àü±îÁö ¹ßÀ°ÇÏ°í ¼ºÀåÇϴ °ø°£ÀÌ´Ù. Àڱüӿ¡ º´º¯ÀÌ ÀÖ¾î ÀÓ½ÅÀÌ °è¼ÓµÉ ¼ö ¾ø°Å³ª ¾Æ´Ï¸é ´Ù¸¥ ÀÌÀ¯·Î ÀӽŵǾî Àִ Å¾Ƹ¦ Á¦°ÅÇϰíÀÚ ÇÒ °æ¿ì¿¡ »ç¿ëµÇ´Â ¹æ¹ýÀÌ´Ù. ¿©±â¼­ ±Ü¾î³»±â À§ÇÏ¿©´Â ¿ì¼± ÀÚ±ÃÀÇ ÀÔ±¸¿¡ ÇØ´çÇϴ ÀڱøñÀ» È®Àå½ÃÄѾߠÇÑ´Ù. ¿©±â¿¡´Â ±Þ¼ÓÈ÷ È®ÀåÀ» ½ÃµµÇϴ ¹ý°ú ¼­¼­È÷ È®ÀåÀ» ½ÃµµÇϴ 2°¡Áö ¹æ¹ýÀÌ ÀÖ´Ù. ÀڱøñÀ» ±Þ¼ÓÈ÷ È®ÀåÇÒ ¶§´Â Çì°¡¸£ ¸ñ°üÈ®Àå±â(Hegar's dilatator)¸¦ »ç¿ëÇÑ´Ù. À̰ÍÀº ÀÛÀº ±Ý¼Ó¸·´ë·Î ÀÛÀº Å©±âºÎÅÍ Å« Å©±â±îÁö ´Ù¾çÇÑ Å©±â°¡ À־ ¿ì¼± ÀÛÀº ¸·´ë·Î ½ÃÀÛÇÏ¿© Á¡Á¡ Å« Å©±âÀÇ ¸·´ë¸¦ Àڱøñ¿¡ ³Ö¾î¼­ ÀڱøñÀ» È®Àå½ÃŲ´Ù. ¼­¼­È÷ È®Àå½Ãų ¶§´Â Laminaria tent¸¦ ¸ñ°ü¿¡ »ðÀÔÇϴ ¹æ¹ýÀ» »ç¿ëÇÑ´Ù. Laminaria tent¶õ ÇØÃʷΠ¸¸µç ÀÛÀº ¸·´ë·Î ¼öºÐÀ» Èí¼öÇϸé Á¡Á¡ ´Ã¾î³ª´Â ¼ºÁúÀÌ ÀÖ´Ù. À̰ÍÀ» ÀÚ±ÃÀÇ ¸ñ¿¡ ³ÖÀ¸¸é À̰ÍÀÌ ¼öºÐÀ» Èí¼öÇÏ¿© ´Ã¾î³ª¹Ç·Î ÃµÃµÈ÷ ÀÚ±ÃÀÇ ¸ñÀÌ ´Ã¾î³­´Ù. ÀڱøñÀÌ ÃæºÐÈ÷ ´Ã¾î³ª¸é ±× ¼ÓÀ¸·Î ³¡ÀÌ ¼ù°¡¶ôó·³ »ý±ä ±â±¸¸¦ ³Ö¾î¼­ ÀڱüÓÀÇ º´º¯À̳ª ÀӽŵȠžƸ¦ ±Ü¾î³»´Âµ¥ ¿©±â¿¡ »ç¿ëµÇ´Â ¼ù°¡¶ôó·³ »ý±ä ±â±¸¸¦ Å¥·¿À̶ó°í ÇÑ´Ù. Ãʱâ ÀÓ½ÅÁßÀý Áï À¯»ê°ú °°Àº ÀӽŰú °ü·ÃµÈ °æ¿ì»Ó¸¸ ¾Æ´Ï¶ó, ºñÀӽŠÀÚ±ÃÀÇ Àڱ󻸷Á¶Á÷ÀǠäÃë ¹× Á¦°Å¸¦ À§Çؼ­µµ ÇàÇØÁö´Â ¼ö±âÀÌ´Ù. À̴ ¿øÄ¢ÀûÀ¸·Î ¸¶ÃëÇÏ¿¡ ½Ç½ÃµÇ´Â °ÍÀ¸·Î Àڱøñ°üÀ» È®ÀåÇÏ°í ±â±¸·Î Àڱà³»¿ë¹°À» Á¦°ÅÇϰí Å¥·¿À¸·Î Àڱ󻺮À» ±ú²ýÀÌ ÇÑ´Ù. ÀÚ±Ãõ°øÀ̳ª ÀڱøñÀÇ ÆÄ¿­ µîÀÇ À§ÇèÀÌ µû¸£¸ç, ¼ö¼úÈÄ °¨¿° ¶Ç´Â ÃâÇ÷ µî¿¡ ´ëÇÑ ÁÖÀǰ¡ ÇÊ¿äÇÏ´Ù.
