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DLD dihydrolipoamide dehydrogenase
FDH familial dysalbuminemic hyperthyroxinemia; focal dermal hypoplasia; formaldehyde dehydrogenase
GADH gastric alcohol dehydrogenase
GAPD glyceraldehyde-3-phosphate dehydrogenase
GAPDH glyceraldehyde-3-phosphate dehydrogenase
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IPMDH 3-Isopropylmalate dehydrogenase
ADH 3-alcohol dehydrogenase
HADH 3-hydroxy-acyl-Co-A dehydrogenase
HBD 3-hydroxybutyrate dehydrogenase
HSD 3beta-hydroxysteroid dehydrogenase
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glyceraldehydephosphate dehydrogenase <enzyme> Chemical name: D-Glyceraldehyde-3-phosphate:NADP+ oxidoreductase
Registry number: EC 1.2.1.9
(12 Dec 1998)
glycerol-1-phosphate dehydrogenase <enzyme> From the archaebacterium methanobacterium thermoautotrophicum; forms the glycerophosphate which is the mirror image of that found in eubacterial and eukaryotic ether phospholipids
Registry number: EC 1.1.1.-
Synonym: sn-glycerol-1-phosphate - nad+ oxidoreductase, sn-g-1-p dehydrogenase
(26 Jun 1999)
glycerol-3-phosphate dehydrogenase Alpha-Glycerol phosphate dehydrogenase; 3-phosphoglycerol dehydrogenase;an oxidoreductase that catalyses the interconversion of dihydroxyacetone phosphate and sn-glycerol 3-phosphate, with the participation of NAD+; its action provides the glycerol moiety from carbohydrate during lipogenesis.
(05 Mar 2000)
glycerolphosphate dehydrogenase <enzyme> Registry number: EC 1.1.-
(12 Dec 1998)
glycine dehydrogenase Enzymes that catalyze the conversion of glycine to glyoxylate and ammonia, using either NAD+ or ferricytochrome c.
(05 Mar 2000)
glycolic acid dehydrogenase <enzyme> Enzyme from human liver converts glycolate to oxalate, acceptor not identified, not oxygen; free glyoxylate is not an intermediate
Registry number: EC 1.1.-
(26 Jun 1999)
retinaldehyde dehydrogenase An oxidoreductase catalyzing the interconversion of retinaldehyde and NAD+ to retinoic acid and NADH; thus affecting growth and differentiation.
Synonym: retinaldehyde dehydrogenase.
(05 Mar 2000)
retinal dehydrogenase An oxidoreductase catalyzing the interconversion of retinaldehyde and NAD+ to retinoic acid and NADH; thus affecting growth and differentiation.
Synonym: retinaldehyde dehydrogenase.
(05 Mar 2000)
retinol dehydrogenase <enzyme> 9-cis-retinol dehydrogenase is also available
Registry number: EC 1.1.1.105
Synonym: 11-cis retinol dehydrogenase, p32 retinol dehydrogenase
(26 Jun 1999)
meso-tartrate dehydrogenase <enzyme> Forms dihydroxyfumarate; distinguished from EC 1.1.1.93 which forms oxaloglycollate
Registry number: EC 1.3.1.7
(26 Jun 1999)
chloridazondihydrodiol dehydrogenase <enzyme> Converts chloridazondihydrodiol to a catechol
Registry number: EC 1.3.1.-
(26 Jun 1999)
chlorobenzene dehydrogenase <enzyme> Converts product of chlorobenzene dioxygenase to chlorocatechol
Registry number: EC 1.3.-
Synonym: chlorobenzene dihydrodiol dehydrogenase
(26 Jun 1999)
guaiacylglycerol beta-O-4-guaiacyl ether dehydrogenase <enzyme> Nad+ required; forms the corresponding ketone at the alpha carbon of the glycerol side chain
Registry number: EC 1.1.1.-
Synonym: gge dehydrogenase
(26 Jun 1999)
cholesterol dehydrogenase <enzyme> Converts cholesterol to coprostanol; mechanism given is incorrect for enzyme name
Registry number: EC 1.3.-
(26 Jun 1999)
Robison ester dehydrogenase <enzyme> An NADP+ enzyme that catalyses the dehydrogenation (oxidation) of d-glucose-6-phosphate to 6-phospho-d-glucono-d-lactone, this reaction initiating the Dickens shunt.
Deficiency of this enzyme is the commonest disease-causing enzyme defect in humans affecting an estimated 400 million people.
The gene for this enzyme is on the X chromosome. Males with the enzyme deficiency develop haemolytic anaemia when red blood cells are exposed to oxidant drugs such as the antimalarial primaquine, the sulfonamide antibiotics or sulfones, naphthalene moth balls, or fava beans.
Synonym: Robison ester dehydrogenase, Zwischenferment.
Acronym: G6PD
(12 Sep 2002)
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