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vWf Von Willebrand factor antigen
vW von Willebrand
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von Spee's curve The anatomic curvature of the mandibular occlusal plane beginning at the tip of the lower cuspid and following the buccal cusps of the posterior teeth, continuing to the terminal molar.
Synonym: von Spee's curve.
(05 Mar 2000)
Von Willebrand disease <disease, haematology> A hereditary platelet disorder caused by defective or deficient Von Willebrand factor, a protein involved in normal blood clotting, that reduces adhesion to collagen but not aggregation. Both bleeding time and coagulation are increased. Factor VIII levels are secondarily reduced.
Symptoms include nosebleeds, bleeding gums, heavy menstrual bleeding, bruising and skin rashes.
Inheritance: autosomal dominant.
(30 Sep 1997)
von Willebrand, E <person> Finnish physician, 1870-1949.
See: von Willebrand's disease.
(05 Mar 2000)
Von Willebrand factor Plasma factor involved in platelet adhesion through an interaction with Factor VIII.
See: Von Willebrand disease.
(18 Nov 1997)
von Willebrand factor-degrading protease <enzyme> A large protease from normal human plasma that degrades vwf at the 842tyr-843met peptide bond
Registry number: EC 3.4.24.-
Synonym: vwf-cleaving protease
(26 Jun 1999)
Von Willebrand's disease <disease> This congenital disease, which is caused a deficiency of a blood factor that promotes platelet adhesion, is characterised by prolonged bleeding and poor blood coagulation.
(09 Oct 1997)
Reuss, August von <person> Austrian ophthalmologist, 1841-1924.
See: Reuss' formula, Reuss' colour tables, Reuss' test.
(05 Mar 2000)
Graefe, Albrecht von <person> German ophthalmologist, 1828-1870.
See: Graefe forceps, Graefe's knife, Graefe's operation, Graefe's sign, Graefe's spots, pseudo-Graefe's phenomenon, Graefe's sign, von Graefe's sign.
(05 Mar 2000)
Gruber, Max von <person> German hygienist, 1853-1927.
See: Gruber's reaction, Gruber-Widal reaction.
(05 Mar 2000)
Ritgen, Ferdinand August Marie Franz von <person> German obstetrician, 1787-1867.
See: Ritgen's manoeuvre.
(05 Mar 2000)
Gudden, Bernhard von <person> German neurologist, 1824-1886.
See: Gudden's commissures, Gudden's ganglion, Gudden's tegmental nuclei.
(05 Mar 2000)
Pfaundler, Meinhard von <person> German physician, 1872-1947.
See: Pfaundler-Hurler syndrome.
(05 Mar 2000)
Rokitansky, Karl Freiherr von <person> Austrian pathologist, 1804-1878.
See: Rokitansky's disease, Rokitansky's hernia, Rokitansky-Aschoff sinuses, Mayer-Rokitansky-Kuster-Hauser syndrome.
(05 Mar 2000)
Meyenburg, H Von <person> Swiss pathologist, *1877.
See: Meyenburg's complex, Meyenburg's disease, Meyenburg-Altherr-Uehlinger syndrome, von Meyenburg's disease.
(05 Mar 2000)
Rothmund, August von <person> German physician, 1830-1906.
See: Rothmund's syndrome, Rothmund-Thomson syndrome.
(05 Mar 2000)
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