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"multiple acyl CoA dehydrogenation deficiency"¿¡ ´ëÇÑ °Ë»ö °á°úÀÔ´Ï´Ù. °Ë»ö °á°ú º¸´Â µµÁß¿¡ Tab ۸¦ ´©¸£½Ã¸é °Ë»ö âÀÌ ¼±Åõ˴ϴÙ.
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  • ¿µ¹®
    ÇѱÛ
  • multiple endocrine neoplasia 2
    ´Ù¹ß³»ºÐºñ»ùÁ¾¾ç2Çü
  • multiple endocrine neoplasia 3
    ´Ù¹ß³»ºÐºñ»ùÁ¾¾ç3Çü
  • multiple epiphyseal dysplasia
    ¹µ»À³¡Çü¼ºÀÌ»ó, ´Ù¹ß°ñ´ÜÇü¼ºÀÌ»ó
  • multiple excitation
    ´Ù¹ßÈïºÐ
  • multiple fetation
    ´Ù¼öÀÓ½Å
  • multiple field irradiation
    ¿©·¯¿µ¿ªÁ¶»ç
  • multiple fission
    ¹µºÐ¿­, ´ÙÁߺп­
  • multiple fracture
    ´Ù¹ß°ñÀý
  • multiple infection
    º¹¼ö°¨¿°, ¿©·¯¹ø°¨¿°
  • multiple intestinal polyposis
    ´Ù¹ßÀåÆú¸³Áõ
  • multiple intussusception
    ´Ù¹ßâÀÚ°ãħÁõ, ´Ù¹ßÀåÁßøÁõ
  • multiple keratoacanthoma
    ´Ù¹ß°¢Áú°¡½Ã¼¼Æ÷Á¾
  • multiple labor
    ´Ù»ê, ´Ùźи¸
  • multiple logistic model
    ´ÙÁß·ÎÁö½ºÆ½¸ðÇü
  • multiple myeloma
    ´Ù¹ß°ñ¼öÁ¾
¿¾ ´ëÇÑÀÇÇù ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 3
  • ¿µ¹®
    ÇѱÛ
  • multiple allele
    ¹µ¸Â¼¶ÀÎÀÚ
  • multiple endocrine adenomatosis
    ´Ù¹ß³»ºÐºñ»ùÁ¾Áõ
  • multiple birth
    ´Ù»ê, ´ÙÅÂÃâ»ê, °æ»ê
  • multiple bond
    ´ÙÁß°áÇÕ
  • multiple character
    ´ÙÁß¼º°Ý
  • multiple correlation
    ´ÙÁß»ó°ü
  • multiple deformity
    º¹ÇÕ±âÇü
  • multiple division
    º¹Çպп­
  • multiple dysplasia
    ¹µÇü¼ºÀå¾Ö
  • multiple personality disorder
    ´ÙÁßÀΰÝÀå¾Ö
  • hereditary multiple exostosis
    À¯Àü´Ù¹ß»Àµ¹ÃâÁõ
  • multiple embolism
    ´Ù¹ß»öÀüÁõ
  • multiple epitheliomatosis
    ´Ù¹ß»óÇÇÁ¾Áõ
  • multiple excitation
    ¹Ýº¹ÈïºÐ
  • multiple fetation
    ´Ù¼öÀÓ½Å
¿¾ ´ëÇÑÀÇÇù 2 ÀÇÇпë¾î »çÀü °Ë»ö À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 3
  • ¿µ¹®
    ÇѱÛ
  • anterior pituitary deficiency
    ³úÇϼöüÀü¿±±â´ÉºÎÀü(Áõ)
  • anterior pituitary deficiency
    ÇϼöüÀü¿±±â´ÉºÎÀü(Áõ).
  • antibody deficiency syndrome
    Ç×ü°áÇÌÁõÈıº(ù÷ô÷ÌÀù¹ñøý¦ÏØ).
