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HHE health hazard evaluation; hemiconvulsion-hemiplegia-epilepsy [syndrome]
IBE International Bureau for Epilepsy
JME juvenile myoclonus epilepsy
MERRF myoclonus epilepsy with ragged red fibers [syndrome]
MERRLA myoclonus epilepsy-ragged red fibers-lactic acidosis [syndrome]
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PME Progressive myoclonic epilepsy
SMEI Severe myoclonic epilepsy in infancy
SUDEP Sudden unexpected death in epilepsy
TLE Temporal Lobe Epilepsy
FLE frontal lobe epilepsy
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reflex epilepsy Seizures which are induced by peripheral stimulation; e.g., audiogenic, laryngeal, photogenic, or other stimulation.
Synonym: sensory precipitated epilepsy.
(05 Mar 2000)
partial epilepsy Epilepsy of various aetiologies characterised by focal seizures or secondarily generalised tonic-clonic seizures. Ictal symptoms are often related to the brain region where the seizure begins focally.
Synonym: cortical epilepsy, local epilepsy, partial epilepsy.
(05 Mar 2000)
visceral epilepsy Epilepsy, usually psychomotor, in which the attacks are initiated by visceral symptoms or sensations; most cases have their focus in the temporal lobe.
(05 Mar 2000)
pattern sensitive epilepsy A form of reflex epilepsy precipitated by viewing certain patterns.
(05 Mar 2000)
centrencephalic epilepsy An imprecise term referring to epilepsy characterised electroencephalographically by bilateral synchronous discharges, and clinically by absence or generalised tonic-clonic seizures.
(05 Mar 2000)
grand mal epilepsy Older term for epilepsy characterised by generalised tonic-clonic seizure.
(05 Mar 2000)
childhood absence epilepsy A generalised epilepsy syndrome characterised by the onset of absence seizures in childhood, typically at age six or seven years. There is a strong genetic predisposition and girls are affected more often than boys. EEG reveals generalised 3 Hz spike-wave activity on a normal background. Prognosis for remission is good if the patient does not also have generalised tonic-clonic seizures.
See: absence.
Synonym: petit mal epilepsy, pyknolepsy.
(05 Mar 2000)
childhood epilepsy with occipital paroxysms A benign epilepsy syndrome characterised by frequent occipital spikes often activated by eye closure. It has a seizure semiology that includes visual manifestations; not always remitting later in life.
(05 Mar 2000)
petit mal epilepsy A generalised epilepsy syndrome characterised by the onset of absence seizures in childhood, typically at age six or seven years. There is a strong genetic predisposition and girls are affected more often than boys. EEG reveals generalised 3 Hz spike-wave activity on a normal background. Prognosis for remission is good if the patient does not also have generalised tonic-clonic seizures.
See: absence.
Synonym: petit mal epilepsy, pyknolepsy.
(05 Mar 2000)
rolandic epilepsy A benign, autosomal, dominant form of epilepsy occurring in children, characterised clinically by arrest of speech, by muscular contractions of the side of the face and arm and epileptic discharges electroencephalographically.
Origin: Luigi Rolando
(05 Mar 2000)
pharmacoresistent epilepsy Epilepsy not adequately controlled by medication.
Synonym: pharmacoresistent epilepsy.
(05 Mar 2000)
photogenic epilepsy A form of reflex epilepsy precipitated by light.
(05 Mar 2000)
complex precipitated epilepsy A form of reflex epilepsy initiated by specialised sensory stimuli, e.g., certain visual patterns.
(05 Mar 2000)
cortical epilepsy Epilepsy of various aetiologies characterised by focal seizures or secondarily generalised tonic-clonic seizures. Ictal symptoms are often related to the brain region where the seizure begins focally.
Synonym: cortical epilepsy, local epilepsy, partial epilepsy.
(05 Mar 2000)
myoclonic astatic epilepsy A petit mal variant characterised by atonic (drop attacks) and tonic or tonic-clonic attacks in neurologically disabled (hemiplegic, ataxic, etc.) children with mental retardation; characterised in EEG by 2/sec spike and wave discharges; usually progresses in spite of medication.
(05 Mar 2000)
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