| 영문 | respiratory distress syndrome(RDS) | 한글 | 호흡곤란증후군 |
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| 설명 | 폐포와 폐모세혈관 사이에 부종으로 인한 확산능 감소로 호흡곤란과 청색증을 보이는 상태로 감염, 수술, 외상 등 모든 종류의 스트레스상황에서 발생할 수 있다. 치료는 선행 요인의 교정과 적절한 혈액내 산소농도 유지이다. |
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| 영문 | acquired immunodeficiency syndrome | 한글 | 후천면역결핍증후군, 에이즈 |
|---|---|---|---|
| 설명 | 인간면역결핍바이러스(HIV)에 의하여 면역 세포가 파괴됨으로써 인체의 면역능력이 극도로 저하되어 병원체에 대하여 무방비 상태에 이르는 병. 에이즈 바이러스의 감염으로 생기며, 1981년 미국에서 처음 보고되었다. 최초 감염으로부터 증상이 나타나기까지는 평균 10년 정도 걸리며 사망률이 대단히 높다. 성적 접촉, 오염 주사기 사용, 오염 혈액 및 혈액 제제 사용, 에이즈 산모로부터 수직감염 따위에 의하여 감염된다. 감염 후 일과성으로 감기와 같은 증상을 보이며 바이러스혈증으로 되지만 바이러스는 감소되고 6~8주 후에는 항체가 양성으로 된다. 6~10년 정도의 무증후성 보균기간을 지나서 에이즈관련증후군(AIDS related syndrome)으로 된다. 저항력의 감소, 림프절비대, 체중감소, 발열, 만성설사가 이어진다. 그 후 에이즈로 되며, 폐포자충폐렴 등의 원충병, 칸디다 등의 진균증, 헤르페스바이러스군 등의 기회감염이 이어진다. 또한 카포시육종, 림프종 등을 병발해서 사망한다. 바이러스의 뇌조직내 증식으로 치매를 일으킬 수도 있다. HIV-1은 10년간에 사망률이 90%, HIV-2는 10%이다. |
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| RS | radioscaphoid; random sample; rating schedule; Raynaud syndrome; recipient's serum; rectal sinus; re... |
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| MD | Doctor of Medicine [Lat. Medicinae Doctor]; magnesium deficiency; main duct; maintenance dose; major... |
| ASLN | Alport syndrome-like hereditary nephritis |
| HHHH | hereditary hemihypotrophy-hemiparesis-hemiathetosis [syndrome] |
| HOODS | hereditary onycho-osteodysplasia syndrome |
| colourectal neoplasms, hereditary nonpolyposis | A syndrome characterised by autosomal dominant inheritance, a low mean age (41 years) for occurrence of colon cancer, and a marked increase in the proportion of tumours in the proximal colon. (12 Dec 1998) |
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| corneal dystrophies, hereditary | Bilateral hereditary disorders of the cornea, usually autosomal dominant, which may be present at birth but more frequently develop during adolescence and progress slowly throughout life. Central macular dystrophy is transmitted as an autosomal recessive defect. (12 Dec 1998) |
| hereditary | <genetics> Transferred via genes from parent to child. (16 Dec 1997) |
| hereditary amyloidosis | <neurology> A disorder in which various peripheral nerves are infiltrated with amyloid and their functions disturbed, an abnormal prealbumin is also formed and is present in the blood; characteristically, it begins during mid-life and is found largely in persons of Portuguese descent. Other rare clinical types occur. Inheritance: autosomal dominant. Synonym: familial amyloidosis, hereditary amyloidosis. (05 Mar 2000) |
| hereditary angioedema | A genetic form of angioedema. (angioedema is also referred to as quinke's disease.) persons with it are born lacking an inhibitor protein (called c1 esterase inhibitor) that normally prevents activation of a cascade of proteins leading to the swelling of angioedema. Patients can develop recurrent attacks of swollen tissues, pain in the abdomen, and swelling of the voice box (larynx) which can compromise breathing. The diagnosis is suspected with a history of recurrent angioedema. It is confirmed by finding abnormally low levels of c1 esterase inhibitor in the blood. Treatment options include antihistamines and male steroids (androgens) that can also prevent the recurrent attacks. Also called hereditary angioneurotic oedema. (12 Dec 1998) |