  • antitrypsin deficiency
    Çׯ®¸³½Å°áÇÌ
  • apolipoprotein C-Il deficiency
    ¾ÆÆ÷Áö´Ü¹é C-II °áÇÌ
  • apolipoprotein b, deficiency
    ¾ÆÆ÷¸®Æ÷´Ü¹éB°áÇÌÁõ(¡­Ó±ÛÜ¡­ÌÀù¹ñø)
  • arylsulfatase a deficiency
    ¾Æ¸±¼³ÆÄŸÁ¦ A °áÇÌÁõ(¡­ÌÀù¹ñø)
  • aspartylglycosamine amide hydrolase, deficiency
    Aspartylglycosamine amide hydrolase°áÇÌ(¡­ÌÀù¹)
  • functional deficiency
    ±â´É°áÇÌ
  • g6pd deficiency
    G6PD(Æ÷µµ´ç-6-Àλ꿰 Å»¼ö¼ÒÈ¿¼Ò) °áÇÌÁõ
  • galactosidase, alpha-galactosidase a, deficiency
    #NAME?
  • glucocerebrosidase deficiency
    ±Û·çÄÚ¼¼·¹ºê·Î½Ãµ¥À̽º °áÇÌÁõ
  • glucose 6 phosphatase deficiency hepa
    ±Û·çÄÚ¿À½º-6 -ÀÎ»ê °áÇ̰£½ÅÇü´ç
  • glucose-6-phosphate dehydrogenase deficiency
    ±Û·çÄÚ½º-6-ÀλêµðÇÏÀÌ µå·ÎÀú³×À̽º °áÇÌ(Áõ)
  • glucuronidase deficiency disease
    ±Û·çÅ¥·Î´Ïµ¥À̽º °áÇÌÁõ
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  • ¿µ¹®
    ÇѱÛ
  • multiple chain
    º¹½Ä(ÜÜãÒ)»ç½½.
  • multiple characters
  • multiple compressed tablet
    ´ÙÁß¾ÐÃàÁ¤Á¦(Òýñìäâõêïüð¥).
  • multiple congenital polyposis
    ´Ù¹ß¼º ¼±Ãµ¼º(¡­à»ô¸àõ) Æú¸³Áõ(¡­ñø)
  • multiple convulsive tic
    ´Ù¹ß¼º °æ·Ã¼º(ÒýÛ¡ àõÌâÕýàõ) ƽ.
  • multiple correlation
    Áß»ó°ü( Ì¡Ë×Ë´).
  • multiple cranial nerve palsy
    ´Ù¹ß¼º ³ú½Å°æ¸¶ºñ(ÒýÛ¡àõÒàãêÌè Ýö).
  • multiple cylindroma
    ´Ù¹ß¼º ¿øÁÖÁ¾
  • multiple deformity
    º¹ÇÕ±âÇü
  • multiple division
    º¹ºÐ¿­(ÜÜÝÂæñ).
  • multiple drug resistance
    ´ÙÁ¦³»¼º
  • multiple drug resistance gene
    º¹ÇÕ¾àÁ¦³»¼ºÀ¯ÀüÀÚ
  • multiple dysplasia (lipochondrodysplasia)
    ¹µÇü¼ºÀå¾Ö (Áö¹æ¿¬°ñÇü¼ºÀå¾Ö)
  • multiple echo
    ´ÙÁß ¿¡ÄÚ
  • multiple echo
    ´ÙÁß (Òýñë) ¿¡ÄÚ
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  • ¿µ¹®
    ÇѱÛ
  • primary deficiency
    ¿ø¹ß¼º °áÇÌ(ê«Û¡àõÌÀù¹)
  • secondary deficiency
    ÀÌÂ÷ °áÇÌ(ì£ó­ÌÀù¹)
  • simian acquired immune deficiency syndrome
    ¿ø¼þÀÌ ÈÄõ¼º¸é¿ª°áÇÌÁúȯ(ý­ô¸àõØóæ¹ÌÀù¹òðü´)
  • sulfite oxidase deficiency
    ¾ÆÈ²»ê(ä¬üÜß«) ¿Á½Ãµ¥À̽º °áÇÌ(ÌÀù¹)
KMLE ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 3
MSD material safety data; mean square deviation; mild sickle cell disease; most significant digit; multi...
