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Fabry, Johannes <person> German dermatologist, 1860-1930.
See: Fabry's disease.
(05 Mar 2000)
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 1
Fabry disease <disease> Storage disease due to deficiency of ceramide trihexosidase.
(18 Nov 1997)
fabry-perot interferometer <apparatus, physics> A type of interferometer with two parallel mirrors (with a variable separation of a few centimetres) arranged so that incoming light is reflected between them multiple times before ultimately being transmitted.
Useful in spectroscopy because it gives very good frequency resolution without losing too much of the incident signal.
(08 Mar 2000)
fabry's disease <disease> Lysosomal storage disease caused by a deficiency of alpha-galactosidase a and resulting in an accumulation of globotriaosylceramide in the renal and cardiovascular systems.
The disease is characterised by telangiectatic skin lesions, renal failure, and disturbances of the cardiovascular, gastrointestinal, and central nervous systems.
Inheritance: x-linked.
(08 Mar 2000)
Bronsted, Johannes <person> Danish physical chemist, 1879-1947.
See: Bronsted acid, Bronsted base, Bronsted theory.
(05 Mar 2000)
van der Waals, Johannes <person> Dutch physicist and Nobel laureate, 1837-1923.
See: van der Waals' forces.
(05 Mar 2000)
van Horne, Johannes <person> Dutch anatomist, 1621-1670.
See: van Horne's canal.
(05 Mar 2000)
Ranke, Johannes <person> German anthropologist and physician, 1836-1916.
See: Ranke's angle.
(05 Mar 2000)
Mikulicz, Johannes von-Radecki <person> Polish surgeon in Germany, 1850-1905.
See: Mikulicz' aphthae, Mikulicz' cells, Mikulicz clamp, Mikulicz' disease, Mikulicz' drain, Mikulicz' operation, Mikulicz' syndrome, Mikulicz-Vladimiroff amputation, Vladimiroff-Mikulicz amputation, Heineke-Mikulicz pyloroplasty.
(05 Mar 2000)
Waardenburg, Petrus Johannes <person> Dutch ophthalmologist, 1886-1979.
See: Waardenburg syndrome.
(05 Mar 2000)
Muller, Johannes <person> German anatomist, physiologist, and pathologist, 1801-1858.
See: Muller's capsule, Muller's duct, Muller's law, Muller's manoeuvre, Muller's tubercle.
(05 Mar 2000)
Purkinje, Johannes von <person> Bohemian anatomist and physiologist, 1787-1869.
See: Purkinje conduction, Purkinje images, Purkinje shift, Purkinje system, Purkinje cell, Purkinje's corpuscle, Purkinje's fibres, Purkinje's figures, Purkinje's layer, Purkinje's network, Purkinje's phenomenon, Purkinje-Sanson images.
(05 Mar 2000)
Oehler, Johannes <person> German physician, *1879.
See: Oehler's symptom.
(05 Mar 2000)
Orth, Johannes <person> German pathologist, 1847-1923.
See: Orth's fixative, Orth's stain.
(05 Mar 2000)
Esser, Johannes <person> Dutch surgeon, 1877-1946.
See: Esser graft, Esser operation.
(05 Mar 2000)
Zoon, Johannes <person> Dutch dermatologist, *1902.
See: balanitis of Zoon, Zoon's erythroplasia.
(05 Mar 2000)
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