| lamellar ichthyosis | A dry form of congenital ichthyosiform erythroderma, an autosomal recessive trait present at birth; characterised by large, coarse scales over most of the body with thickened palms and soles, and associated with ectropion; histologically, there is hyperkeratosis, a prominent granular layer in the epidermis, slight acanthosis, many mitotic figures, and normal or reduced epidermal cell turnover. See: collodion baby, harlequin foetus. (05 Mar 2000) |
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