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"Amino Acid Metabolism, Inborn Errors"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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  • ¿µ¹®
    ÇѱÛ
  • dibasic acid
    ÀÌ¿°±â»ê
  • dicarboxylic acid
    µðÄ«¸£º¹½Ç»ê
  • dilute acid
    ¹±Àº»ê
  • essential fatty acid
    ÇʼöÁö¹æ»ê
  • ethylenediamine tetraacetic acid
    ¿¡Æ¿·»µð¾Æ¹Î»ç¾Æ¼¼Æ®»ê
  • fatty acid
    Áö¹æ»ê
  • fixed acid
    °íÁ¤»ê
  • folic acid
    ¿±»ê, Æú»ê
  • folinic acid
    Æú¸®´Ñ»ê
  • formic acid
    Æ÷¸§»ê, °³¹Ì»ê
  • free acid
    À¯¸®»ê
  • free fatty acid
    À¯¸®Áö¹æ»ê
  • fumaric acid
    Ǫ¸¶¸£»ê
  • gastric acid
    ˤȐ
  • general acid
    ÀϹݻê
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  • ¿µ¹®
    ÇѱÛ
  • glyceric acid
    ±Û¸®¼¼¸°»ê
  • glycocholic acid
    ±Û¸®ÄÚÄÝ»ê
  • glycolic acid
    ±Û¸®ÄÝ»ê
  • heteropoly acid
    ÇìÅ׷δÙÁß»ê
  • hippuric acid
    È÷Ǫ¸£»ê, ¸¶´¢»ê
  • humic acid
    È޹λê
  • hyaluronic acid
    È÷¾Ë·ç·Ð»ê
  • hydrochloric acid
    ¿°»ê
  • hydrocyanic acid
    È÷µå·Î½Ã¾È»ê
  • hydrofluoric acid
    ºÒÈ­¼ö¼Ò»ê
  • hydroxyindoleacetic acid
    È÷µå·Ï½ÃÀε¹¾Æ¼¼Æ®»ê
  • inosinic acid
    À̳ë½Å»ê
  • isothiocyanic acid
    ÀÌ¼ÒÆ¼¿À½Ã¾È»ê
  • ketonic acid
    ÄÉÅæ»ê
  • lactic acid
    Á¥»ê, ¶ôÆ®»ê
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  • ¿µ¹®
    ÇѱÛ
  • acid fast bacterium
    Ç×»ê(¼º) ¼¼±Õ.
  • acid fast organism
    Ç×»ê±Õ
  • acid fast stain
    Ç×»ê(¼º) ¿°»ö(¡­æøßä).
  • acid fastness
    Ç׻꼺
  • acid food
    »ê¼º½Äǰ.
  • acid forming
    »ê¹ß»ý(ß«Û¡ßæ)ÀÇ.
  • acid free diet
    ¹«»ê½ÄÀÌ.
  • acid hematin method
    »êÇ츶ƾ¹ý(¡­Ûö).
  • acid intoxication
    »êÁßµ¶(Áõ)(ß«ñéÔ¸ñø).
  • acid lipase deficiency
    »ê¼º ¸®ÆÄÁ¦ °áÇÌÁõ(ß«àõ¡­ÌÀù¹ñø)
  • acid mucopolysaccharide(s)
    »ê¼ºÁ¡´Ù´çÁú(ïÄÒýÓØòõ)
  • acid perfusion
    »ê°ü·ù(߫δêü), »êȯ·ù.
  • acid phosphatase
    »ê¼ºÆ÷½ºÆÄŸÁ¦
  • acid phosphatase
    »ê¼ºÆ÷½ºÆÄÅ×À̽ºÁ¦.
  • acid phosphatase
    »ê¼º Æ÷½ºÆÄÅ×À̽º(ß«àõ¡­)
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  • ¿µ¹®
    ÇѱÛ
  • abietolic acid
    ¾Æºñ¿¡Åç»ê.
  • acetic acid
    ¾Æ¼¼Æ®»ê
  • acetic acid
    ¾Æ¼¼Æ®»ê, ÃÊ»ê(õ³ß«).
  • acetoacetic acid
    ¾Æ¼¼Å侯¼¼Æ®»ê
  • acetoacetic acid
    ¾Æ¼¼Å侯¼¼Æ®»ê.
