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galactosyl transferase <enzyme> Enzyme catalysing the transfer of galactose units from the sugar nucleotide, uridine diphospho galactose UDP galactose) to an acceptor, commonly N acetyl glucosamine in a glycan chain, forming a glycosidic bond involving C1 of galactose.
(18 Nov 1997)
galactosyl(alpha 1-4)galactosylceramide galactosyl hydrolase <enzyme> Active in pH 3.0 component of human plasma (pn-a-2); greatly decreased in fabry's disease
Registry number: EC 3.2.1.-
Synonym: digalactosylceramidase
(26 Jun 1999)
galactosyl-1-3-N-acetylgalactosaminyl-specific 2,6-sialyltransferase <enzyme> Genbank x77775
Registry number: EC 2.4.99.-
Synonym: galbeta1,3galnac 2,6-sialyltransferase, st6galnac II
(26 Jun 1999)
galactosylceramidase <enzyme> An enzyme that hydrolyzes galactose from ceramide monohexosides.
Chemical name: D-Galactosyl-N-acylsphingosine galactohydrolase
Registry number: EC 3.2.1.46
(12 Dec 1998)
galactosylceramide A sphingolipid that accumulates in individuals with Krabbe's disease.
(05 Mar 2000)
galactosylceramide lipoidosis <radiology> Dysmyelinating disease, autosomal recessive, usually presents by 1 yr, specific enzyme deficiency identified, rapid spontaneous nystagmus, poikilothermia
Synonym: Krabbe leukodystrophy
(12 Dec 1998)
galactosylceramide sulfotransferase <enzyme> Models for the study of inborn errors of metabolism
Registry number: EC 2.8.2.11
Synonym: cerebroside sulfotransferase, galactocerebroside sulfotransferase, glycosphingolipid sulfotransferase, galcst, glycolipid sulfotransferase, galcer-st, galactosylceramide sulphotransferase
(26 Jun 1999)
galactosylceramides Cerebrosides which contain as their polar head group a galactose moiety bound in glycosidic linkage to the hydroxyl group of ceramide. Their accumulation in tissue, due to a defect in beta-galactosidase, is the cause of galactosylceramide lipidosis or globoid cell leukodystrophy.
(12 Dec 1998)
galactosyltransferases <enzyme> Enzymes that catalyze the transfer of galactose from a nucleoside diphosphate galactose to an acceptor molecule which is frequently another carbohydrate.
Registry number: EC 2.4.1.-
(12 Dec 1998)
galactosylxylosylprotein 3-beta-galactosyltransferase <enzyme> Catalyses the reaction of udpgalactose and 4-beta-d-(galactosyl-o-beta-d-xylosylprotein to yield udp and 3-beta-d-galactosyl-o-beta-d-xylosylprotein
Registry number: EC 2.4.1.134
Synonym: galactosyltransferase II,
(26 Jun 1999)
galactotherapy Treatment of disease by means of an exclusive or nearly exclusive milk diet.
Synonym: lactotherapy.
(05 Mar 2000)
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galactosemia a rare hereditary disease leading not only to cirrhosis in infants, but more seriously, to early devastating illness if not diagnosed quickly.
Ãâó: www.theliverfoundationforkids.org/glossary.html
galactogogue Increase the secretion of mother's milk. Examples are: Aniseed, blessed thistle, borage, fennel, fenugreek and raspberry.
Ãâó: www.earthspirits-herbals.com/fyi/spring04.htm
galactolipin A phosphorus-free lipid combined with galactose; a cerebroside.
Ãâó:
galactoma Galactocele (1).
Ãâó:
galactopexy The fixation of galactose by the liver.
Ãâó:
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