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"multiple acyl CoA dehydrogenation deficiency"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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  • ¿µ¹®
    ÇѱÛ
  • multiple myositis
    ´Ù¹ß±Ù(À°)¿°
  • multiple neurofibromatosis
    ´Ù¹ß½Å°æ¼¶À¯Á¾Áõ
  • multiple neuroma
    ´Ù¹ß½Å°æÁ¾
  • multiple paramyoclonus
    ´Ù¹ß±Ù´ë¼º¹ßÀÛ
  • multiple peripheral neuritis
    ´Ù¹ß¸»ÃʽŰ濰
  • multiple personality
    ´ÙÁßÀΰÝ
  • multiple personality disorder
    ´ÙÁßÀΰÝÀå¾Ö
  • multiple pregnancy
    ´ÙÅÂÀÓ½Å, ¹µÀÓ½Å
  • multiple scattering
    ´ÙÁß»ê¶õ
  • multiple sclerosis
    ´Ù¹ß°æÈ­Áõ
  • multiple serositis
    ´Ù¹ßÀ帷¿°
  • multiple sleep latency test
    ¼ö¸éÀẹ±â¹Ýº¹°Ë»ç
  • multiple subpial transection
    ´Ù¹ß¿¬¸·¹ØÀý´Ü(¼ú)
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  • ¿µ¹®
    ÇѱÛ
  • multiple fission
    ¹µºÐ¿­, ´Ù¼öºÐ¿­
  • multiple fracture
    ´Ù¹ß°ñÀý
  • multiple sclerotic gait
    ´Ù¹ß°æÈ­Áõ°ÉÀ½
  • multiple infection
    ¿©·¯¹ø°¨¿°
  • multiple intussusception
    ´Ù¹ßâÀÚ°ãħÁõ
  • multiple field irradiation
    ´ÙÁ¶»ç¿µ¿ªÁ¶»ç
  • multiple keratoacanthoma
    ´Ù¹ß°¢Áú°¡½Ã¼¼Æ÷Á¾
  • multiple labor
    ´Ù»ê, ´Ùźи¸
  • multiple
    ´Ù¹ß-, ¿©·¯-, ¹µ-, ´Ù-
  • multiple myeloma
    ´Ù¹ß°ñ¼öÁ¾
  • multiple myositis
    ´Ù¹ß±ÙÀ°¿°
  • multiple neurofibromatosis
    ´Ù¹ß½Å°æ¼¶À¯Á¾Áõ
  • multiple neuroma
    ´Ù¹ß½Å°æÁ¾
  • multiple paramyoclonus
    ´Ù¹ß±Ù°£´ë°æ·Ã
  • multiple personality
    ´ÙÁßÀΰÝ
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  • ¿µ¹®
    ÇѱÛ
  • glutathione reductase deficiency
    ±Û·çŸƼ¿Â ȯ¿øÈ¿¼Ò °áÇÌÁõ.
  • glycosidase deficiency
    ±Û¸®ÄڽôپÆÁ¦°áÇÌ(Áõ).
  • gonadal deficiency
    »ý½Ä¼±ºÎÀü(ßæãÖàÍÝÕîï).
  • gonadal deficiency
    »ý½Ä¼±ºÎÀü(ßæãÖàÍÝÕîï).
  • hepatophosphorylase deficiency
    °£Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦°áÇÌÁõ.
  • hexokinase deficiency
    Çí¼ÒÄ«À̳×À̽º°áÇÌ.
  • hexokinase deficiency
    Çí¼ÒŰ³ªÁ¦°áÇÌ.
  • hexosaminidase a deficiency
    Çí¼Ò»ç¹Ì´Ïµ¥À̽º A °áÇÌ(Áõ)
  • iduronate sulfatase deficiency
    Iduronate sulfatase deficiency
  • iga deficiency
    ¸é¿ª±Û·ÎºÒ¸° A °áÇÌ
  • immune deficiency disease
    ¸é¿ª°áÇÌÁúȯ<º´>.
