| 3-hydroxybutyrate dehydrogenase |
[EC 1.1.1.30] an enzyme of the oxidoreductase class that catalyzes the oxidation of D-3-hydroxybutyrate to form acetoacetate, using NAD+ as an electron acceptor. The enzyme functions in nervous tissues and muscles, enabling use of circulating hydroxybutyrate as a fuel. In the liver mitochondrial matrix, the enzyme can also catalyze the reverse reaction, a step in ketogenesis. Written also β-hydroxybutyrate dehydrogenase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
|---|---|
| 3-hydroxybutyryl-CoA epimerase |
[EC 5.1.2.3] an enzyme of the isomerase class that catalyzes the epimerization around C-3 of a D-3-hydroxyacyl coenzyme A to form the L isomer, a substrate for beta oxidation. The reaction is necessary for metabolism of some unsaturated fatty acids. Called also 3-hydroxyacyl-CoA epimerase.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| 3-hydroxyisobutyryl |
the acyl radical of an isomer of 3-hydroxybutyric acid; the thioester formed with coenzyme A, 3-hydroxyisobutyryl CoA, is an intermediate in the catabolism of valine.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| 3-hydroxyisobutyryl-CoA hydrolase |
[EC 3.1.2.4] an enzyme of the hydrolase class that catalyzes the cleavage of the coenzyme A (CoA) moiety from 3-hydroxyisobutyryl CoA as a step in the use of valine as a fuel. Deficiency results in toxic tissue accumulation of the CoA thioester of methacrylic acid and its cysteine compound conjugates.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|
| 3-hydroxyisovaleric acid |
a methylated form of isovaleric acid accumulating abnormally and excreted in the urine in several disorders of leucine catabolism.
출처: www.mercksource.com/pp/us/cns/cns_health_library.j...
|