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  • Histiocytosis, Non-Langerhans-Cell - »õâ Group of disorders which feature accumulations of active HISTIOCYTES and LYMPHOCYTES, but where the histiocytes are not LANGERHANS CELLS. The group includes HEMOPHAGOCYTIC LYMPHOHISTIOCYTOSIS; SINUS HISTIOCYTOSIS; xanthogranuloma; reticulohistiocytoma; JUVENILE XANTHOGRANULOMA; xanthoma disseminatum; as well as the lipid storage diseases (SEA-BLUE HISTIOCYTE SYNDROME; and NIEMANN-PICK DISEASES).
    Synonyms : Disseminatum, Xanthoma, Histiocytosis, Non Langerhans Cell, Non-Langerhans-Cell Histiocytosis, Reticulohistiocytomas
  • Histiocytosis, Sinus - »õâ Benign, non-Langerhans-cell, histiocytic proliferative disorder that primarily affects the lymph nodes. It is often referred to as sinus histiocytosis with massive lymphadenopathy.
    Synonyms : Destombes Rosai Dorfman Syndrome, Disease, Rosai-Dorfman, Histiocytoses, Sinus, Rosai Dorfman Disease, Sinus Histiocytoses, Sinus Histiocytosis, Syndrome, Destombes-Rosai-Dorfman
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histiocytic medullary reticulosis A form of malignant histiocytosis marked by anemia; granulocytopenia; enlargement of the spleen, liver, and lymph nodes; and phagocytosis of red blood cells.
Ãâó:
histi(o)- a combining form denoting relationship to tissue.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
histic pertaining to or of the nature of tissue.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
histidase histidine ammonia-lyase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
histidine ammonia-lyase [EC 4.3.1.3] an enzyme of the lyase class that catalyzes the deamination of histidine to urocanate, the initial step of histidine catabolism. Deficiency of the enzyme, an autosomal recessive trait, causes histidinemia. Called also histidase.
Ãâó: www.mercksource.com/pp/us/cns/cns_health_library.j...
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