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CoA Coarctation of the Aorta
FAO Fatty acyl CoA oxidase
HMGR HMG CoA reductase
IVD Isovaleryl-CoA dehydrogenase
LCHAD Long chain 3-hydroxyacyl-CoA-dehydrogenase
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clofibroyl-CoA hydrolase <enzyme> Rat liver cytosolic enzyme is not the same as palmitoyl CoA hydrolase (EC 3.1.2.2)
Registry number: EC 3.1.2.-
Synonym: clofibroyl-coenzyme a hydrolase
(26 Jun 1999)
CoA <abbreviation> Coenzyme A.
(05 Mar 2000)
CoA transferases Thiaphorases;enzymes transferring CoA from acetyl-CoA or succinyl-CoA to other acyl radicals.
(05 Mar 2000)
phytanoyl-CoA ligase <enzyme> An acyl-CoA ligase found in peroxisomes of fibroblasts; it is distinct from palmitoyl-CoA ligase and lignoceroyl-CoA ligase
Registry number: EC 6.2.1.-
Synonym: phytanoyl-coenzyme a ligase
(26 Jun 1999)
cyclohexylideneacetyl-CoA hydratase <enzyme> From arthrobacter; forms (1-hydroxycyclohexan-1-yl)acetyl-CoA
Registry number: EC 4.2.1.-
Synonym: ca-CoA-hydratase, cyclohexylideneacetyl-coenzyme a hydratase
(26 Jun 1999)
pristanoyl-CoA oxidase <enzyme> Pristanoic acid undergoes beta-oxidation giving alternatively rise to acetyl-CoA or propionyl-CoA and h2o2
Registry number: EC 1.3.3.-
Synonym: 2,6,10,14-tetramethylpentadecanoyl-CoA oxidase, 2-methylpalmitoyl-CoA oxidase, pristanyl-CoA oxidase
(26 Jun 1999)
propionyl-CoA The coenzyme A thioester derivative of propionic acid; an intermediate in the degradation of l-valine, l-isoleucine, l-threonine, l-methionine, and odd-chain fatty acids; a precursor for the synthesis of odd-chain fatty acids; it accumulates in individuals with a deficiency of propionyl-CoA carboxylase.
Propionyl-CoA carboxylase, an enzyme that catalyses the reaction of propionyl-CoA with CO2 and ATP to produce ADP, inorganic phosphate, and d-methylmalonyl-CoA; a biotin-dependent enzyme; an inherited deficiency of this enzyme will lead to propionic acidemia and developmental retardation.
(05 Mar 2000)
propionyl-CoA carboxylase <enzyme> See also propionyl CoA carboxylase (ATP-hydrolyzing) (EC 6.4.1.4)
Registry number: EC 4.1.1.41
Synonym: methylmalonyl-CoA decarboxylase, propionyl-coenzyme a carboxylase
(26 Jun 1999)
propionyl CoA hydrolase <enzyme> Nadh sensitive; found in brown adipose tissue mitochondria of rat; prevents a deterimental increase of propionyl-CoA in mitochondria; mw at least 240 kD
Registry number: EC 3.1.2.-
Synonym: propionyl coenzyme a hydrolase
(26 Jun 1999)
HMG-CoA <abbreviation> Beta-hydroxy-beta-methylglutaryl-CoA.
(05 Mar 2000)
HMG CoA reductase inhibitor Drugs, such as lovastatin and pravastatin, which interfere with the biosynthesis of cholesterol; used to treat hyperlipidemia.
(05 Mar 2000)
HMG-CoA reductase phosphatase <enzyme> Similar to phosphoprotein phosphatase, EC 3.1.3.16
Registry number: EC 3.1.3.-
Synonym: 3-hydroxy-3-methylglutaryl coenzyme a reductase phosphatase
(26 Jun 1999)
hydroxycinnamoyl-CoA-tyramine N-(hydroxycinnamoyl)transferase <enzyme> Catalyses synthesis of n-(hydroxycinnamoyl)tyramine; isolated from nicotiana tabacum
Registry number: EC 2.3.1.-
Synonym: tht enzyme
(26 Jun 1999)
short-chain acyl-CoA dehydrogenase See: acyl-CoA dehydrogenase (NADPH+).
(05 Mar 2000)
short-chain beta-hydroxyacyl-CoA dehydrase <enzyme> Forms trans-2-enoyl-CoA; maximal activity with trans-2-hexenoyl-CoA, followed by crotonyl-CoA; not the same as EC 4.2.1.17
Registry number: EC 4.2.1.-
Synonym: beta-hydroxybutyryl-CoA dehydrase, short-chain beta-hydroxyacyl-coenzyme a dehydrase
(26 Jun 1999)
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