¿µ¹® autonomic nervous system ÇÑ±Û ÀÚÀ²½Å°æ°è
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  »ç¶÷ÀÇ ÀÇÁö¿Í °ü°è¾øÀÌ, Ä§À» È긮°Å³ª ¼ÒÈ­¿îµ¿ µî°ú °°Àº ½º½º·Î Á¶Á¤ÀÌ µÇ¾î ¿òÁ÷À̴ ½Å°æ°èÀ̸砿©±â¿¡´Â ´ÙÀ½°ú °°Àº µÎ °¡Áö°¡ ÀÖ´Ù.
  
  1.±³°¨½Å°æ°è(sympathetic nervous system)-»ç¶÷ÀÌ À§Çè»óÅ¿¡ À̸£·¶À» °æ¿ì¿¡ ÈïºÐÀÌ µÇ´Â ÀÚÀ²½Å°æ°è. ÁɹڼöÀÇ Áõ°¡, ¼ÒÈ­±â ¿îµ¿ÀÇ °¨¼Ò µîÀÇ ÀÏÀÌ À̰÷À» ÅëÇØ¼­ ÀϾ´Ù. ±³°¨½Å°æÀÌ ÈïºÐµÇ¸é ±³°¨½Å°æÀÇ ¸»´Ü¿¡¼­ epinephrine, norepinephrine µîÀÇ ¹°ÁúÀÌ ºÐºñµÇ°í À̰͵鿡 ÀÇÇØ¼­ ¸»ÃÊÀå±â°¡ º¯È­¸¦ ÀÏÀ¸Å²´Ù. ÇÏÁö¸¸ Àå±â¿¡ µû¶ó¼­ epinephrineÀ̳ª norepinephrineÀÇ ¼ö¿ëü¸¦ °¡Áö°í À־ ¿©·¯ °¡Áö ´Ù¸¥ Àå±âÀÇ ¹ÝÀÀÀ» º¼ ¼ö°¡ ÀÖ´Ù. ¼ö¿ëü´Â ´ÙÀ½°ú °°´Ù.
  
    -¾ËÆÄ¼ö¿ëü(alpha-receptor): ¸»ÃÊÇ÷°üÀÇ ¼öÃà, ±â°üÁöÀÇ ¼öÃà, µ¿°øÀÇ ±ÙÀ°ÀÇ ¼öÃà
  
    -º£Å¸1¼ö¿ëü(beta 1-receptor): ½ÉÀå¿¡ Á¸ÀçÇϴ ¼ö¿ëü, ½ÉÀåÀ» »¡¸® ¶Ù°ÔÇϴ ¿ªÇÒÀ» ÇÑ´Ù.
