| von hippel-lindau syndrome | <radiology> Retinocerebellar angiomatosis, phakomatosis, autosomal dominant (variable penetrance), haemangioblastoma: most frequent cause of death, cerebellar (most common), also medullary and spinal, retinal angiomatosis (45%), renal cell carcinoma: 2nd most common cause of death, pheochromocytoma (17%), cortical renal cysts (75%), cysts in virtually any organ, renal/liver haemangioma/adenoma, pancreatic cystic neoplasms, isleT-cell tumours, paraganglioma (12 Dec 1998) |
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| von Kossa, Julius | <person> 19th century Austro-Hungarian pathologist. See: von Kossa stain. (05 Mar 2000) |
| von Kossa stain | <technique> A stain for calcium in mineralised tissue, utilizing a silver nitrate solution followed by sodium thiosulfate; calcified bone but not osteoid is stained brown to black. Synonym: Kossa stain. (05 Mar 2000) |
| von Langenbeck's bipedicle mucoperiosteal flap | An operation to close a cleft of the palate using lateral incisions designed to move medially where they are sutured together. (05 Mar 2000) |
| von Meyenburg's disease | A degenerative disease of cartilage producing a bizarre form of arthritis, with collapse of the ears, the cartilaginous portion of the nose, and the tracheobronchial tree; death may occur from chronic infection or suffocation because of loss of stability in the tracheobronchial tree of autosomal origin. Synonym: chronic atrophic polychondritis, generalised chondromalacia, Meyenburg's disease, Meyenburg-Altherr-Uehlinger syndrome, relapsing perichondritis, systemic chondromalacia, von Meyenburg's disease. (05 Mar 2000) |
| von Recklinghausen disease | type 1 neurofibromatosis |
| von Recklinghausen's disease | <disease> A rare genetic disorder which affects the cell growth of nerve tissue. Individuals have multiple cutaneous and subcutaneous tumours which appear in late childhood. Clinical features include medium-brown, flat discolourations to the skin, known as cafe-au-lait spots. Secondary hypertension may develop from renal artery stenosis, pheochromocytoma or coarctation of the aorta. Inheritance: autosomal dominant. (04 Nov 1997) |
| von Schrotter, Leopold | <person> Austrian laryngologist, 1837-1908. See: Paget-von Schrotter syndrome. (05 Mar 2000) |
| von Spee's curve | The anatomic curvature of the mandibular occlusal plane beginning at the tip of the lower cuspid and following the buccal cusps of the posterior teeth, continuing to the terminal molar. Synonym: von Spee's curve. (05 Mar 2000) |
| Von Willebrand disease | <disease, haematology> A hereditary platelet disorder caused by defective or deficient Von Willebrand factor, a protein involved in normal blood clotting, that reduces adhesion to collagen but not aggregation. Both bleeding time and coagulation are increased. Factor VIII levels are secondarily reduced. Symptoms include nosebleeds, bleeding gums, heavy menstrual bleeding, bruising and skin rashes. Inheritance: autosomal dominant. (30 Sep 1997) |
| von Willebrand, E | <person> Finnish physician, 1870-1949. See: von Willebrand's disease. (05 Mar 2000) |
| Von Willebrand factor | Plasma factor involved in platelet adhesion through an interaction with Factor VIII. See: Von Willebrand disease. (18 Nov 1997) |
| von Willebrand factor-degrading protease | <enzyme> A large protease from normal human plasma that degrades vwf at the 842tyr-843met peptide bond Registry number: EC 3.4.24.- Synonym: vwf-cleaving protease (26 Jun 1999) |
| Von Willebrand's disease | <disease> This congenital disease, which is caused a deficiency of a blood factor that promotes platelet adhesion, is characterised by prolonged bleeding and poor blood coagulation. (09 Oct 1997) |
| Reuss, August von | <person> Austrian ophthalmologist, 1841-1924. See: Reuss' formula, Reuss' colour tables, Reuss' test. (05 Mar 2000) |