  • immunoglobulin A deficiency
    ¸é¿ª±Û·ÎºÒ¸° A °áÇÌ(Áõ)
  • immunologic deficiency state
    ¸é¿ª°áÇÌ »óÅÂ.
  • immunologic deficiency syndrome
    ¸é¿ª°áÇÌ ÁõÈıº(¡­ÌÀù¹ ñøý¦ÏØ)
  • immunological deficiency state
    ¸é¿ª°áÇÌ »óÅÂ.
¿¾ ´ëÇÑÀÇÇù 3 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 4
  • ¿µ¹®
    ÇѱÛ
  • multiple embolism
    ¹æ»ç ´Ù¹ß¼º »öÀüÁõ.
  • multiple embolism
    ´Ù¹ß¼º »öÀüÁõ(¡­ ßáîûñø)
  • multiple endocrine adenoma
    ´Ù¹ß¼º ³»ºÐºñ¼±Á¾(¡­Ò®ÝÂù²àÍðþ).
  • multiple endocrine adenoma
    ´Ù¹ß¼º ³»ºÐºñ¼±Á¾(¡­Ò®ÝÂù²àÍðþ)
  • multiple endocrine adenoma
    ´Ù¹ß¼º ³»ºÐºñ¼±Á¾(¡­³»ºÐÇʼ±Á¾).
  • multiple endocrine adenomatosis =MEA
    ´Ù¹ß¼º ³»ºÐºñ¼±Á¾Áõ(ÒýÛ¡àõÒ®ÝÂù²àÍðþñø).
  • multiple endocrine adenomatosis =MEA
    ´Ù¹ß¼º ³»ºÐºñ¼±Á¾Áõ(´Ù¹ß¼º³»ºÐÇʼ±Á¾Áõ).
  • multiple endocrine adenomatosis =mea
    ´Ù¹ß¼º ³»ºÐºñ¼±Á¾Áõ(¡­ñø)
  • multiple endocrine neoplasia
    ´Ù¹ß¼º ³»ºÐºñ ½Å»ý¹°
  • multiple endocrine neoplasia
    º¹ÇÕ³»ºÐºñ¼±½Å»ý¹°(ãæßæÚª)
  • multiple endocrine neoplasia syndrome
    ´Ù¹ß¼º ³»ºÐºñ¼±Á¾Áõ
  • multiple endocrine neoplasia(MEN)
  • multiple epiphyseal dysplasia
    ¹æ»ç º´¸®´Ù¹ß¼º °ñ´ÜÀÌÇü¼ºÁõ.
  • multiple epiphyseal dysplasia
    ´Ù¹ß¼º °ñ´ÜÀÌÇü¼ºÁõ(ÒýÛ¡àõÍéÓ®ì¶û¡à÷ñø).
  • multiple epitheliomatosis
    ´Ù¹ß»óÇÇÁ¾Áõ(Òý Û¡ß¾ù«ðþñø).
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 4
CoA-SPC coenzyme A-synthetizing protein complex
HADH hydroxyacyl CoA dehydrogenase
HMG CoA 3-hydroxy-3-methylglutaryl coenzyme A
HS-CoA reduced coenzyme A
DAG Di-Acyl-Gylcerol
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 4
VLCAD Very long chain acyl-CoA dehydrogenase
ACOX acyl CoA oxidase
HMG CoA 3-hydroxy-3-methylglutaroyl CoA
HMG-CoA reductase 3-Hydroxy-3-methylglutaryl CoA reductase
HMG-CoA 3-hydroxymethylglutaryl-CoA
°æºÏ´ë Ä¡°ú´ëÇÐ ±¸°­³»°ú ±³½Ç »çÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 4
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    ÇѱÛ
    ¼³¸í
  • vitamin I deficiency
    ºñŸ¹Î °áÇÌ, ºñŸ¹Î °áÇÌÁõ
  • vitamin K deficiency
    ºñŸ¹Î K °áÇÌ, ºñŸ¹Î K °áÇÌÁõ
    Ç÷¾×ÀÇ ÀÀ°í ½Ã°£ÀÌ ±æ¾îÁø´Ù.