  
    -º£Å¸2¼ö¿ëü(beta 2-receptor): Ç÷°üÀÇ ÀÌ¿Ï, ±â°üÁöÀÇ ÀÌ¿Ï, Áï °¢ Àå±âµéÀº ±× Àå±â°¡ °¡Áö°í Àִ ±³°¨½Å°æÀÇ ¼ö¿ëü¿¡ µû¶ó ±³°¨½Å°æÀÇ ÈïºÐ(±³°¨½Å°æ ¸»´Ü¿¡¼­ÀÇ epinephrineÀÇ ºÐºñ)¿¡ ´ëÇÑ ¹ÝÀÀÀÌ ´Þ¶óÁø´Ù(¿¹-±³°¨½Å°æÀÌ ÈïºÐ½Ã¿¡ beta 1-¼ö¿ëü¸¦ °¡Áö°í Àִ ½ÉÀåÀº »¡¸® ¶Ù°Ô µÈ´Ù. ±³°¨½Å°æ ÈïºÐ½Ã¿¡ µ¿°øÀÇ ±ÙÀ°ÀÌ ¼öÃàÇØ¼­ µ¿°øÀÇ Å©±â°¡ Ä¿Áø´Ù)
  
  2.ºÎ±³°¨½Å°æ°è(parasympathetic nervous system)-±³°¨½Å°æ°ú ¹Ý´ë·Î ÀÛ¿ëÇÑ´Ù. Áï »ç¶÷ÀÌ Á¹¸®°Å³ª ½¯ °æ¿ì¿¡ ÈïºÐÇÑ´Ù. ºÎ±³°¨½Å°æÀÌ ÈïºÐÇÒ ¶§¿¡´Â ½Å°æÀÇ ¸»´Ü¿¡¼­ ¾Æ¼¼Ä¥Äݸ°ÀÇ ºÐºñ°¡ ÀϾ°í À̰ÍÀ¸·Î ÀÎÇØ¼­ °¢ Àå±âÀÇ º¯È­°¡ ÀϾ´Ù.
´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • hereditary motor sensory neuropathy
    À¯Àü¿îµ¿°¨°¢½Å°æº´(Áõ)
  • autonomic bladder
    ÀÚÀ²¹æ±¤
  • autonomic blocking agent
    ÀÚÀ²½Å°æÂ÷´ÜÁ¦
  • autonomic crisis
    ÀÚÀ²½Å°æ¼ºÀ§±â
  • autonomic disturbance
    ÀÚÀ²½Å°æÀå¾Ö
  • autonomic drug
    ÀÚÀ²½Å°æ¾à
  • autonomic ganglion
    ÀÚÀ²½Å°æÀý
  • autonomic hyperreflexia
    ÀÚÀ²½Å°æ¹Ý»çÇ×Áø
  • autonomic imbalance
    ÀÚÀ²½Å°æºÒ±ÕÇü
  • autonomic instability
    ÀÚÀ²½Å°æºÒ¾ÈÁõ
  • autonomic insufficiency
    ÀÚÀ²½Å°æºÎÀü
  • autonomic nerve
    ÀÚÀ²½Å°æ
  • autonomic nerve fiber
    ÀÚÀ²½Å°æ¼¶À¯
  • autonomic nerve plexus
    ÀÚÀ²½Å°æ¾ó±â
  • autonomic nervous system
    ÀÚÀ²½Å°æ°èÅë, ÀÚÀ²½Å°æ°è
´ëÇÑÀÇÇù Çʼö ÀÇÇпë¾îÁý »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • diphteria and tetanus toxoids and acellular pert vaccine
    °³·®µðÇÇÆ¼
  • hereditary motor sensory neuropathy
    À¯Àü¿îµ¿°¨°¢½Å°æº´Áõ
  • autonomic disturbance
    ÀÚÀ²½Å°æÀå¾Ö
  • hereditary
    À¯Àü-
  • autonomic nerve
    ÀÚÀ²½Å°æ
  • autonomic neuropathy
    ÀÚÀ²½Å°æº´Áõ
  • hereditary spherocytosis
    À¯ÀüµÕ±ÙÀûÇ÷±¸Áõ, À¯Àü±¸ÇüÀûÇ÷±¸Áõ
  • kidney ureter and bladder
    ÄáÆÏ¿ä°ü¹æ±¤´Ü¼øÃÔ¿µ
  • dilatation and curettage
    Àڱñܾ¼ú, ÀÚ±Ã¼ÒÆÄ¼ú
  • peritoneal oocyte and sperm transfer
    »ý½Ä¼¼Æ÷º¹°­³»À̽Ä, »ý½Ä¼¼Æ÷º¹°­³»Àü´Þ
  • sensory disturbance
    °¨°¢Àå¾Ö
  • sensory dissociation
    °¨°¢Çظ®
  • sensory nerve
    °¨°¢½Å°æ
  • sensory organ
    °¨°¢±â°ü
  • sensory paralysis
    °¨°¢¸¶ºñ