  • acetylsalicylic acid
    ¾Æ¼¼Æ¿»ì¸®½Ç»ê
  • acid phosphatase
    »êÀλêÈ¿¼Ò
  • acid alcohol
    »ê¼º¾ËÄÚ¿Ã.
  • acid ash diet
    »ê¼º½ÄÀÌ.
  • acid aspiration syndrome
    À§»ê ÈíÀÔ ÁõÈıº
  • acid bath
    »ê¿å(ß«é±).
  • acid burn
    »ê¼ºÈ­»ó
  • acid burn
    »ê¼º¿Ü»ó, »ê¼ºÈ­»ó.
  • acid catalyser
    »êÃ˸Å(ß«õºØÚ).
  • acid challenge test
    »ê Åõ¿©½ÃÇè
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  • ¿µ¹®
    ÇѱÛ
  • acid-fast
    Ç׻꼺 (ù÷ß«àõ)
  • acid-thiol ligase
    »ê(ß«)ŸÀ̿öóÀ̰ÔÀ̽º
  • adenylic acid
    ¾Æµ¥´Ò»ê(ß«)
  • aldaric acid
    ¾Ë´Ù¸£»ê(ß«)
  • aldonic acid
    ¾Ëµ·»ê(ß«)
  • alginic acid
    ¾Ë±ä»ê(ß«)
  • anthranilic acid
    ¾ÈÆ®¶ó´Ò»ê(ß«)
  • apurinic acid
    ¾ÆÆ÷¸°»ê(ß«)
  • apyrimidinic acid
    ¾ÆÇǸ®¹Ìµò»ê(ß«)
  • arachidic acid
    ¾Æ¶ó۵å»ê(ß«)
  • arachidonic acid
    ¾Æ¶ó۵·»ê(ß«)
  • arachidonic acid cascade
    ¾Æ¶ó۵·»ê(ß«) ÄɽºÄÉÀ̵å
  • ascorbic acid
    ¾Æ½ºÄÚ¸£ºó»ê(ß«)
  • aspartic acid
    ¾Æ½ºÆÄ¸£Æ®»ê (ß«)
  • aurinetricarboxylic acid
    ¾Æ¿ì¸°Æ®¸®Ä«¸£º¹½Ç»ê(ß«)
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PASA Para-Amino-Salicyclic Acid
  = PAS
AAA abdominal aortic aneurysm/aneurysmectomy; acne-associated arthritis; acquired aplastic anemia; acute...
AAAD aromatic amino acid decarboxylase
AAAE amino acid activating enzyme
AADC amino acid decarboxylase
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CAT Cationic amino acid transporter
D(-)AP5 D(-)-2-amino-5-phosphonopentanoic acid
D(-)APV D(-)-2-amino-5-phosphonovaleric acid
D(-)AP5 D(-)2-amino-5-phosphonovaleric acid
D-AAO D-Amino acid oxidase
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  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • cerebronic acid
    ¼¼·¹ºê·Ð»ê
    ½ºÇÎ°í¸¶ÀÌ¿¤¸°¿¡¼­ À¯µµµÇ¾î »ý±â´Â Áö¹æ »ê.
  • chamber acid
    ¿¬½Ç Ȳ»ê
  • chondroitin sulfuric acid
    Äܵå·ÎÀÌÆ¾ Ȳ»ê
    LeveneÀÌ ºÙÀÎ ±¸Á¶½ÄÀ¸·Î, ¿¬°ñÀÇ À¯Á¡Ã¼¿¡ µé¾î ÀÖ´Â ´ç´Ü¹éÁúÀÇ ¹èÇÕÁ·. °­ÇÏ°Ô °¡¼öºÐÇØÇϸé Äܵå·Î»ç¹Î, ÃÊ»ê, ±Û·çÄí·Ð»ê, Ȳ»êÀÌ »ý±ä´Ù.
  • chronic acid
    Å©·Ò»ê
  • conjugate acid
    ¦»ê
    °ø¾×¿°±â¿¡ ¾ç ÀüÀÚ¸¦ ÷°¡ÇÏ¿© Çü¼ºÇÑ È­ÇÐ ¹°Áú.
