| muscular tunic of gallbladder | Muscular tunic of the gallbladder, consisting of layers of smooth muscle fibres coursing in various directions immediately external to the mucosa of the gallbladder. (05 Mar 2000) |
|---|---|
| muscular tunics | See: muscular coat. (05 Mar 2000) |
| progressive infantile spinal muscular atrophy | Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised. Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy. (05 Mar 2000) |
| progressive muscular atrophy | A serious neurologic disease that results from the progressive degeneration of the motor neurons. (27 Sep 1997) |
| progressive spinal muscular atrophy | One of the subgroups of motor neuron disease; a progressive degenerative disorder of the motor neurons of the spinal cord, manifested as progressive, often symmetrical, weakness and wasting, typically beginning in the distal portions of the limbs, particularly in the upper extremities, and spreading proximally; fasciculation potentials are often present, but evidence of corticospinal tract disease (e.g., increased deep tendon reflexes, Babinski sign) is not. (05 Mar 2000) |
| Hoffmann's muscular atrophy | Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised. Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy. (05 Mar 2000) |
| smooth muscular sphincter | A sphincter of smooth musculature. Synonym: smooth muscular sphincter. Origin: G. Lissos, smooth, + sphincter (05 Mar 2000) |
| spinal muscular atrophy | <radiology> 2nd most common autosomal recessive disease in Caucasians, pathology, degeneration of the spinal anterior horn cells, atrophy and wasting of skeletal muscles, types, SMA I = Werdnig-Hoffman disease: rapidly progressive, SMA II = intermediate form, SMA III = Kugelberg-Welander disease: slowly progressive, uncommon adult forms, usual presentations, floppy baby, arthrogryposis, muscle weakness in infancy, diagnosis, weakness and wasting with areflexia, electrophysiology shows anterior horm cell disease, genetics, linked to chromosome 5q., neuronal apoptosis inhibitory protein (NAIP) gene, survival motor neuron (SMN) gene (12 Dec 1998) |
| striated muscular sphincter | A sphincter made up of striated musculature. Synonym: striated muscular sphincter. Origin: rhabdo-+ G. Sphinkter, sphincter (05 Mar 2000) |
| idiopathic muscular atrophy | A form of progressive muscular atrophy in which the disease begins in the muscle and not in the spinal centres. Synonym: Erb atrophy, idiopathic muscular atrophy. (05 Mar 2000) |
| infantile muscular atrophy | Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised. Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy. (05 Mar 2000) |
| infantile progressive spinal muscular atrophy | Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised. Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy. (05 Mar 2000) |
| infantile spinal muscular atrophy | Transmitted as autosomal recessive on chromosome 5q. Progressive dysfunction of the anterior horn cells in the spinal cord and brainstem cranial nerves with profound weakness and bulbar dysfunction occurring in the first two years of life. Three groups, based on age of clinical onset, are recognised. Synonym: familial spinal muscular atrophy, Hoffmann's muscular atrophy, infantile muscular atrophy, infantile progressive spinal muscular atrophy, progressive infantile spinal muscular atrophy, Werdnig-Hoffmann disease, Werdnig-Hoffmann muscular atrophy. (05 Mar 2000) |
| ischemic muscular atrophy | See: Volkmann's contracture. (05 Mar 2000) |
| electro-muscular | <physiology> Pertaining the reaction (contraction) of the muscles under electricity, or their sensibility to it. Source: Websters Dictionary (01 Mar 1998) |