| 4-hydroxyproline | 4-Hydroxy-2-pyrrolidinecarboxylic acid;the trans-l-isomer is an imino acid found among the hydrolysis products of collagen; not found in proteins other than those of connective tissue. A vitamin C deficiency will result in impaired formation of hydroxyproline. (05 Mar 2000) |
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| 4-hydroxyproline oxidase | A flavoenzyme that catalyses the conversion of 4-hydroxyproline to d'-pyrroline-3-hydroxy-5-carboxylate using FAD; this enzyme appears to be deficient in individuals with hyperhydroxyprolinaemia, an enzyme that catalyses the reaction of 4-hydroxyproline with NAD+ to form NADH and 4-oxoproline. Synonym: 4-oxoproline reductase. (05 Mar 2000) |
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