CoA Coarctation of Aorta
  - Complications
    1. Severe Hypertensi...
acetyl-CoA acetyl coenzyme A
COA Canadian Ophthalmological Association; Canadian Orthopaedic Association; certificate of authority; c...
CoA coenzyme A
KMLE ÀÚµ¿ÃßÃâ ÀÇÇоà¾î »çÀü À¯»ç °Ë»ö °á°ú : 5 ÆäÀÌÁö: 3
CoA Acyl-coenzyme A
FAO Fatty acyl CoA oxidase
LCAD Long chain acyl-CoA dehydrogenase
MCAD Medium Chain Acyl CoA Dehydrogenase
SCAD Short-chain acyl-CoA dehydrogenase
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  • ¿µ¹®
    ÇѱÛ
    ¼³¸í
  • lactase deficiency
    ¶ôŸÁ¦ °áÇÌ
  • mental deficiency
    Áö´É ¹Ú¾à, Áö´É ¹Ú¾àÁõ, Á¤½Å ¹Ú¾àÁõ
    ¿©·¯ °¡Áö ¿øÀο¡ ÀÇÇØ¼­ Áö´É ¹ß´ÞÀÌ Æò±Õº¸´Ù ³·°í Á¤½ÅÀû, ½ÅüÀû Àå¾Ö·Î ÀÎÇØ »çȸ »ýȰ¿¡ ´ëÇÑ ÀûÀÀÀÌ °ï¶õÇÑ »óÅÂ. Á¤½Å Áöü¶ó°íµµ ÇÑ´Ù. Çö´ë ÀÇÇп¡¼­´Â ÁøÇ༺ ¸¶ºñ¿¡ ÀÇÇÑ Ä¡¸Å³ª ÀϽÃÀûÀÎ Á¤½Å ±â´ÉÀÇ ÅðÇà°ú ±¸º°ÇÏ¿© Ç×±¸ÀûÀÎ Áöü »óŸ¦ ÀǹÌÇÑ´Ù. ¶ÇÇÑ ÀÏ¹Ý Áö´ÉÀÇ °áÇÔ¸¸ÀÌ ¾Æ´Ï¶ó '»çȸ »ýȰ¿¡¼­ÀÇ ½ÇõÀû Áö´É'À̶ó ºÎ¸¦ ¸¸ÇÑ Ãø¸é¿¡µµ ÁÖ¸ñÇÏ°Ô µÇ¸é¼­ Á¤½Å ¹Ú¾àÀÇ ºÐ·ù´Â »çȸÀÇ ÀûÀÀµµ¿Í »çȸÀû »ýȰ ´É·Â Á¤µµ¸¦ ¹èÇÕ½ÃŰ°Ô µÇ¾ú´Ù.
  • mineral deficiency
    ¹«±âÁú °áÇÌ, ¹«±âÁú °áÇÌÁõ
  • myeloperoxidase deficiency
    ¸¶ÀÌ¿¤·Î ÆÛ·Ï½Ãµ¥À̽º °áÇÌÁõ
    »ó¿°»öü¼º ¿­¼º ÇüÁú·Î À¯ÀüµÇ¸ç, Áß¼º±¸¿Í ´Ü±¸ÀÇ È£¾ÆÁÖ¸£¼º °ú¸³ ³»¿¡ MPO°¡ ÀüÇô ¾ø´Ù.
