| malonyl-CoA-isoflavone-7-O-glucoside-6''-O-malonyltransferase | <enzyme> From chick pea roots; specificity for isoflavones formononetin and biochanin a Registry number: EC 2.3.1.- Synonym: mcoa-if7g malonyltransferase, malonyl-coenzyme a-isoflavone-7-o-glucoside-6''-o-malonyltransferase (26 Jun 1999) |
|---|---|
| glutaconyl CoA decarboxylase | <enzyme> Forms crotonyl CoA Registry number: EC 4.1.1.- Synonym: glutaconyl coenzyme a decarboxylase (26 Jun 1999) |
| glutaryl-CoA | The mono thiol ester of coenzyme A and glutaric acid; an intermediate in l-lysine and l-tryptophan catabolism. Glutaryl-CoA dehydrogenase, an enzyme that catalyses the reaction of glutaryl-CoA with an acceptor to form crotonoyl-CoA, CO2, and the reduced acceptor; a deficiency of this enzyme will lead to either glutaric acidemia type I or hyperoxaluria type II. Glutaryl-CoA synthetase, an enzyme similar to acyl-CoA synthetase, but which splits ATP, GTP, or ITP to the nucleoside diphosphate and orthophosphate in acting on glutarate, thus forming glutaryl-Coa. (05 Mar 2000) |
| glutaryl-CoA dehydrogenase | <enzyme> Glutaric aciduria may be due to deficiency of this enzyme Registry number: EC 1.3.99.7 Synonym: glutaryl CoA dehydrogenase, glutaryl-coenzyme a dehydrogenase (26 Jun 1999) |
| medium-chain acyl-CoA dehydrogenase | <enzyme> Deficiency in mitochondrial beta oxidation of fatty acids gives a disorder frequently masquerading as reye syndrome or sudden infant death; leads to buildup of octanoyl carnitine in urine Registry number: EC 1.3.- Synonym: mcaca-dehydrogenase, medium-chain acyl-coenzyme a dehydrogenase, octanoyl-CoA dehydrogenase, mcad enzyme (26 Jun 1999) |
| methylglutaconyl-CoA hydratase | <enzyme> Catalyses conversion of 3-hydroxy-3-methylglutaryl-CoA to trans-3-methylglutaconyl-CoA and water Registry number: EC 4.2.1.18 Synonym: 3-hydroxy-3-methylglutaryl-CoA hydro-lyase, 3-methylglutaconyl-coenzyme a hydratase, 3-methylglutaconyl-CoA hydratase (26 Jun 1999) |
| methylmalonyl-CoA | An intermediate in the degradation of several metabolites (e.g., valine, methionine, odd-chain fatty acids, theronine); elevated in cases of pernicious anaemia. (05 Mar 2000) |
| methylmalonyl-CoA epimerase | <enzyme> An enzyme that catalyses the interconversion of d-methylmalonyl-CoA and l-methylmalonyl-CoA. (05 Mar 2000) |
| methylmalonyl-CoA mutase | <enzyme> An enzyme that catalyses the conversion of methylmalonyl-CoA to succinyl-CoA by transfer of the carbonyl group. It requires a cobamide coenzyme. A block in this enzymatic conversion leads to the metabolic disease, methylmalonic aciduria. Chemical name: (R)-2-Methyl-3-oxopropanoyl-CoA CoA-carbonylmutase Registry number: EC 5.4.99.2 (12 Dec 1998) |
| phenylacetate - CoA ligase | <enzyme> Catalyses the synthesis of phenylacetyl-CoA and phenoxyacetyl-CoA Registry number: EC 6.2.1.30 Synonym: phenylacetyl-CoA ligase, phenylacetic acid activating enzyme, phenoxyacetic acid activating enzyme, phenacyl coenzyme a ligase, phenylacetate-CoA ligase (AMP-forming) (26 Jun 1999) |
| clofibroyl-CoA hydrolase | <enzyme> Rat liver cytosolic enzyme is not the same as palmitoyl CoA hydrolase (EC 3.1.2.2) Registry number: EC 3.1.2.- Synonym: clofibroyl-coenzyme a hydrolase (26 Jun 1999) |
| CoA | <abbreviation> Coenzyme A. (05 Mar 2000) |
| phytanoyl-CoA ligase | <enzyme> An acyl-CoA ligase found in peroxisomes of fibroblasts; it is distinct from palmitoyl-CoA ligase and lignoceroyl-CoA ligase Registry number: EC 6.2.1.- Synonym: phytanoyl-coenzyme a ligase (26 Jun 1999) |
| cyclohexylideneacetyl-CoA hydratase | <enzyme> From arthrobacter; forms (1-hydroxycyclohexan-1-yl)acetyl-CoA Registry number: EC 4.2.1.- Synonym: ca-CoA-hydratase, cyclohexylideneacetyl-coenzyme a hydratase (26 Jun 1999) |
| pristanoyl-CoA oxidase | <enzyme> Pristanoic acid undergoes beta-oxidation giving alternatively rise to acetyl-CoA or propionyl-CoA and h2o2 Registry number: EC 1.3.3.- Synonym: 2,6,10,14-tetramethylpentadecanoyl-CoA oxidase, 2-methylpalmitoyl-CoA oxidase, pristanyl-CoA oxidase (26 Jun 1999) |