| galactosyl transferase | <enzyme> Enzyme catalysing the transfer of galactose units from the sugar nucleotide, uridine diphospho galactose UDP galactose) to an acceptor, commonly N acetyl glucosamine in a glycan chain, forming a glycosidic bond involving C1 of galactose. (18 Nov 1997) |
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| galactosyl(alpha 1-4)galactosylceramide galactosyl hydrolase | <enzyme> Active in pH 3.0 component of human plasma (pn-a-2); greatly decreased in fabry's disease Registry number: EC 3.2.1.- Synonym: digalactosylceramidase (26 Jun 1999) |
| galactosyl-1-3-N-acetylgalactosaminyl-specific 2,6-sialyltransferase | <enzyme> Genbank x77775 Registry number: EC 2.4.99.- Synonym: galbeta1,3galnac 2,6-sialyltransferase, st6galnac II (26 Jun 1999) |
| galactosylceramidase | <enzyme> An enzyme that hydrolyzes galactose from ceramide monohexosides. Chemical name: D-Galactosyl-N-acylsphingosine galactohydrolase Registry number: EC 3.2.1.46 (12 Dec 1998) |
| galactosylceramide | A sphingolipid that accumulates in individuals with Krabbe's disease. (05 Mar 2000) |
| galactosylceramide lipoidosis | <radiology> Dysmyelinating disease, autosomal recessive, usually presents by 1 yr, specific enzyme deficiency identified, rapid spontaneous nystagmus, poikilothermia Synonym: Krabbe leukodystrophy (12 Dec 1998) |
| galactosylceramide sulfotransferase | <enzyme> Models for the study of inborn errors of metabolism Registry number: EC 2.8.2.11 Synonym: cerebroside sulfotransferase, galactocerebroside sulfotransferase, glycosphingolipid sulfotransferase, galcst, glycolipid sulfotransferase, galcer-st, galactosylceramide sulphotransferase (26 Jun 1999) |
| galactosylceramides | Cerebrosides which contain as their polar head group a galactose moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in beta-galactosidase, is the cause of galactosylceramide lipidosis or globoid cell leukodystrophy. (12 Dec 1998) |
| galactosyltransferases | <enzyme> Enzymes that catalyze the transfer of galactose from a nucleoside diphosphate galactose to an acceptor molecule which is frequently another carbohydrate. Registry number: EC 2.4.1.- (12 Dec 1998) |
| galactosylxylosylprotein 3-beta-galactosyltransferase | <enzyme> Catalyses the reaction of udpgalactose and 4-beta-d-(galactosyl-o-beta-d-xylosylprotein to yield udp and 3-beta-d-galactosyl-o-beta-d-xylosylprotein Registry number: EC 2.4.1.134 Synonym: galactosyltransferase II, (26 Jun 1999) |
| galactotherapy | Treatment of disease by means of an exclusive or nearly exclusive milk diet. Synonym: lactotherapy. (05 Mar 2000) |