  • conjugated acid
    ¦ »ê, °ø¾× »ê, °áÇÕ »ê
  • corrosive acid
    ºÎ½Ä »ê
  • cyclamic acid
    »çÀÌŬ¶ó¹Î»ê
    À̰ÍÀÇ Ä®½·¿°°ú ³ªÆ®·ýÀº ÇѶ§ ºñ¿µ¾ç¼º °¨¹Ì·á·Î¼­ »çÅÁ ´ë¿ëǰÀ¸·Î ³Î¸® »ç¿ëµÇ¾úÀ¸³ª, µ¿¹° ½ÇÇè¿¡¼­ ¹æ±¤ Á¾¾ç°ú °ü·ÃÀÌ ÀÖ´Ù°í ÇÏ¿© ÇöÀç´Â À½½Ä ÷°¡¹°·Î¼­ »ç¿ëÇÏÁö ¾Ê°Ô µÇ¾ú´Ù.
  • damaluric acid
    ´Ù¸»·ç¸£ »ê
  • dehydroacetic acid
    µ¥È÷µå·Î ÃÊ»ê, µðÈ÷µå·Î¾Æ¼¼Æ®»ê
    ¿°±â¼º Ã˸ÅÀÇ Á¸Àç ÇÏ¿¡ ¾Æ¼¼Æ®»ê¿¡Æ¿ÀÇ ÃàÇÕÀ̳ª µðÄÉÅÙÀÇ ÀÌÇÕüȭ¿¡ ÀÇÇÏ¿© ÇÕ¼ºµÇ´Â È­ÇÕ¹°. ºÐÀÚ½Ä CHO. ¹é»öÀÇ Ä§»ó ¶Ç´Â ÆÇ»ó °áÁ¤À¸·Î, ³ì´ÂÁ¡ 109~111 ¡É, ²ú´ÂÁ¡ 269.9 ¡ÉÀÌ´Ù. ¹°¿¡´Â ³ìÁö ¾ÊÁö¸¸, ¿¡Å׸£¿¡´Â ³ì´Â´Ù. ½ÄǰÀÇ ¹æºÎÁ¦³ª ÇǺΠġ·áÁ¦·Î »ç¿ëµÈ´Ù.
  • deoxyribonucleic acid
    µ¥¿Á½Ã¸®º¸ ÇÙ»ê
  • dialuric acid
    ´ÙÀ̾˿ä»ê
    °áÁ¤¼­ÀÇ »ê. ¾Ë·Ï»êÀ¸·ÎºÎÅÍ ¾ò´Â´Ù.
  • diatrizoic acid
    ´ÙÀÌ¾ÆÆ®¶óÀÌÁ¶»ê
    ¹æ»ç¼± Á¶¿µÁ¦ Á¦Á¶¿¡ ¾²ÀδÙ.
  • dihydroxystearic acid
    ´ÙÀÌÇÏÀ̵å·Ï½Ã ½ºÅ׾Ƹ°»ê
    ¿Ã·¹ÀλêÀÇ »êÈ­·Î ¾òÀ¸¸ç, ÇǸ¶ÀÚÀ¯¿¡¼­ ¹ß°ßµÈ´Ù.
  • esophageal acid infusion test
    ½Äµµ»ê ÁÖÀÔ ½ÃÇè
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 7
RNA, transfer, amino acyl Intermediates in protein biosynthesis. The compounds are formed from amino acids, ATP and transfer RNA, a reaction catalyzed by aminoacyl trna synthetase. They are key compounds in the genetic translation process.