  • affecting multiple system
    ´Ù¹ß¼º °èÅëÀ» ħ¹üÇÑ
  • discrete multiple endocrine adenomatosis syndrome
    ºÐ¸®¼º ´Ù¹ß ³»ºÐºñ ¼±Á¾ ÁõÈıº
  • multiple
    ´Ù¹ß¼º, ´Ù¼öÀÇ
  • multiple abutment
    ´Ù¼ö Áö´ëÄ¡
  • multiple allelomorph
    º¹´ë¸³ À¯ÀüÀÚ
  • multiple anchorage
    º¹ÇÕ °íÁ¤
    1Çü½Ä ÀÌ»óÀÇ ÈûÀ» °¡ÇÏ´Â ÀåÄ¡¸¦ »ç¿ëÇÏ´Â °íÁ¤.
  • multiple angioma
    ´Ù¹ß¼º ¸Æ°üÁ¾
  • multiple biologically active peptide fragment
    ´Ù¹ß¼º »ý¹°ÇÐÀû Ȱ¼º ÆéŸÀÌµå ºÐÀý
  • multiple cavernous hemangioma
    ´Ù¹ß¼º ÇØ¸é Ç÷°üÁ¾
  • multiple condylome
    ´Ù¹ß¼º ½À¿ì
  • multiple cranial nerve palsy
    ´Ù¹ß¼º ³ú ½Å°æ ¸¶ºñ
  • multiple diagnosis
    º¹¼ö Áø´Ü
  • multiple drug misuse
    ¿©·¯ ¾à¹°ÀÇ ¿À¿ë
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 4
N-acyl-D-aspartate amidohydrolase <enzyme> Specific for d-aspartate; amino acid sequence given in first source
Registry number: EC 3.5.1.-
Synonym: d-aaase, n-acyl-d-asp amidohydrolase
(26 Jun 1999)
N-acyl-D-glutamate deacylase <enzyme> Substrate specificity is for short chain acyl glutamates, including n-formyl-d-glutamate, n-chloroacetyl-d-glutamate and n-acetyl-d-glutamate
Registry number: EC 3.5.1.-
Synonym: n-acyl-d-glutamate amidohydrolase, d-agase
(26 Jun 1999)
N-acyl-D-mannosamine dehydrogenase <enzyme> Catalyses the conversion of n-acetyl-d-mannosamine and nad+ to n-acetyl-d-mannosaminic acid and NADH
Registry number: EC 1.1.1.-
Synonym: nadm-dehydrogenase, n-acylmannosamine dehydrogenase
(26 Jun 1999)
fatty acyl ethyl ester synthase <enzyme> Myocardial enzyme; esterifies free fatty acids in the absence of ATP and coenzyme a; the fatty acid ethyl ester synthase III has homology with glutathione s-transferase
Registry number: EC 2.3.1.-
Synonym: fatty acid ethyl ester synthase, fatty acid ethyl ester synthase III, faee synthase, faees-iii gene product
(26 Jun 1999)
1-acyl-glycerophosphoethanolamine acyltransferase <enzyme> Guinea pig heart microsome enzyme; not the same as EC 2.3.1.25 (plasmalogen synthase)
Registry number: EC 2.3.1.-
Synonym: acyl-CoA-1-acylglycerophosphoethanolamine 2-acyltransferase, 1-agpe acyltransferase, acyl-coenzyme a-1-acylglycerophosphoethanolamine 2-acyltransferase
(26 Jun 1999)
1-O-alkyl-2-acyl-sn-glycero-3-phosphorylethanolamine desaturase <enzyme> Alkylacylglycerophosphorylethanolamine alk-1-enylacyl-glycerophosphorylethanolamine (ethanolamine plasmalogen) type of reaction (cis-olefination), cofactor requirement resembles fatty acid desaturases
Registry number: EC 1.14.99.-
(26 Jun 1999)
3-oxoacyl-(acyl-carrier-protein) synthase <enzyme> An enzyme of long-chain fatty acid synthesis, that adds a two-carbon unit from malonyl-(acyl carrier protein) to another molecule of fatty acyl-(acyl carrier protein), giving a beta-ketoacyl-(acyl carrier protein) with the release of carbon dioxide.