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  • ¿µ¹®
    ÇѱÛ
  • hereditary motor sensory neuropathy
    À¯Àü¿îµ¿°¨°¢½Å°æº´Áõ
  • autonomic bladder
    (¢¡autonomous bladder) ÀÚÀ²¹æ±¤
  • autonomic crisis
    ÀÚÀ²À§±â
  • autonomic disturbance
    ÀÚÀ²½Å°æÀå¾Ö
  • autonomic drug
    ÀÚÀ²½Å°æ¾à
  • autonomic excitation
    ÀÚÀ²½Å°æÈïºÐ
  • autonomic ganglion
    ÀÚÀ²½Å°æÀý
  • autonomic hyperreflexia
    ÀÚÀ²½Å°æ°ú´Ù¹Ý»ç
  • autonomic imbalance
    ÀÚÀ²½Å°æºÒ±ÕÇü
  • autonomic instability
    ÀÚÀ²½Å°æºÒ¾ÈÁõ
  • autonomic insufficiency
    ÀÚÀ²½Å°æºÎÁ·
  • autonomic nerve
    ÀÚÀ²½Å°æ
  • autonomic neuron
    ÀÚÀ²½Å°æ¼¼Æ÷
  • autonomic neuropathy
    ÀÚÀ²½Å°æº´Áõ
  • autonomic reflex
    ÀÚÀ²½Å°æ¹Ý»ç
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  • ¿µ¹®
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  • hereditary motor and sensory neuropathy
    À¯Àü¼º¿îµ¿ °¨°¢½Å°æº´Áõ
  • hoof and mouth disease =foot and mouth d.
    ±¸Á¦(¿ª)(Ï¢ð´æ¹) º´.
  • posterior root [sensory root]
    µÚ»Ñ¸®
  • primary sensory area
    ÀÏÂ÷°¨°¢¿µ¿ª (¡­çÐæ´).
  • MAC-BAR(minimum alveolar concentration-blockade of autonomic response)
    ÀÚÀ²½Å°æ¾ïÁ¦ ÃÖ¼ÒÆóÆ÷³»³óµµ
  • ganglia of autonomic plexuses
    ÀÚÀ²½Å°æ¾ó±â½Å°æÀý
  • ganglion of autonomic plexus<³ª> gangliona plexusum autonomicorum
    ÀÚÀ²(½Å°æ)ÃѽŰæÀý.
  • renal autonomic plexus
    ½Å ÀÚÀ²½Å°æÃÑ
  • DSM-I=Diagnostic and Statistical Manual of Mental Disorders-I
    Á¤½ÅÀå¾Ö(º´)Áø´ÜÅë°èÆí¶÷ Á¦ 1ÆÇ
  • Death and dying
    »ç¸Á°úÀÓÁ¾
  • ENT =ear, nose and throat
    À̺ñÀÎÈİú(ÇÐ)
  • General anesthesia, reticular activating system and.
    Àü½Å¸¶Ãë(îïãóئö­), ¸Á»óüȰ¼ºÈ­°è(ØÑßÒô÷üÀàõûùͧ)
  • Gravity, cardiac output and
    Áß·Â(ñìÕô), ½É¹ÚÃâ·®(ãýÚÑõóÕá)
  • KUB= kidney, ureter and bladder
    ½Å-´¢°ü-¹æ±¤ ´Ü¼øÃÔ¿µ
  • Kell antigen and antibody
    ÄÌÇ׿øÇ×ü
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  • ¿µ¹®
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  • hereditary motor and sensory neuropathy
    À¯Àü¼º¿îµ¿ °¨°¢½Å°æº´Áõ
  • hoof and mouth disease =foot and mouth d.
