| galactose tolerance test | A liver function test, based on the ability of the liver to convert galactose to glycogen, measured by the rate of excretion of galactose following ingestion or intravenous injection of a known amount; normally, less than 3 g appear in the urine within 5 hours after the ingestion of 40 g. (05 Mar 2000) |
|---|---|
| galactose-1-phosphatase | <enzyme> From rat brain; requires mg for activity; phosphate is potent inhibitor Registry number: EC 3.1.3.- (26 Jun 1999) |
| galactose-1-phosphate | A phosphorylated derivative of galactose that is key in galactose metabolism; accumulates in certain types of galactosaemia. (05 Mar 2000) |
| galactose-1-phosphate uridylyltransferase | <enzyme> An enzyme catalyzing the reaction of UTP and alpha-d-galactose 1-phosphate to form UDPgalactose and pyrophosphate, the second and most important step in the metabolism of d-galactose; a deficiency of this enzyme results in an accumulation of galactose, galactose-1-phosphate, and galactitol. (05 Mar 2000) |
| galactose-6-phosphate dehydrogenase | <enzyme> Possibly a ketoaldose, phosphorylated at primary alcoholic group; found in goat liver cytoplasm, requires nad, has high substrate specificity Registry number: EC 1.1.1.- Synonym: hexose-6-phosphate dehydrogenase (26 Jun 1999) |
| galactose-6-phosphate isomerase | <enzyme> Converts galactose 6-phosphate to tagatose 6-phosphate Registry number: EC 5.3.1.- Synonym: galactose 6-phosphate isomerase, gal-6-p isomerase, tagatose-6-phosphate isomerase (26 Jun 1999) |
| galactose-6-sulfatase | <enzyme> An enzyme that eliminates sulfur from the galactose-6-sulfate residues of certain mucopolysaccharides, producing 3,6-anhydrogalactose residues; it is absent in Morquio's syndrome type A. Synonym: galactose-6-sulfurase. (05 Mar 2000) |
| galactose-6-sulfurase | <enzyme> An enzyme that eliminates sulfur from the galactose-6-sulfate residues of certain mucopolysaccharides, producing 3,6-anhydrogalactose residues; it is absent in Morquio's syndrome type A. Synonym: galactose-6-sulfurase. (05 Mar 2000) |
| galactose-diphosphoglycosyl carrier lipid synthetase | <enzyme> Catalyses synthesis of gcl-pp-gal from udp gal and p-gcl; also catalyses exchange between the uridylyl moiety of udpgal and ump Registry number: EC 2.4.1.- (26 Jun 1999) |
| galactosemia | <biochemistry> A rare genetic (autosomal recessive) disorder characterised by the inability a defect in the enzyme (galactose 1 phosphate uridyl transferase) that converts galactose 1 phosphate into glucose 1 phosphate is absent. Excess galactose 1 phosphate accumulates in the blood and a variety of problems result. Inheritance: autosomal recessive. Origin: Gr. Haima = blood (27 Sep 1997) |
| galactosephosphates | Phosphoric acid esters of galactose. (12 Dec 1998) |
| galactosidase | <enzyme> One of a class of enzymes which cuts the glycosidic bond between the sugar galactose and another sugar molecule (of a different type than galactose). There are two subclasses - the alpha galactosidases and beta galactosidases - which cuts the two types of glycosidic bonds (alpha and beta, respectively). (09 Oct 1997) |
| galactosidases | <enzyme> A family of galactoside hydrolases that hydrolyze compounds with an o-galactosyl linkage. Registry number: EC 3.2.1.- (12 Dec 1998) |
| galactoside | A compound in which the H of the OH group on carbon-1 of galactose is replaced by an organic radical. (05 Mar 2000) |
| galactoside 2-fucosyltransferase | <enzyme> Synthesise blood group h; secretor (se) fucosyltransferase is the human counterpart of h fucosyltransferase; fut1 isolated from red cells and vascular endothelium Registry number: EC 2.4.1.69 Synonym: blood group h fucosyltransferase, alpha(1-2)fucosyltransferase, galactoside 2-alpha-l-fucosyltransferase, GDP-l-fucose-beta-d-galactoside 2-alpha-l-fucosyltransferase, blood group h alpha-2-fucosyltransferase, h-transferase, GDP-l-fucose-beta-d-galactosyl alpha-2-l-fucosyltransferase, GDPfg-2-fucosyltransferase, GDP-l-fucose-galactoside-2'-fucosyltransferase, beta-galactoside alpha-1,2-fucosyltransferase, alpha-2'-l-fucosyltransferase, 2-fucosyltransferase, secretor alpha-2-fucosyltransferase, se 2-fucosyltransferase, alpha-2-fucosyltransferase, fut1 gene product, fut2 gene product (26 Jun 1999) |