Chemical name: Acyl-(acyl carrier protein):malonyl-(acyl-carrier-protein) C-acyltransferase (decarboxylating)
Registry number: EC 2.3.1.41
(12 Dec 1998)
long-chain-fatty-acid-(acyl-carrier-protein) ligase <enzyme> Fatty acid, acyl-carrier-protein-sh and ATP gives acyl-(acyl-carrier-protein), AMP and ppi
Registry number: EC 6.2.1.20
Synonym: fatty acid-acyl carrier protein ligase (AMP), acyl-(acyl-carrier-protein)synthetase, aacp synthetase, fatty acyl-acyl carrier protein synthase, vibrio harveyi, acyl-(acyl-carrier-protein) synthetase, acyl-acp synthetase
(26 Jun 1999)
long-chain-fatty-acyl-glutamate deacylase <enzyme> Lca aminoacylase I almost specific to l-glutamate-containing lipoamino acids; lca aminoacylase II acts on fatty acyl amino acids with chain lengths between c11 and c16
Registry number: EC 3.5.1.55
Synonym: lca aminoacylase I, lca aminoacylase II, n-long chain acyl aminoacylase
(26 Jun 1999)
abortion, multiple Couples who have had 2 or more miscarriages (spontaneous abortions) have about a 5% chance that one member of the couple is carrying a chromsome translocation responsible for the miscarriages.
(12 Dec 1998)
advanced multiple-beam equalization radiography A variant of scanning equalization radiography using several X-ray beams.
(05 Mar 2000)
amyloidosis of multiple myeloma Foci of amyloidosis in mesenchymal tissues of some persons with multiple myeloma; no direct relation between amyloid and Bence Jones protein is conclusively known.
(05 Mar 2000)
cancer, multiple myeloma A bone marrow cancer involving a type of white blood cell called a plasma (or myeloma) cell. The tumour cells can form a single collection (a plasmacytoma) or many tumours (multiple myeloma). Plasma cells are part of the immune system and make antibodies. Because patients have an excess of identical plasma cells, they have too much of one type of antibody. As myeloma cells increase in number, they damage and weaken the bones, causing pain and often fractures. When bones are damaged, calcium is released into the blood leading to hypercalcaemia (excess calcium in the blood) and that causes loss of appetite, nausea, thirst, fatigue, muscle weakness, restlessness, and confusion. Myeloma cells prevent the bone marrow from forming normal plasma cells and other white blood cells important to the immune system so patients may not be able to fight infections. The cancer cells can also prevent the growth of new red blood cells, causing anaemia. Excess antibody proteins and calcium may prevent the kidneys from filtering and cleaning the blood properly Cancer, non-Hodgkin's lymphoma: A lymphoma is a cancer that develops in the lymphatic system. The most common symptom of non-Hodgkin's lymphomas is a painless swelling in the lymph nodes in the neck, underarm, or groin. Non-Hodgkin's lymphomas are diagnosed with a biopsy of an enlarged lymph node. Follow-up examinations are important after lymphoma treatment. Most relapses occur in the first 2 years after therapy.
(12 Dec 1998)
chromosomes in multiple miscarriages Couples who have had more than one miscarriage (spontaneous abortion) have about a 5% chance that one member of the couple is carrying a chromsome translocation responsible for the miscarriages.
(12 Dec 1998)
miscarriages, multiple, chromosomes in Couples who have had more than one miscarriage have about a 5% chance that one member of the couple is carrying a chromsome translocation responsible for the miscarriages.
(12 Dec 1998)
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