    ±¸Á¦(¿ª)(Ï¢ð´æ¹) º´.
  • papilomatosis of Gougerot and Carteaud => confluent and reticulated pa
  • autonomic
    ÀÚÀ²¼º(í»ëÏàõ)
  • autonomic ataxia
    ÀÚÀ²½Å°æ¼º ¿îµ¿½ÇÁ¶.
  • autonomic bladder
    ÀÚÀ²(¼º)¹æ±¤(¡­Û¹ÎÍ).
  • autonomic blocking agent
    ÀÚÀ²½Å°æÂ÷´Ü<ºÀ¼â>Á¦(í»ëÏãêÌèó´Ó¨<Üæáð>ð¥).
  • autonomic branches
    ÀÚÀ²½Å°æ°¡Áö
  • autonomic center
    ÀÚÀ²½Å°æÁßÃß(¡­ñéõÒ)
  • autonomic disturbance
    ÀÚÀ²½Å°æÀå¾Ö(¡­ãê Ìèî¡äô).
  • autonomic drug
    ÀÚÀ²½Å°æ°è(ÀÛ¿ë)¾à.
  • autonomic dysreflexia
    ÀÚÀ² ÅëÇչݻçÀå¾Ö ?
  • autonomic dysreflexia
    ÀÚÀ²½Å°æ¼º ¹Ý»çºÎÀüÁõ
  • autonomic epilepsy
    ÀÚÀ²½Å°æ°è °£Áú
  • autonomic excitation
    ÀÚÀ²½Å°æ¼º ÈïºÐ
´ëÇÑÇØºÎÇÐȸ ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
  • ¿µ¹®
    ÇѱÛ
  • Autonomic nerve
    ÀÚÀ²½Å°æ
    [¿¾ ¿ë¾î] ÀÚÀ²½Å°æ
  • Autonomic branches
    ÀÚÀ²½Å°æ°¡Áö
    [¿¾ ¿ë¾î] ÀÚÀ²½Å°æÁö
  • Autonomic nerve fiber
    ÀÚÀ²½Å°æ¼¶À¯
    [¿¾ ¿ë¾î] ÀÚÀ²½Å°æ¼¶À¯
  • Autonomic fibers [Visceral fibers]
    ÀÚÀ²½Å°æ¼¶À¯ [³»Àå½Å°æ¼¶À¯]
    [¿¾ ¿ë¾î] ÀÚÀ²½Å°æ¼¶À¯
  • Autonomic neuron
    ÀÚÀ²½Å°æ¼¼Æ÷
    [¿¾ ¿ë¾î] ÀÚÀ²½Å°æ¼¼Æ÷
  • Autonomic nerve plexus
    ÀÚÀ²½Å°æ¾ó±â
    [¿¾ ¿ë¾î] ÀÚÀ²½Å°æÃÑ
  • Autonomic plexus
    ÀÚÀ²½Å°æ¾ó±â
    [¿¾ ¿ë¾î] ÀÚÀ²½Å°æÃÑ
  • Ganglia of autonomic plexuses
    ÀÚÀ²½Å°æ¾ó±â½Å°æÀý
    [¿¾ ¿ë¾î] ÀÚÀ²½Å°æÃѽŰæÀý
  • Autonomic ganglia
    ÀÚÀ²½Å°æÀý
    [¿¾ ¿ë¾î] ÀÚÀ¯½Å°æÀý
  • Autonomic ganglia
    ÀÚÀ²½Å°æÀý
    [¿¾ ¿ë¾î] ÀÚÀ²½Å°æÀý
  • Autonomic ganglion [Visceral ganglion]
    ÀÚÀ²½Å°æÀý [³»Àå½Å°æÀý]
    [¿¾ ¿ë¾î] ÀÚÀ²½Å°æÀý
  • Sensory epithelial cell
    °¨°¢»óÇǼ¼Æ÷
    [¿¾ ¿ë¾î] °¨°¢»óÇǼ¼Æ÷
  • Sensory root [Nasociliary root]
    °¨°¢½Å°æ»Ñ¸® [ÄÚ¼¶¸ðü½Å°æ»Ñ¸®]
    [¿¾ ¿ë¾î] Áö°¢±Ù
  • Sensory ganglia of cranial nerve [Cranial ganglia]
    ³ú½Å°æÀý
    [¿¾ ¿ë¾î] ³ú½Å°æÀý
  • Craniospinal ganglia [Sensory ganglia]
    ³úô¼ö½Å°æÀý [°¨°¢½Å°æÀý]
    [¿¾ ¿ë¾î] ³úô¼ö½Å°æÀý
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  • ¿µ¹®
    ÇѱÛ
  • sensory papillae
    °¨°¢À¯µÎ
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  • ¿µ¹®
    ÇѱÛ
  • hereditary code
    À¯Àü ºÎÈ£(ë¶îîݬûÜ)
  • hereditary material
    À¯Àü ¹°Áú(ë¶îîÚªòõ)
  • ball and stick model
    °ø ¸·´ë ¸ðµ¨
  • breakage and reunion model
    Àý´ÜÀç°áÇÕ(ï·Ó¨î¢Ì¿ùê)¸ðµ¨
  • cut and patch repair
    Àß¶ó±é±â ¼öº¹(áóÜÖ) (ÔÒ) excision repair
  • Dean and Webb method
    µò°ú¿þºê ¹ý(Ûö)