  • myoadenylate deaminase deficiency
    ¸¶ÀÌ¿À ¾Æµ¥´Ò·¹ÀÌÆ® µð¾Æ¹Ì³×À̽º °áÇÌÁõ
  • nutrition deficiency
    ¿µ¾ç °áÇÌÁõ
  • nutritional deficiency
    ¿µ¾ç °áÇÌ
  • plasma thromboplastin antecedent deficiency
    PTA °áÇÌÁõ
  • pyridoxine deficiency
    ÇǸ®µ¶½Å °áÇÌ
  • salt deficiency
    ¿°·ù °áÇÌ
  • sulfatase deficiency
    ¼³ÆÄÅ×À̽º °áÇÌ
  • vitamin B2 deficiency
    ºñŸ¹Î B2 °áÇÌÁõ
  • vitamin D deficiency
    ºñŸ¹Î D °áÇÌ, ºñŸ¹Î D °áÇÌÁõ
    ±¸·çº´-°ñ¿¬È­ÁõÀ¸·Î µî»À³ª °¡½¿»À µûÀ§°¡ ±Á´Â º´. °ö»çº´.
  • vitamin deficiency
    ºñŸ¹Î °áÇÌ, ºñŸ¹Î °áÇÌÁõ
    ¸é Á¾·ùÀÇ ½ÄǰÀ» ¼¯Àº º¸ÅëÀÇ ½Ä»ç¸¦ º¸Åë Á¶¸®¹ý¿¡ µû¶ó ¸ÔÀ» °æ¿ì´Â ºñŸ¹Î °áÇÌÁõÀÌ ³ªÅ¸³ªÁö ¾Ê´Â´Ù. ±×·¯³ª ¿¹¿Ü·Î½á ºñŸ¹Î D°áÇÌÁõÀº ÀÚÁÖ ³ªÅ¸³­´Ù. ½Äǰ Áß¿¡´Â ¿©·¯ Á¾·ùÀÇ ºñŸ¹ÎÀÌ °øÁ¸Çϰí Àֱ⠶§¹®¿¡ 1 Á¾·ù¸¸ÀÇ ºñŸ¹Î °áÇÌÁõº¸´Ùµµ ¿©·¯ Á¾·ùÀÇ ºñŸ¹Î °áÇÌÁõÀÌ ¸¹´Ù. ¼ÒÈ­±â Áúȯ¿¡ ¼ö¹ÝµÇ´Â Èí¼öÀå¾Ö, °¢Á¾ ¾àÀçÀÇ º¹¿ë¿¡ ÀÇÇÑ Àå³» ¼¼±ÕÃþÀÇ º¯È­, ü³»¿¡¼­ÀÇ ºñŸ¹Î Ȱ¼ºÈ­ÀÇ ÀúÇØ, »ý¸®Àû º¯È­¿¡ ´ëÀÀÇÑ ¿ä±¸·®ÀÇ Áõ°¡, °¨¿° µî¿¡ ÀÇÇØ °áÇÌÁõÀÌ ¹ß°ßµÇ´Â °æ¿ì°¡ ÀÖ´Ù. ±×·¯³ª ¾àÇÑ Á¤µµÀÇ °áÇÌÀÎ °æ¿ì¿¡´Â ÀüÇüÀû Áõ»óÀº º¸ÀÌÁö ¾ÊÀ¸¸ç, ÀÌ ¶§ÀÇ Áõ»óÀ» ºñŸ¹Î °¨¼ÒÁõÀ̶ó°í ÇÑ´Ù.
  • vitamin deficiency symptom
    ºñŸ¹Î °áÇÌÁõ
    ºñŸ¹ÎÀÇ ºÎÁ·À¸·Î ÀϾ´Â »ý¸® ±â´É Àå¾Ö. ¾ß¸ÍÁõ, °¢±âº´ µûÀ§°¡ ÀÖ´Ù.
CancerWEB ¿µ¿µ ÀÇÇлçÀü À¯»ç °Ë»ö °á°ú : 15 ÆäÀÌÁö: 3
acyl An organic radical derived from an organic acid by the removal of the carboxylic hydroxyl group.