| hereditary angioneurotic oedema | A genetic form of angioedema. (angioedema is also referred to as quinke's disease.) persons with it are born lacking an inhibitor protein (called c1 esterase inhibitor) that normally prevents activation of a cascade of proteins leading to the swelling of angioedema. Patients can develop recurrent attacks of swollen tissues, pain in the abdomen, and swelling of the voice box (larynx) which can compromise breathing. The diagnosis is suspected with a history of recurrent angioedema. It is confirmed by finding abnormally low levels of c1 esterase inhibitor in the blood. Treatment options include antihistamines and male steroids (androgens) that can also prevent the recurrent attacks. Also called hereditary angioedema. (12 Dec 1998) |
| hereditary angio oedema | <biochemistry> Condition in which there seems to be uncontrolled production of C2 kinin because of a deficiency in C1 inhibitor levels. (18 Nov 1997) |
| hereditary areflexic dystasia | A rare autosomal dominant neurological disorder with many of the clinical features of hereditary hypertrophic sensorimotor polyneuropathy combined with an essential tremor. Synonym: hereditary areflexic dystasia. (05 Mar 2000) |
| hereditary ataxia | A simple autosomal recessive trait in fox terrier dogs that produces a progressive general ataxia. (05 Mar 2000) |
| hereditary benign intraepithelial dyskeratosis | An autosomal dominant condition consisting of white spongy lesions of the buccal mucosa, floor of the mouth, ventral lateral tongue, gingiva and palate. Transient gelatinous plaques form over the cornea, which may produce temporary blindness, hereditary benign intraepithelial dyskeratosis. Synonym: hereditary benign intraepithelial dyskeratosis. (05 Mar 2000) |
| hereditary cerebellar ataxia | A disease of later childhood and early adult life, marked by ataxic gait, hesitating and explosive speech, nystagmus, and sometimes optic neuritis. It probably comprises several distinct conditions with diverse patterns of inheritance. Collective term for a number of hereditary disorders in which cerebellar signs are the most prominent finding. (05 Mar 2000) |
| hereditary chorea | A progressive disorder usually beginning in young to middle age, consisting of a triad of choreoathetosis, dementia, and autosomal dominant inheritance with complete penetrance. Bilateral marked wasting of the putamen and the head of the caudate nucleus is characteristic. Synonym: chronic progressive chorea, degenerative chorea, hereditary chorea, Huntington's disease. (05 Mar 2000) |
| hereditary coproporphyria | <haematology> A group of metabolic disorders that result from a disturbance in porphyrin metabolism, causing increased formation and excretion of porphyrin or its precursors. Acute intermittent porphyria is a rare inherited form that can result in abdominal pain, photosensitivity and neurological disturbances. The various forms can be differentiated measuring various blood prophyrins. Inheritance: autosomal dominant. (27 Sep 1997) |
| hereditary deafness and nephropathy | <nephrology, pathology> An inherited disorder involving damage to the kidneys, haematuria and hearing loss. In some individuals vision may also be affected. This genetic disease is uncommon. Symptoms include loss of hearing, abnormal colour to urine, swelling, cough and decline in vision. Inheritance: sex-linked autosomal dominant. Incidence: 1 in 50,000. Origin: Gr. Pathos = disease (27 Sep 1997) |
| hereditary deforming chondrodystrophy | A disturbance of enchondral bone growth in which multiple, generally benign osteochondromas of long bones appear during childhood, commonly with shortening of the radius and fibula; the ill-effects are usually mechanical but malignant change is rare; autosomal dominant inheritance. Synonym: diaphysial aclasis, hereditary deforming chondrodystrophy, multiple exostosis, osteochondromatosis. (05 Mar 2000) |