  • Jacob and Monod hypothesis
    Àð°ö¡¤¸ð³ë ¼³(àã)
  • knife and fork model
    ³ªÀÌÇÁÆ÷Å© ¸ðµ¨
  • "Koshland, Nemethy, and Filmer model"
    "ÄÚ½¬·»µå,³×¸ÞƼ,ÇÊ¸Ó ¸ðµ¨"
  • Lavoisier and Laplace law
    ¶óº¸¾ÆÁ¦ ¶óÇÁ¶óÀ̽º¹ýÄ¢(ÛööÎ)
  • lock and key theory
    ÀÚ¹°¼è-¿­¼èÀÌ·Ð(ìµÖå)
  • modification and restriction
    ¼ö½Ä(áóãÞ)°ú Á¦ÇÑ(ð¤ùÚ)
  • "Monod, Wyman, and Changeux model"
    ¸ð³ë.¿ÍÀ̸¸.¼§Á¶¸ðµ¨
  • Park and Johnson method
    ÆÄÅ© Á¸½¼ ¹ý(Ûö)
  • patch and cut repair
    Àý´Ü ºÎ ¼öº¹(ï·Ó¨Ý¾áóÜÖ)
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KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
HSAN hereditary sensory and autonomic neuropathy
HMSN hereditary motor and sensory neuropathy
HMSN Hereditary Motor-Sensory Neuropathy
HSN hereditary sensory neuropathy; hospital satellite network
AH abdominal hysterectomy; absorptive hypercalciuria; accidental hypothermia; acetohexamide; acid hydro...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 1
HMSN Hereditary Motor and Sensory Neuropathies
HMSN Hereditary motor and sensory neuropathy
HMSN I Hereditary motor and sensory neuropathy type 1
HMSN hereditary motor sensory neuropathy
AD Autonomic Dysreflexia
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
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CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
neuropathies, hereditary sensory and autonomic A group of inherited disorders in which there is selective involvement of the peripheral sensory and autonomic neurons and degeneration of fibres by axonal atrophy and degeneration. Five types of disorders have been described and classified type I through type v.
(12 Dec 1998)
neuropathies, hereditary motor and sensory A group of slowly progressive inherited disorders in which the predominant involvement is the peripheral motor neurons with lesser involvement of the peripheral sensory neurons. Neuronal degeneration and atrophy are characteristic of these disorders. Some of the associated characteristics are phytanic acid excess, optic atrophy, and retinitis pigmentosa.
(12 Dec 1998)
hereditary sensory radicular neuropathy Neuropathy characterised by the occurrence of severe, relapsing foot ulcerations of neuropathic origin, destruction of terminal digits of feet and hands, and a loss of sensation; autosomal dominant inheritance is associated with onset in the second decade or later.
