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  • ipecac syrup
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  • maple syrup urine disease
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  • maple syrup urine disease
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  • syrup of ipecae
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  • CoA
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syr. syrupus; syrup
MSU maple sugar urine; maple syrup urine; medical studies unit; mid-stream urine; monosodium urate; myoc...
MSUD maple syrup urine disease
syr syrup [Lat. syrupus]; syringe
CoA Coarctation of Aorta
  - Complications
    1. Severe Hypertensi...
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HFCS High-Fructose Corn Syrup
MSUD Maple Syrup Urine Disease
HMG CoA 3-hydroxy-3-methylglutaroyl CoA
HMG-CoA reductase 3-Hydroxy-3-methylglutaryl CoA reductase
HMG-CoA 3-hydroxymethylglutaryl-CoA
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maple syrup urine See: maple syrup urine disease.
(05 Mar 2000)
maple syrup urine disease Hereditary disease due to deficiency of an enzyme involved in amino acid metabolism, characterised by urine that smells like maple syrup.
(12 Dec 1998)
syrup 1. A thick and viscid liquid made from the juice of fruits, herbs, etc, boiled with sugar.
2. A thick and viscid saccharine solution of superior quality (as sugarhouse sirup or molasses, maple sirup); specifically, in pharmacy and often in cookery, a saturated solution of sugar and water (simple sirup), or such a solution flavored or medicated. "Lucent sirups tinct with cinnamon." (Keats) Mixing sirup. See the Note under Dextrose.
Origin: F. Sirop (cf. It. Siroppo, Sp. Jarabe, jarope, LL. Siruppus, syrupus), fr. Ar. Sharab a drink, wine, coffee, sirup. Cf. Sherbet.
Source: Websters Dictionary
(01 Mar 1998)
disease, maple syrup urine Hereditary disease due to deficiency of an enzyme involved in amino acid metabolism, characterised by urine that smells like maple syrup.
(12 Dec 1998)
ipecac syrup A sweetened liquid medicinal preparation containing powdered ipecac extract, which contains the alkaloids emetine and cephaline; used as an emetic in certain cases of poisoning and (at lower doses) as an expectorant.
(05 Mar 2000)
ipecac (syrup) <chemical> A syrup made from the dried rhizomes of two different species, c. Ipecacuanha and c. Acuminata of cephaelis (or uragoga) of the rubiaciae; they contain emetine, cephaeline, psychotrine and other isoquinolines. Ipecac syrup is used widely as an emetic acting both locally on the gastric mucosa and centrally on the chemoreceptor trigger zone. It may also be used as an expectorant.
Pharmacological action: emetics, expectorants.
Chemical name: Ipecac
(12 Dec 1998)
butyryl-CoA acetoacetate CoA transferase <enzyme> Butyryl-CoA + acetoacetate yields butyrate + acetoacetyl-CoA
Registry number: EC 2.8.3.-
Synonym: butyryl-coenzyme a acetoacetate coenzyme a transferase
(26 Jun 1999)
malonyl-CoA-acetyl CoA-acyl carrier protein S-acyltransferase <enzyme> Specific for either malonyl-CoA or acetyl-CoA; a component of fatty acid synthase
Registry number: EC 2.8.3.-
Synonym: mcoa-acoa acp acyltransferase
(26 Jun 1999)
succinyl-CoA-3-hydroxy-3-methylglutarate CoA transferase <enzyme> Rat liver mitochondrial enzyme which catalyses transfer of a conezyme a molecule from succinyl-CoA to 3-hydroxy-3-methylglutarate
Registry number: EC 2.8.3.-
Synonym: succinylcoa-hmg CoA transferase, sca-hmg cat
(26 Jun 1999)
succinyl CoA propionate CoA-transferase <enzyme> Succinyl CoA and propionate gives propionyl CoA and succinate
Registry number: EC 2.8.3.-
Synonym: succinyl coenzyme a propionate coenzyme a-transferase
(26 Jun 1999)
enoyl-CoA hydratase - 3-hydroxyacyl-CoA dehydrogenase - dodecanoyl-coenzyme A delta-isomerase <chemical> Catalyses the second and third reactions of the fatty acid beta-oxidation cycle, converting enoyl-CoA to 3-ketoacyl-CoA; EC 4.2.1.17 and EC 1.1.1.35 and EC 5.3.3.8; consider also multifunctional protein-a
Synonym: peroxisomal bifunctional enzyme, enoyl-coenzyme a hydratase -- 3-hydroxyacyl-coenzyme a dehydrogenase, peroxisomal trifunctional enzyme, delta(3), delta(2)-enoyl-CoA isomerase--2-enoyl-CoA hydratase--3-hydroxyacyl-CoA dehydrogenase
(26 Jun 1999)
acetate-CoA ligase <enzyme> An enzyme that catalyses the formation of CoA derivatives from ATP, acetate, and CoA to form AMP, pyrophosphate, and acetyl CoA. It acts also on propionates and acrylates.
Chemical name: Acetate:CoA ligase (AMP-forming)
Registry number: EC 6.2.1.1
(12 Dec 1998)
acetate-succinate CoA-transferase <enzyme> Tritichomonas and trichomonas enzyme converts acetyl-CoA and succinate to acetate and succinyl-CoA
Registry number: EC 2.8.3.-
Synonym: acetate-succinate coenzyme a-transferase
(26 Jun 1999)
acetoacetyl-CoA Intermediate in the oxidation of fatty acids and in the formation of ketone bodies; also formed from two molecules of acetyl-CoA; major role is condensation with acetyl-CoA to form the important beta-hydroxy-beta-methylglutaryl-CoA.
Synonym: acetoacetyl-coenzyme A.
(05 Mar 2000)
acetoacetyl-CoA reductase An oxidoreductase catalyzing interconversion of a 3-oxoacyl-CoA and NADPH, and the corresponding d-3-hydroxyacyl-CoA, and NADP+. A step in fatty acid synthesis.
(05 Mar 2000)
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