(12 Dec 1998)
c-Jun amino-terminal kinase <enzyme> A stress-activated protein kinase; 46-kD kinase that phosphorylates ser(63) and ser(73) of c-jun; similar to yeast hog1 kinase; amino acid sequence given in second source; genbank l23118
Registry number: EC 2.7.10.-
Synonym: jn kinase, jnk1 protein kinase, jnk-46, jnk1 protein, jun-nh2-terminal kinase, stress-activated protein kinase 1, sap kinase-1, sapk1, p46 sap kinase, c-jun kinase-1
(26 Jun 1999)
N-(5'-phosphoribosylformimino)-5-amino-1-(5''-phosphoribosyl)-4-imidazolecarboxamide isomerase <enzyme> Has beta/alpha-barrel fold structure; involved in biosynthesis of histidine
Registry number: EC 5.3.1.16
Synonym: hisa gene product, pfacr isomerase, phosphoribosylformimino-5-aminoimidazole carboxamide ribotide isomerase
(26 Jun 1999)
succinylalanyl-alanyl-prolyl-phenylalanyl-7-amino-4-methylcoumarin hydrolase <enzyme> Enzyme may be involved in attainment of transformed state
Registry number: EC 3.4.24.-
Synonym: suc-ala-ala-pro-phe-amc hydrolase, saapp-amc-hydrolase
(26 Jun 1999)
essential amino acids Alpha-amino acids nutritionally required by an organism and which must be supplied in its diet (i.e., cannot be synthesised by the organism) either as free amino acid or in proteins.
(05 Mar 2000)
excitatory amino acids Endogenous amino acids released by neurons as excitatory neurotransmitters. Glutamic acid is the most common excitatory neurotransmitter in the brain. Aspartic acid has been regarded as an excitatory transmitter for many years, but the extent of its role as a transmitter is unclear.
(12 Dec 1998)
2-amino-2-deoxy-D-galactose <chemical> Chemical name: D-Galactose, 2-amino-2-deoxy-
(12 Dec 1998)
2-amino-5-phosphonovalerate <chemical> A potent and specific antagonist of nmda receptors (receptors, nmda) in the d-enantiomeric form. The l form is inactive at nmda receptors but may affect the ap4 (2-amino-4-phosphonobutyrate; apb) excitatory amino acid receptors.
Pharmacological action: excitatory amino acid antagonists.
Chemical name: Norvaline, 5-phosphono-
(12 Dec 1998)
(3-(arginyl)amino-4-(4-nitrophenyl)butyryl)-leucyl-prolyl-threonine Pharmacological action: neurotransmitters
Synonym: 2-afb(p-no2)-proctolin, (afb(p-no2)(2))-proctolin
(26 Jun 1999)
8-amino-7-oxononanoate synthase <enzyme> Chemical name: 7-keto-8-aminopelargonic acid synthetase
Registry number: EC 2.3.1.47
Synonym: 7-kap synthetase, 8-amino-7-oxopelargonate synthase, 7-oxo-8-aminononanoate synthase, biof gene product
(26 Jun 1999)
Rambourg's chromic acid-phosphotungstic acid stain <technique> A stain for glycoproteins, used with an electron microscope, with which ultrathin tissue sections reveal complex carbohydrates in the same locations as shown by Rambourg's periodic acid-chromic methenamine-silver stain.
(05 Mar 2000)
a1-acid glycoprotein <biology> Plasma protein of mammals and birds, 38% carbohydrate. In humans a single chain glycoprotein of 39 kD. Increased levels are associated with inflammation, pregnancy and various diseases.
(18 Nov 1997)
abscisic acid <biochemistry> A lipid hormone that inhibits cell growth in plants, it is associated with fruit drop, leaf death and seed dormancy. It is synthesised in the plastids from carotenoids. This hormone helps plants deal with water loss, and its effects can be reversed with gibberellins.
(06 May 1997)
abscisic acid 8'-hydroxylase <enzyme> Catalyses conversion of abscisic acid to 8'-hydroxyabscisic acid, which rearranges to phaseic acid
Registry number: EC 1.14.99.-
Synonym: aba 8'-hydroxylase
(26 Jun 1999)
acetic acid <chemical> The acid most commonly associated with vinegar, it is the most commercially important organic acid and is used to manufacture a wide range of chemical products, such as plastics and Acetobacter but, except for making vinegar, is usually made through synthetic processes.
Derivatives of acetic acid which may be formed by substitution reactions. Mono- and di-substituted, as well as, halogenated compounds have been synthesised.
Experimentally, alpha- and n2- substituted acetic acids have been examined for their anti-inflammatory activity and effect on the central nervous system respectively. Additionally, limited exposure data has been collected on dibromo and dichloroacetic acids to determine whether they pose health effects.
Synonym: ethanoic acid.
(26 Jun 1999)
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