(05 Mar 2000)
amyloid neuropathies Disorders of the peripheral nervous system associated with deposition of amyloid. Amyloid neuropathies may result from non-hereditary or hereditary amyloidosis. Several different forms of familial amyloid neuropathies have been described, most of which have specific mutations in the prealbumin gene.
(12 Dec 1998)
hereditary deafness and nephropathy <nephrology, pathology> An inherited disorder involving damage to the kidneys, haematuria and hearing loss. In some individuals vision may also be affected. This genetic disease is uncommon.
Symptoms include loss of hearing, abnormal colour to urine, swelling, cough and decline in vision.
Inheritance: sex-linked autosomal dominant.
Incidence: 1 in 50,000.
Origin: Gr. Pathos = disease
(27 Sep 1997)
autonomic <physiology> Self controlling, functionally independent.
(02 Jan 1998)
autonomic agents Agents affecting the function of, or mimicking the actions of, the autonomic nervous system and thereby having an effect on such processes as respiration, circulation, digestion, body temperature regulation, certain endocrine gland secretions, etc.
(12 Dec 1998)
autonomic denervation The removal or interruption of some part of the autonomic nervous system for therapeutic or research purposes.
(12 Dec 1998)
autonomic disorder Disorganization of autonomic processes.
(05 Mar 2000)
autonomic epilepsy Episodes of autonomic dysfunction presumably due to diencephalic irritation.
Synonym: diencephalic epilepsy, vasomotor epilepsy, vasovagal epilepsy.
(05 Mar 2000)
autonomic fibres, postganglionic Nerve fibres which project from cell bodies of autonomic ganglia to synapses on target organs.
(12 Dec 1998)
autonomic fibres, preganglionic Nerve fibres which project from the central nervous system to autonomic ganglia. In the sympathetic division most preganglionic fibres originate with neurons in the intermediolateral column of the spinal cord, exit via ventral roots from upper thoracic through lower lumbar segments, and project to the paravertebral ganglia; there they either terminate in synapses or continue through the splanchnic nerves to the prevertebral ganglia. In the parasympathetic division the fibres originate in neurons of the brainstem and sacral spinal cord. In both divisions the principal transmitter is acetylcholine but peptide cotransmitters may also be released.
(12 Dec 1998)
autonomic ganglia Visceral ganglia.
See: autonomic nervous system.
(05 Mar 2000)
autonomic hyperreflexia <physiology> An autonomic response that may include hypertension, sweating, bradycardia and severe headache.
Autonomic hyperreflexia may occur secondary to an injury to the upper spinal cord, during cystoscopy or with distention of the bladder or colon.
(02 Jan 1998)
autonomic imbalance A lack of balance between sympathetic and parasympathetic nervous systems, especially in relation to the vasomotor disturbances.
Synonym: vasomotor imbalance.
(05 Mar 2000)
MeSH(Medical Subject Headings) ¸ÂÃã °Ë»ö (http://www.nlm.nih.gov) °á°ú : 1 ÆäÀÌÁö: 1
  • Hereditary Sensory and Autonomic Neuropathies - »õâ A group of inherited disorders characterized by degeneration of dorsal root and autonomic ganglion cells, and clinically by loss of sensation and autonomic dysfunction. There are five subtypes. Type I features autosomal dominant inheritance and distal sensory involvement. Type II is characterized by autosomal inheritance and distal and proximal sensory loss. Type III is DYSAUTONOMIA, FAMILIAL. Type IV features insensitivity to pain, heat intolerance, and mental deficiency. Type V is characterized by a selective loss of pain with intact light touch and vibratory sensation. (From Joynt, Clinical Neurology, 1995, Ch51, pp142-4)
    Synonyms : Congenital Insensitivity to Pain with Anhidrosis, HSAN (Hereditary Sensory Autonomic Neuropathy), Hereditary Sensory Autonomic Neuropathy, Type 1, Hereditary Sensory Autonomic Neuropathy, Type 2, Hereditary Sensory Autonomic Neuropathy, Type 4, HSAN Type Is
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