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"Deficiency, phenylalanine hydroxylase"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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  • glucuronidase deficiency disease
    ±Û·çÅ¥·Î´Ïµ¥À̽º °áÇÌÁõ
  • glutathione reductase deficiency
    ±Û·çŸƼ¿Â ȯ¿øÈ¿¼Ò °áÇÌÁõ.
  • glycosidase deficiency
    ±Û¸®ÄڽôپÆÁ¦°áÇÌ(Áõ).
  • gonadal deficiency
    »ý½Ä¼±ºÎÀü(ßæãÖàÍÝÕîï).
  • gonadal deficiency
    »ý½Ä¼±ºÎÀü(ßæãÖàÍÝÕîï).
  • hepatophosphorylase deficiency
    °£Æ÷½ºÆ÷¸±¶ó¾ÆÁ¦°áÇÌÁõ.
  • hexokinase deficiency
    Çí¼ÒÄ«À̳×À̽º°áÇÌ.
  • hexokinase deficiency
    Çí¼ÒŰ³ªÁ¦°áÇÌ.
  • hexosaminidase a deficiency
    Çí¼Ò»ç¹Ì´Ïµ¥À̽º A °áÇÌ(Áõ)
  • iduronate sulfatase deficiency
    Iduronate sulfatase deficiency
  • iga deficiency
    ¸é¿ª±Û·ÎºÒ¸° A °áÇÌ
  • immune deficiency disease
    ¸é¿ª°áÇÌÁúȯ<º´>.
  • immunoglobulin A deficiency
    ¸é¿ª±Û·ÎºÒ¸° A °áÇÌ(Áõ)
  • immunologic deficiency state
    ¸é¿ª°áÇÌ »óÅÂ.
  • immunologic deficiency syndrome
    ¸é¿ª°áÇÌ ÁõÈıº(¡­ÌÀù¹ ñøý¦ÏØ)
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  • combined immunity deficiency synsdrome
    º¹Çո鿪°áÇÌÁõÈıº.
  • complement deficiency
    º¸Ã¼°áÇÌ
  • congenital deficiency of glucuronyl transfe ra se
    ¼±Ãµ¼º ±Û·çÄí·Ð»ê Àü À§È¿¼Ò°áÇÌÁõ(¡­ï®êÈý£áÈÌÀù¹ñø).
  • copper deficiency
    ±¸¸®°áÇÌÁõ(¡­ÌÀù¹ñø)
  • cytochrome C oxidase deficiency
    ½ÃƮũ·Ò C ¿Á½Ã´ÙÁ¦(»êÈ­È¿¼Ò)°áÇÌ
  • cytochrome b5 reductase deficiency
    ½ÃÅäÅ©·Ò b5 ȯ¿øÈ¿¼Ò °áÇÌ
  • cytogenetic deficiency
    ¼¼Æ÷¹ß»ý°áÇÌ
  • deficiency
    °áÇÌ(Áõ)(ÌÀù¹ñø)
  • deficiency
    °áÇÌ
  • deficiency (monstrous tumor)
    °áÇÌ (±«¹°Á¾)
  • deficiency (nanismus)
    °áÇÌ(³­ÀåÀÌÁõ)
  • deficiency state, complement
    º¸Ã¼°áÇÌÁõ
  • diabetes mellitus,insulin deficiency
    Àν¶¸° °áÇÌÁõ(¡­ÌÀù¹ñø)
  • dietary deficiency
    ½ÄÀ̼º ¿µ¾ç°áÇÌ(½ÄÀ̼º¿µ¾ç°áÇÌ).
  • dietary deficiency
    ½ÄÀ̼º ¿µ¾ç°áÇÌ(ãÝìÈàõç½å×ÌÀù¹).
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PHA passive hemagglutination [test]; peripheral hyperalimentation; phenylalanine; phytohemagglutinin; ph...
Phe phenylalanine
PLV partial liquid ventilation; poliomyelitis live vaccine; panleukopenia virus; phenylalanine, lysine, ...
AAMD American Association on Mental Deficiency; ¹Ì±¹ Á¤½Å ¹Ú¾à Çùȸ
AAMD-ABS American Association on Mental Deficiency-Adaptive Behavior Scale; ¹Ì±¹ Á¤½Å ¹Ú¾à Çùȸ ÀûÀÀ Çൿ ôµµ...