(05 Mar 2000)
acyl-ACP dehydrogenase enoyl-ACP reductase (NADPH)
acyl-activating enzyme <enzyme> Fatty acid thiokinase (long-chain), a ligase forming acyl-CoA, AMP, and pyrophosphate from long-chain fatty acids, ATP, and coenzyme A. Activity is independent of phosphatidylcholine
Registry number: EC 6.2.1.3
Synonym: acyl-activating enzyme, dodecanoyl-CoA synthetase, fatty acid thiokinase (long chain), acid-coenzyme a ligase, fatty acid-CoA ligase, acyl-CoA synthetase, acyl-CoA ligase, coash ligase, ciprofibroyl-CoA synthetase, pristanoyl-CoA synthetase, palmityl CoA synthetase, palmitoyl CoA synthetase, palmitoyl CoA ligase, fatty acyl-CoA synthetase, very long chain fatty acid acyl-CoA synthetase, vlcfa acyl-CoA synthetase, nafenopin-CoA ligase, palmitoyl-CoA synthase, faa2 gene product, faa2p protein, vlacs enzyme
(26 Jun 1999)
acyl carrier protein <protein> A small (77 peptides long) protein which binds six other enzymes involved in fatty acid synthesis. It was first isolated in E. Coli bacteria.
(09 Oct 1997)
acyl carrier protein acylase <enzyme> From E coli
Registry number: EC 2.3.1.-
Synonym: acp acylase
(26 Jun 1999)
acyl-coenzyme A RCH2COSCoA or RCH2CO~SCoA;condensation product of a carboxylic acid and coenzyme A, and metabolic intermediate of importance, notably in the oxidation and synthesis of fat.
Synonym: acyl-coenzyme A.
(05 Mar 2000)
acyl dihydroxyacetone phosphate oxidoreductase <enzyme> Forms acyl-sn-glycerol 3-phosphate; uses NADPH
Registry number: EC 1.1.1.-
(26 Jun 1999)
acyl glutamic acid amidohydrolase <enzyme> Specific for long chain acyl groups such as lauroyl, myristoyl and palmitoyl
Registry number: EC 3.5.1.-
(26 Jun 1999)
acyl-malonyl-ACP synthase <enzyme> An enzyme condensing malonyl-ACP and acyl-cys-protein to 3-oxoacyl-ACP + cys-protein + CO2, and similar reactions, as steps in fatty acid synthesis; cys-protein is also a part of the fatty acid synthase complex.
Synonym: acyl-malonyl-ACP synthase, beta-ketoacyl-ACP synthase.
(05 Mar 2000)
acyl protein synthetase <enzyme> Component of the fatty acid reductase complex of luminescent bacteria
Registry number: EC 2.3.1.-
Synonym: luxe gene product, fatty acyl-protein synthetase
(26 Jun 1999)
acyl thioester transacylase <enzyme> Component of the fatty acid synthetase complex; forms acetyl pantetheine from acetyl CoA and pantetheine
Registry number: EC 2.3.1.-
(26 Jun 1999)
amino acyl-tRNA ligases <enzyme> Any of the group of ligases that catalyses the ATP-driven formation of a bond between an amino acid and a trna, activating the amino acids as a step in protein synthesis. Individual enzymes are highly specific for one amino acid and for any trna corresponding to that amino acid.
Registry number: EC 6.1.1.
(12 Dec 1998)
beta-hydroxyacyl-(acyl-carrier-protein)dehydrase <enzyme> In fatty acid synthesis; specific for acyl carrier protein; cannot use acyl CoA; see also faba gene product
Registry number: EC 4.2.1.-
Synonym: beta-ohacyl-acp dehydrase, beta-hydroxyacyl-acyl carrier protein dehydratase, fabz gene product
(26 Jun 1999)
RNA, transfer, amino acyl Intermediates in protein biosynthesis. The compounds are formed from amino acids, ATP and transfer RNA, a reaction catalyzed by aminoacyl trna synthetase. They are key compounds in the genetic translation process.
(12 Dec 1998)
protein acyl kinase <enzyme> Transfers gamma-phosphate of ATP to a protein acceptor with formation of an acyl phosphate bond
Registry number: EC 2.7.2.-
(26 Jun 1999)
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