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 4
FMLP N-formyl-methionyl-leucine-phenylalanine
fMLF N-formyl-methionyl-leucyl-phenylalanine
AHH ARyl hydrocarbon hydroxylase
AH Aniline hydroxylase
BPH Benzo(a)pyrene hydroxylase
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 4
hexobarbital hydroxylase <enzyme> Hexobarbital goes to 3-hydroxyhexobarbital
Registry number: EC 1.14.-
(26 Jun 1999)
hydroxycholesterol 25-hydroxylase <enzyme> Acts on 22r-hydroxycholesterol and 20s-hydroxycholesterol
Registry number: EC 1.14.99.-
Synonym: 25-hydroxylase
(26 Jun 1999)
hydroxylase <enzyme> A type of enzyme which adds -OH groups to its substrate during hydroxylation reactions by attaching oxygen atoms to it.
(09 Oct 1997)
steroid 11-alpha-hydroxylase <enzyme> Converts 11-deoxycortisol to 11-alpha cortisol (the 11-alpha isomer of hydrocortisone)
Registry number: EC 1.14.99.-
(26 Jun 1999)
steroid 14-alpha-hydroxylase <enzyme> From induced vegetative cell cultures of mucor piriformis; hydroxylates progesterone to 14-alpha-hydroxyprogesterone in the presence of NADPH and oxygen
Registry number: EC 1.14.13.-
Synonym: progesterone 14-alpha-hydroxylase
(26 Jun 1999)
steroid 15-beta-hydroxylase <enzyme> Contains p-450 and ferredoxin; from bacillus megaterium
Registry number: EC 1.14.99.-
Synonym: cytochrome p-450 15 beta-hydroxylase, p-450 (15-beta), steroid-15 beta-monooxygenase, cytochrome p-450meg, cytochrome p4502c12, cyp2c12 protein
(26 Jun 1999)
steroid 19-hydroxylase <enzyme> Enzyme from adrenal mitochondria; forms 19-hydroxy-11-deoxycorticosterone
Registry number: EC 1.14.13.-
Synonym: 19-hydroxysteroid hydroxylase, deoxycorticosterone 11-19-hydroxylase
(26 Jun 1999)
steroid (23R)-hydroxylase <enzyme> Increased (23r)-hydroxylase activity in patients with cerebrotendinous xanthomatosis, an inborn error of metabolism in bile acid synthesis resulting in (23r)-hydroxylation of bile acids
Registry number: EC 1.14.99.-
Synonym: bile acid (23r)-hydroxylase, bile alcohol (23r)-hydroxylase
(26 Jun 1999)
steroid 25-hydroxylase <enzyme> Involved in cholesterol degradation to cholic acid
Registry number: EC 1.14.99.-
(26 Jun 1999)
steroid 7 alpha-hydroxylase <enzyme> Testosterone and androstenedione incubated with microsomes from rat testes produced 7alpha-hydroxytestosterone and 7alpha-hydroxyandrostenedione
Registry number: EC 1.14.99.-
Synonym: testicular 7 alpha-hydroxylase, 7 alpha-hydroxylase, microsomal 7alpha-hydroxylase, andiostenedione 7 alpha-hydroxylase, sterol 7 alpha-hydroxylase, cytochrome p-450iia1, cytochrome p450iia1
(26 Jun 1999)
sterol 27-hydroxylase <enzyme> Performs multiple monooxygenations in the conversion of 5 beta cholestane-3 alpha, 7 alpha, 12 alpha-triol into 3 alpha, 7 alpha, 12 alpha-trihydroxy-5 beta-cholestanoic acid in presence of NADPH and cytochrome p-450
Registry number: EC 1.14.12.-
Synonym: cyp27, cytochrome p450 cyp27, c-triol 27-hydroxylase, cyp27 gene product, p450c27
(26 Jun 1999)
n-hexadecane-omega-hydroxylase <enzyme> Membrane bound hydroxylase from candida lipolytica
Registry number: EC 1.14.-
(26 Jun 1999)
N-nitrosopyrrolidine alpha-hydroxylase <enzyme> A variety of cytochrome p-450 isoenzymes involved in rabbit liver microsomal activity
Registry number: EC 1.14.13.-
Synonym: npa-hydroxylase
(26 Jun 1999)
deacetoxycephalosporin C hydroxylase <enzyme> From streptomyces clavuligerus; hydroxylates deacetoxycephalosporin c at the c3 methyl group to yield deacetylcephalosporin c
Registry number: EC 1.14.11.-
Synonym: daoc hydroxylase, deacetylcephalosporin c synthetase, daoc 3'-hydroxylase, ceff gene product
(26 Jun 1999)
deoxyhypusine hydroxylase <enzyme> Catalyses formation of hypusine from deoxyhypusine; does not require alpha-ketoglutarate, iron or ascorbic acid
Registry number: EC 1.14.99.29
(26 Jun 1999)
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